S. Cannon

S. Cannon, Josef M. Miller, R. Jyung, 1989, Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery.

A highly-selective chloride microelectrode based on a mercuracarborand anion carrier

Alexander M. Spokoyny, S. Cannon, M. Quinonez, 2019, bioRxiv.

A highly-selective chloride microelectrode based on a mercuracarborand anion carrier

Alexander M. Spokoyny, S. Cannon, M. Quinonez, 2019, Scientific Reports.

Effect of electrical stimulation on middle latency response in the guinea pig.

S. Cannon, J. Miller, J. Crowther, 1990, American journal of otolaryngology.

The cloning and expression of a sodium channel beta 1-subunit cDNA from human brain.

S. Cannon, J. Gusella, S. Slaugenhaupt, 1993, Human molecular genetics.

Human sodium channel gating defects caused by missense mutations in S6 segments associated with myotonia: S804F and V1293I

S. Cannon, A. George, D. S. Green, 1998, The Journal of physiology.

Paying the Price at the Pump Dystonia from Mutations in a Na+/K+-ATPase

S. Cannon, 2004, Neuron.

Recovery from acidosis is a robust trigger for loss of force in murine hypokalemic periodic paralysis

S. Cannon, Fenfen Wu, M. Quinonez, 2019, The Journal of general physiology.

A Four Electrode Method to Study Dynamics of Ion Activity and Transport in Skeletal Muscle Fibers

S. Cannon, M. DiFranco, J. Heiny, 2019, bioRxiv.

Bumetanide prevents transient decreases in muscle force in murine hypokalemic periodic paralysis

S. Cannon, Fenfen Wu, Wentao Mi, 2013, Neurology.

Disrupted coupling of gating charge displacement to Na+ current activation for DIIS4 mutations in hypokalemic periodic paralysis

S. Cannon, V. Rybalchenko, Wentao Mi, 2014, The Journal of general physiology.

A calcium channel mutant mouse model of hypokalemic periodic paralysis.

S. Cannon, D. Burns, Fenfen Wu, 2012, The Journal of clinical investigation.

A sodium channel knockin mutant (NaV1.4-R669H) mouse model of hypokalemic periodic paralysis.

S. Cannon, D. Burns, Fenfen Wu, 2011, The Journal of clinical investigation.

Leaky sodium channels from voltage sensor mutations in periodic paralysis, but not paramyotonia

S. Cannon, V. Rybalchenko, A. Struyk, 2011, Neurology.

Small fiber neuropathy

S. Cannon, 2012, Neurology.

Mice with an NaV1.4 sodium channel null allele have latent myasthenia, without susceptibility to periodic paralysis.

S. Cannon, Fenfen Wu, Wentao Mi, 2016, Brain : a journal of neurology.

Epilepsy channelopathies go neddy: stabilizing NaV1.1 channels by neddylation.

S. Cannon, 2021, The Journal of clinical investigation.

Slow inactivation of the NaV1.4 sodium channel in mammalian cells is impeded by co-expression of the β1 subunit

S. Cannon, Jadon Webb, Fen-fen Wu, 2009, Pflügers Archiv - European Journal of Physiology.

Non-dystrophic Myotonias And Periodic Paralyses

S. Cannon, A. Struyk, 2005 .

Nondystrophic myotonia: Challenges and future directions

S. Cannon, R. Griggs, J. Trivedi, 2014, Experimental Neurology.

Modification of the Na+ current conducted by the rat skeletal muscle α subunit by coexpression with a human brain β subunit

S. Cannon, J. Gusella, A. McClatchey, 1993, Pflügers Archiv.

Modification of the Na+ current conducted by the rat skeletal muscle alpha subunit by coexpression with a human brain beta subunit.

S. Cannon, J. Gusella, A. McClatchey, 1993, Pflugers Archiv : European journal of physiology.

Sequence of the voltage-gated sodium channel beta1-subunit in wild-type and in quivering mice.

S. Cannon, D. Corey, J. Gusella, 1996, Brain research. Molecular brain research.

and in qui˝ering mice

S. Cannon, D. Corey, J. Gusella, 1996 .

Sequence of the voltage-gated sodium channel b-subunit in wild-type 1 and in qui Õ ering mice

S. Cannon, D. Corey, J. Gusella, 1996 .

The cloning and expression of a sodium channel β1-subunit cDNA from human brain

S. Cannon, J. Gusella, S. Slaugenhaupt, 1993 .

Voltage-Dependent Ca2+ Release Is Impaired in Hypokalemic Periodic Paralysis Caused by CaV1.1-R528H but not by NaV1.4-R669H

S. Cannon, M. DiFranco, 2022, bioRxiv.

Review of the Diagnosis and Treatment of Periodic Paralysis

S. Cannon, R. Griggs, J. Statland, 2017, Muscle & nerve.

Beneficial effects of bumetanide in a CaV1.1-R528H mouse model of hypokalaemic periodic paralysis.

