J. Cooper

J. Cooper, J. Blesa, A. Vettorazzi, 2021, Food and chemical toxicology : an international journal published for the British Industrial Biological Research Association.

MITOCHONDRIAL COMPLEX I DEFICIENCY IN PARKINSON'S DISEASE

A. H. V. Schapira, J. M. Cooper, D. Dexter, 1989, The Lancet.

Lysosomal dysfunction increases exosome-mediated alpha-synuclein release and transmission

Chris Gardiner, A. Schapira, J. Cooper, 2011, Neurobiology of Disease.

Brain, skeletal muscle and platelet homogenate mitochondrial function in Parkinson's disease.

C. Marsden, J. Cooper, A. Schapira, 1992, Brain : a journal of neurology.

Molecular mechanisms in mitochondrial DNA depletion syndrome.

J. Cooper, A. Schapira, P. Clayton, 1997, Human molecular genetics.

Respiratory-deficient human fibroblasts exhibiting defective mitochondrial DNA replication.

J. Cooper, A. Schapira, A. Bodnar, 1995, The Biochemical journal.

Nuclear complementation restores mtDNA levels in cultured cells from a patient with mtDNA depletion.

J. Cooper, A. Schapira, A. Bodnar, 1993, American journal of human genetics.

Coenzyme Q10 and vitamin E deficiency in Friedreich’s ataxia: predictor of efficacy of vitamin E and coenzyme Q10 therapy

J. Cooper, J. Bradley, A. Schapira, 2008, European journal of neurology.

Antioxidant treatment of patients with Friedreich ataxia: four-year follow-up.

A. Blamire, D. Manners, P. Styles, 2005, Archives of neurology.

A missense mutation of cytochrome oxidase subunit II causes defective assembly and myopathy.

I. Nelson, J. Cooper, A. Schapira, 1999, American journal of human genetics.

G2019S leucine-rich repeat kinase 2 causes uncoupling protein-mediated mitochondrial depolarization

M. Duchen, J. Cooper, A. Schapira, 2012, Human molecular genetics.

Influence of microRNA deregulation on chaperone-mediated autophagy and α-synuclein pathology in Parkinson's disease

J. Obeso, M. Rodriguez-Oroz, A. Schapira, 2013, Cell Death and Disease.

Mutant torsinA, which causes early‐onset primary torsion dystonia, is redistributed to membranous structures enriched in vesicular monoamine transporter in cultured human SH‐SY5Y cells

J. Cooper, A. Misbahuddin, M. Placzek, 2005, Movement disorders : official journal of the Movement Disorder Society.

Mitochondrial Dysfunction in Neurodegeneration

J M Cooper, A H Schapira, J. Cooper, 1997, Journal of bioenergetics and biomembranes.

Complex I Inhibitors Induce Dose‐Dependent Apoptosis in PC12 Cells: Relevance to Parkinson's Disease

A Hartley, A H Schapira, J. Cooper, 1994, Journal of neurochemistry.

Mitochondrial myopathies: Clinical and biochemical features of 30 patients with major deletions of muscle mitochondrial DNA

J. Cooper, A. Harding, A. Toscano, 1989, Annals of neurology.

Biochemical abnormalities and excitotoxicity in Huntington's disease brain

S. Tabrizi, J. Cooper, J. Taanman, 1999, Annals of neurology.

Anatomic and Disease Specificity of NADH CoQ1 Reductase (Complex I) Deficiency in Parkinson's Disease

C. Marsden, J. Cooper, S. Daniel, 1990, Journal of neurochemistry.

Analyses of mitochondrial respiratory chain function and mitochondrial DNA deletion in human skeletal muscle: Effect of ageing

J. Cooper, A. Schapira, V. Mann, 1992, Journal of the Neurological Sciences.

Clinical, biochemical and molecular genetic correlations in Friedreich's ataxia.

J. Cooper, J. Bradley, A. Schapira, 2000, Human molecular genetics.

Friedreich's Ataxia: Disease mechanisms, antioxidant and Coenzyme Q10 therapy

J. Cooper, A. Schapira, 2003, BioFactors.

Biochemical and molecular features of deficiencies of Complexes I, II and III

J. Cooper, A. Schapira, 1994 .

Impaired Mitophagy and Protein Acetylation Levels in Fibroblasts from Parkinson’s Disease Patients

J. Cooper, J. M. Bravo-San Pedro, M. Niso-Santano, 2018, Molecular Neurobiology.

Myopathy in vitamin E deficient rats: muscle fibre necrosis associated with disturbances of mitochondrial function.

J. Cooper, A. Schapira, R. King, 1993, Journal of anatomy.

Oxidative-phosphorylation defects in liver of patients with Wilson's disease

J. Cooper, M Gu, JM Cooper, 2000, The Lancet.

Cyclosporin inhibition of apoptosis induced by mitochondrial complex I toxins

J. Cooper, A. Schapira, Tracey A Seaton, 1998, Brain Research.

MitBASE : a comprehensive and integrated mitochondrial DNA database. The present status

Domenica D'Elia, Flavio Licciulli, Marcella Attimonelli, 2000, Nucleic Acids Res..

Systemic exosomal siRNA delivery reduced alpha-synuclein aggregates in brains of transgenic mice

J. Cooper, M. Wood, S. El-Andaloussi, 2014, Movement disorders : official journal of the Movement Disorder Society.

MELAS mitochondrial DNA mutation A3243G reduces glutamate transport in cybrids cell lines

J. Cooper, L. Tremolizzo, C. Ferrarese, 2008, Experimental Neurology.

Analysis of the factors influencing the cardiac phenotype in Friedreich's ataxia

A. Blamire, J. Francis, S. Neubauer, 2010, Movement disorders : official journal of the Movement Disorder Society.

British Association for the Study of the Liver

A. Perelson, C. Dejong, Y. Ma, 1991 .

Mitochondrial defect in Huntington's disease caudate nucleus

J. Cooper, F. Javoy‐Agid, A. Schapira, 1996, Annals of neurology.

Clinical correlates of mitochondrial function in Huntington's disease muscle

J. Cooper, A. Schapira, C. Turner, 2007, Movement disorders : official journal of the Movement Disorder Society.

Smoking and mitochondrial function: a model for environmental toxins.

A H Schapira, J. Cooper, A. Schapira, 1993, The Quarterly journal of medicine.

Biochemical and molecular aspects of human mitochondrial respiratory chain disorders.

J. Cooper, A. Schapira, A. Harding, 1990, Biochemical Society transactions.

MOLECULAR BASIS OF MITOCHONDRIAL MYOPATHIES: POLYPEPTIDE ANALYSIS IN COMPLEX-1 DEFICIENCY

J. Cooper, C. Ragan, A. Schapira, 1988, The Lancet.

Molecular defects of NADH-ubiquinone oxidoreductase (Complex I) in mitochondrial diseases

J. Cooper, A. Schapira, J. Morgan-Hughes, 1988, Journal of bioenergetics and biomembranes.

Platelet mitochondria function in Parkinson's disease

Anthony H.V. Schapira, C. Marsden, J. Cooper, 1992 .

Mitochondrial function in Parkinson's disease

C. Marsden, J. Cooper, D. Krige, 1992, Annals of neurology.

Mitochondrial myopathies: clinical defects.

J. Cooper, A. Schapira, A. Harding, 1990, Biochemical Society transactions.

Mitochondrial dysfunction and free radical damage in the Huntington R6/2 transgenic mouse

A H Schapira, S. Tabrizi, J. Cooper, 2000, Annals of neurology.

Central role and mechanisms of β‐cell dysfunction and death in friedreich ataxia–associated diabetes

A. Koeppen, C. Depondt, M. Pandolfo, 2012, Annals of neurology.

Mitochondrial function, GSH and iron in neurodegeneration and Lewy body diseases

C. Marsden, J. Cooper, D. Dexter, 1998, Journal of the Neurological Sciences.

Coordinating outcomes measurement in ataxia research: Do some widely used generic rating scales tick the boxes?

J. Hobart, J. Cooper, S. Cano, 2006, Movement disorders : official journal of the Movement Disorder Society.

Friedreich's ataxia: coenzyme Q10 and vitamin E therapy.

J. Cooper, A. Schapira, 2007, Mitochondrion.

Congenital encephalomyopathy and adult-onset myopathy and diabetes mellitus: different phenotypic associations of a new heteroplasmic mtDNA tRNA glutamic acid mutation.

I. Nelson, J. Cooper, A. Harding, 1995, American journal of human genetics.

Antioxidant treatment improves in vivo cardiac and skeletal muscle bioenergetics in patients with Friedreich's ataxia

A H Schapira, A. Blamire, D. Manners, 2001, Annals of neurology.

Role of Oxidative Damage in Friedreich's Ataxia

J. Cooper, J. Bradley, A. Schapira, 2004, Neurochemical Research.

Extensive Anti-CoA Immunostaining in Alzheimer’s Disease and Covalent Modification of Tau by a Key Cellular Metabolite Coenzyme A

I. Gout, J. Cooper, V. Filonenko, 2021, Frontiers in Cellular Neuroscience.

Free radical scavengers protect dopaminergic cell lines from apoptosis induced by complex I inhibitors.