S. Cannon, Fenfen Wu, Wentao Mi, 2013, Brain : a journal of neurology.

Mind the magnesium, in dantrolene suppression of malignant hyperthermia

S. Cannon, 2017, Proceedings of the National Academy of Sciences.

Retigabine Suppresses Loss of Force in a Mouse Model of Hypokalemic Periodic Paralysis

S. Cannon, M. Quinonez, 2022, bioRxiv.

Proposed Mechanism for Post‐Exercise Weakness in Hypokalemic Periodic Paralysis

S. Cannon, Fenfen Wu, Wentao Mi, 2016 .

Cooh-Terminal Truncated Alpha1S Subunits Conduct Current Better than Full-Length Dihydropyridine Receptors

S. Cannon, J. A. Morrill, James A. Morrill, 2000, The Journal of general physiology.

Pathomechanisms in channelopathies of skeletal muscle and brain.

S. Cannon, 2006, Annual review of neuroscience.

Voltage-gated ion channelopathies of the nervous system

S. Cannon, 2001, Clinical Neuroscience Research.

MOD-1 is a serotonin-gated chloride channel that modulates locomotory behaviour in C. elegans

H. Horvitz, S. Cannon, R. Ranganathan, 2000, Nature.

A proposed neural network for the integrator of the oculomotor system

Stephen C. Cannon, David A. Robinson, Shihab Shamma, 1983, Biological Cybernetics.

The effect of the rotational magnification of corrective spectacles on the quantitative evaluation of the VOR.

R J Leigh, D S Zee, R. Leigh, 1985, Acta oto-laryngologica.

Myotonic Myopathy With Secondary Joint and Skeletal Anomalies From the c.2386C>G, p.L796V Mutation in SCN4A

S. Cannon, Lijia Huang, G. Graham, 2020, Frontiers in Neurology.

The non-dystrophic myotonias: molecular pathogenesis, diagnosis and treatment.

S. Cannon, R. Griggs, R. Barohn, 2010, Brain : a journal of neurology.

Myasthenic syndrome caused by mutation of the SCN4A sodium channel

S. Cannon, K. Ohno, A. Engel, 2003, Proceedings of the National Academy of Sciences of the United States of America.

A sodium channel defect in hyperkalemic periodic paralysis: Potassium-induced failure of inactivation

S. Cannon, D. Corey, Robert H. Brown, 1991, Neuron.

Hypokalaemic periodic paralysis with a charge-retaining substitution in the voltage sensor

S. Cannon, N. Kokubun, B. Fontaine, 2020, Brain communications.

Targeted mutation of mouse skeletal muscle sodium channel produces myotonia and potassium-sensitive weakness.

S. Cannon, Robert H. Brown, E. Hoffman, 2008, The Journal of clinical investigation.

Sodium Channel Gating No Margin for Error

S. Cannon, 2002, Neuron.

Channelopathies of skeletal muscle excitability.

S. Cannon, 2015, Comprehensive Physiology.

Effects of mutations causing hypokalaemic periodic paralysis on the skeletal muscle L‐type Ca2+ channel expressed in Xenopus laevis oocytes

S. Cannon, J. A. Morrill, James A. Morrill, 1999, The Journal of physiology.

Guidelines on clinical presentation and management of nondystrophic myotonias

S. Cannon, R. Griggs, G. Meola, 2020, Muscle & nerve.

Theoretical reconstruction of myotonia and paralysis caused by incomplete inactivation of sodium channels.

D P Corey, S. Cannon, D. Corey, 1993, Biophysical journal.

Skeletal muscle-specific T-tubule protein STAC3 mediates voltage-induced Ca2+ release and contractility

S. Cannon, E. Olson, J. McAnally, 2013, Proceedings of the National Academy of Sciences.

Sodium Channelopathies of Skeletal Muscle.

S. Cannon, 2018, Handbook of experimental pharmacology.

Functional expression of sodium channel mutations identified in families with periodic paralysis

S. Cannon, S. Strittmatter, 1993, Neuron.

Ion-channel defects and aberrant excitability in myotonia and periodic paralysis

S. Cannon, Stephen C Cannon, 1996, Trends in Neurosciences.

A C‐terminal skeletal muscle sodium channel mutation associated with myotonia disrupts fast inactivation

S. Cannon, E. Hoffman, E. Gordon, 2005, The Journal of physiology.

Defective slow inactivation of sodium channels contributes to familial periodic paralysis

S. Cannon, L. Hayward, S. Cannon, 1999, Neurology.

When all is lost…a severe myopathy with hypotonia from sodium channel mutations.

S. Cannon, 2016, Brain : a journal of neurology.

Mexiletine block of disease‐associated mutations in S6 segments of the human skeletal muscle Na+ channel

S. Cannon, M. Takahashi, 2001, The Journal of physiology.

Inactivation defects caused by myotonia-associated mutations in the sodium channel III-IV linker

S. Cannon, L. Hayward, R. H. Brown, 1996, The Journal of general physiology.

The primary periodic paralyses: diagnosis, pathogenesis and treatment.

S. Cannon, R. Griggs, M. Tristani-Firouzi, 2006, Brain : a journal of neurology.

Gating of the L-Type Ca Channel in Human Skeletal Myotubes: An Activation Defect Caused by the Hypokalemic Periodic Paralysis Mutation R528H

S. Cannon, Robert H. Brown, James A. Morrill, 1998, The Journal of Neuroscience.

Randomized, placebo-controlled trials of dichlorphenamide in periodic paralysis

S. Cannon, A. Pestronk, R. Conwit, 2016, Neurology.

Gating pore currents occur in CaV1.1 domain III mutants associated with HypoPP

S. Cannon, Fenfen Wu, M. Quinonez, 2021, The Journal of general physiology.

An expanding view for the molecular basis of familial periodic paralysis

S. Cannon, 2002, Neuromuscular Disorders.

A Na+ Channel Mutation Linked to Hypokalemic Periodic Paralysis Exposes a Proton-selective Gating Pore

S. Cannon, A. Struyk, 2007, The Journal of general physiology.

Voltage‐sensor mutations in channelopathies of skeletal muscle

S. Cannon, 2010, The Journal of physiology.

A proposed mutation, Val781Ile, associated with hyperkalemic periodic paralysis and cardiac dysrhythmia is a benign polymorphism

S. Cannon, A. George, L. Hayward, 1997, Annals of neurology.

Pathophysiology of myotonia and periodic paralysis

S. Cannon, G. Mckhann, W. Mcdonald, 2002 .

Stac3 enhances expression of human CaV1.1 in Xenopus oocytes and reveals gating pore currents in HypoPP mutant channels

S. Cannon, Fenfen Wu, M. Quinonez, 2018, The Journal of general physiology.

From mutation to myotonia in sodium channel disorders

S. Cannon, 1997, Neuromuscular Disorders.

Gating Pore Currents in DIIS4 Mutations of NaV1.4 Associated with Periodic Paralysis: Saturation of Ion Flux and Implications for Disease Pathogenesis

S. Cannon, V. Markin, A. Struyk, 2008, The Journal of general physiology.

Paradoxical depolarization of BA2+‐ treated muscle exposed to low extracellular K+: Insights into resting potential abnormalities in hypokalemic paralysis

S. Cannon, A. Struyk, 2008, Muscle & nerve.

Identification and Functional Characterization of Kir2.6 Mutations Associated with Non-familial Hypokalemic Periodic Paralysis*

S. Cannon, Shih-Hua Lin, Chou-Long Huang, 2011, The Journal of Biological Chemistry.

Physiologic principles underlying ion channelopathies

S. Cannon, 2007, Neurotherapeutics.

Sodium channel defects in myotonia and periodic paralysis.

S. Cannon, 1996, Annual review of neuroscience.

Cold-induced defects of sodium channel gating in atypical periodic paralysis plus myotonia

S. Cannon, Jadon Webb, 2008, Neurology.

The common missense mutation D489N in TRIM32 causing limb girdle muscular dystrophy 2H leads to loss of the mutated protein in knock-in mice resulting in a Trim32-null phenotype.

S. Cannon, E. Kudryashova, M. Spencer, 2011, Human molecular genetics.

Resurgent and Gating Pore Currents Induced by De Novo SCN2A Epilepsy Mutations

S. Cannon, T. Cummins, Fenfen Wu, 2019, eNeuro.

GAP-43 augments G protein-coupled receptor transduction in Xenopus laevis oocytes.