A H Schapira, J. Cooper, A. Schapira, 1997, Brain research.

Cardiac energetics are abnormal in Friedreich ataxia patients in the absence of cardiac dysfunction and hypertrophy: an in vivo 31P magnetic resonance spectroscopy study.

A. Blamire, P. Styles, B. Rajagopalan, 2001, Cardiovascular research.

Mitochondrial DNA mutation underlying Leigh's syndrome: Clinical, pathological, biochemical, and genetic studies of a patient presenting with progressive myoclonic epilepsy

C. R. Kennedy, J. Cooper, A. Harding, 1994, Journal of the Neurological Sciences.

Glial activation precedes alpha-synuclein pathology in a mouse model of Parkinson’s disease

J. Cooper, J. Blesa, L. Alvarez-Erviti, 2020, Neuroscience Research.

Impaired Mitophagy and Protein Acetylation Levels in Fibroblasts from Parkinson’s Disease Patients

J. Cooper, J. M. Bravo-San Pedro, M. Niso-Santano, 2018, Molecular Neurobiology.

Mitochondrial function in neurodegeneration and ageing.

J. Cooper, A. Schapira, A. Schapira, 1992, Mutation research.

International cooperative ataxia rating scale (ICARS): Appropriate for studies of Friedreich's ataxia?

J. Hobart, J. Cooper, S. Cano, 2005, Movement disorders : official journal of the Movement Disorder Society.

DELETIONS OF MUSCLE MITOCHONDRIAL DNA

J. Cooper, A. Harding, I. Holt, 1988, The Lancet.

Friedreich's ataxia impact scale: A new measure striving to provide the flexibility required by today's studies

J. Hobart, J. Cooper, S. Cano, 2009, Movement disorders : official journal of the Movement Disorder Society.

α-Synuclein expression in HEK293 cells enhances the mitochondrial sensitivity to rotenone

A. H. V. Schapira, J. M. Cooper, S. Tabrizi, 2003, Neuroscience Letters.

Proteasomal inhibition causes loss of nigral tyrosine hydroxylase neurons

J. Cooper, J. Muddle, A. Schapira, 2006, Annals of neurology.

MITOCHONDRIAL-FUNCTION IN ALZHEIMERS-DISEASE

J. Cooper, A. Schapira, C. Wischik, 1993 .

Antibodies to human optic nerve in Leber's hereditary optic neuropathy

J. Cooper, A. Schapira, A. Harding, 1995, Journal of the Neurological Sciences.

Nitric oxide enhances MPP+ inhibition of complex I

J. Cooper, A. Schapira, M. Cleeter, 2001, FEBS letters.

Cellular Models of Huntington's Disease

J. Cooper, L. Jones, A. Schapira, 2002 .

Mitochondrial DNA transmission of the mitochondrial defect in Parkinson's disease

J. Cooper, J. Taanman, A. Schapira, 1998, Annals of neurology.

Overexpression of wild-type and mutant alpha-synuclein in a neuroblastoma cell line

A. Schapira, J. Cooper, L. Korlipara, 2002 .

A mitochondrial encephalomyopathy with specific deficiencies of two respiratory chain polypeptides and a circulating autoantibody to a mitochondrial matrix protein.

J. Cooper, A. Schapira, J. Morgan-Hughes, 1990, Brain : a journal of neurology.

The mitBASE human dataset structure

Flavio Licciulli, Marcella Attimonelli, Cecilia Saccone, 1998, Nucleic Acids Res..

Mitochondrial myopathies: genetic defects.

J. Cooper, A. Schapira, A. Harding, 1990, Biochemical Society transactions.

Pramipexole Reduces Phosphorylation of α-Synuclein at Serine-129

J. Cooper, K. Chau, A. Schapira, 2013, Journal of Molecular Neuroscience.

One-step immunoaffinity purification of complex I subunits from beef heart mitochondria.

J. Cooper, A. Schapira, J. Morgan-Hughes, 1992, Protein expression and purification.

Friedreich's ataxia impact scale: A new measure striving to provide the flexibility required by today's studies

J. Hobart, J. Cooper, S. Cano, 2009, Movement disorders : official journal of the Movement Disorder Society.

MitBASE: a comprehensive and integrated mitochondrial DNA database

Domenica D'Elia, Marcella Attimonelli, Cecilia Saccone, 1999, Nucleic Acids Res..