S. Cannon, M. Fishman, S. Strittmatter, 1993, Proceedings of the National Academy of Sciences of the United States of America.

Gating behaviour of sodium currents in adult mouse muscle recorded with an improved two‐electrode voltage clamp

S. Cannon, V. Markin, A. Struyk, 2011, The Journal of physiology.

Slow Inactivation Does Not Affect Movement of the Fast Inactivation Gate in Voltage-gated Na+ Channels

S. Cannon, V. Vedantham, Vasanth Vedantham, 1998, The Journal of general physiology.

The distinct role of the four voltage sensors of the skeletal CaV1.1 channel in voltage-dependent activation

S. Cannon, R. Olcese, Fenfen Wu, 2021, The Journal of general physiology.

β-Catenin stabilization in skeletal muscles, but not in motor neurons, leads to aberrant motor innervation of the muscle during neuromuscular development in mice.

S. Cannon, M. Taketo, Fenfen Wu, 2012, Developmental biology.

Spectrum of sodium channel disturbances in the nondystrophic myotonias and periodic paralyses.

S. Cannon, 2000, Kidney international.

Sodium channel inactivation is impaired in equine hyperkalemic periodic paralysis.

S. Cannon, L. Hayward, J. Beech, 1995, Journal of neurophysiology.

An improved neural-network model for the neural integrator of the oculomotor system: More realistic neuron behavior

Stephen C. Cannon, David A. Robinson, D. Robinson, 1985, Biological Cybernetics.

Kv4.2 autism and epilepsy mutation enhances inactivation of closed channels but impairs access to inactivated state after opening

S. Cannon, D. Papazian, Meng-chin A. Lin, 2018, Proceedings of the National Academy of Sciences.

Inhibition protects acquired song segments during vocal learning in zebra finches

S. Cannon, S. Houser, E. Olson, 2022 .

A role for external Ca2+ in maintaining muscle contractility in periodic paralysis

S. Cannon, 2020, The Journal of general physiology.

Myasthenic congenital myopathy from recessive mutations at a single residue in NaV1.4

S. Cannon, M. Hanna, P. Shieh, 2019, Neurology.

Hypokalemic periodic paralysis ( HypoPP ) is an ion channelopathy of skeletal muscle characterized by attacks of muscle weakness associated with low serum

S. Cannon, D. Burns, Fenfen Wu, 2011 .

Further evidence for shared genetic susceptibility in both sporadic and Thyrotoxic periodic paralysis

S. Cannon, 2020, Journal of the Neurological Sciences.

New territory opened by periodic paralysis associated with mitochondrial DNA mutation

S. Cannon, R. Ruff, 2013, Neurology.

Anesthesia Effects on the Electrically Evoked Middle Latency Response in Guinea Pigs

S. Cannon, J. Crowther, P. Kileny, 1989, Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery.

Truncated ClC-1 mRNA in myotonic dystrophy exerts a dominant-negative effect on the Cl current

S. Cannon, C. Thornton, Hong Jiang, 2004, Neurology.

Mice with an NaV1.4 sodium channel null allele have latent myasthenia, without susceptibility to periodic paralysis.

S. Cannon, Fenfen Wu, Wentao Mi, 2016, Brain : a journal of neurology.

Stac3 Facilitated Expression of CaV1.1 in Xenopus Oocytes to Assess Functional Consequences of Hypopp Mutant CaV1.1-R528H

S. Cannon, Fenfen Wu, 2017 .

Bumetanide prevents transient decreases in muscle force in murine hypokalemic periodic paralysis

S. Cannon, Fenfen Wu, Wentao Mi, 2013, Neurology.

The non-dystrophic myotonias: molecular pathogenesis, diagnosis and treatment.

S. Cannon, R. Griggs, R. Barohn, 2010, Brain : a journal of neurology.

Slow Inactivation Does Not Block the Aqueous Accessibility to the Outer Pore of Voltage-gated Na Channels

S. Cannon, A. Struyk, 2002, The Journal of general physiology.

Modulation of Na+channel inactivation by the β1 subunit: A deletion analysis

S. Cannon, Chinfei Chen, 1995, Pflügers Archiv.

A four-electrode method to study dynamics of ion activity and transport in skeletal muscle fibers

S. Cannon, M. DiFranco, J. Heiny, 2019, bioRxiv.