J. Pilewski

发表

AMPK agonists ameliorate sodium and fluid transport and inflammation in cystic fibrosis airway epithelial cells.

Simon C Watkins, Jay K Kolls, K. Hallows, 2010, American journal of respiratory cell and molecular biology.

Pseudomonas aeruginosa utilizes host polyunsaturated phosphatidylethanolamines to trigger theft-ferroptosis in bronchial epithelium

Simon C Watkins, Janet S. Lee, I. Bahar, 2018, The Journal of clinical investigation.

Molecular and functional properties of lung SP cells.

T. Betsuyaku, B. Stripp, P. Reynolds, 2007, American journal of physiology. Lung cellular and molecular physiology.

Biomarkers for cystic fibrosis drug development.

F. Accurso, J. Pilewski, A. Ziady, 2016, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Biomarkers for cystic fi brosis drug development

F. Accurso, J. Pilewski, A. Ziady, 2016 .

Long-term outcome of lung and heart-lung transplantation for idiopathic pulmonary arterial hypertension.

M. Zenati, J. Pilewski, Y. Toyoda, 2008, The Annals of thoracic surgery.

Insulin-like growth factor binding proteins 3 and 5 are overexpressed in idiopathic pulmonary fibrosis and contribute to extracellular matrix deposition.

J. Pilewski, C. Feghali-Bostwick, Li-xin Liu, 2005, The American journal of pathology.

Plasma Inflammatory Mediators Associated with Bone Metabolism in COPD

F. Sciurba, S. Greenspan, J. Pilewski, 2010, COPD.

Primary Uroepithelial Cultures

T. Sun, G. Apodaca, J. Pilewski, 1999, The Journal of Biological Chemistry.

Highly Effective Cystic Fibrosis Clinical Research Teams: Critical Success Factors

C. Goss, E. Nelson, J. Pilewski, 2014, Journal of General Internal Medicine.

Cystic Fibrosis Foundation consensus guidelines for the care of individuals with advanced cystic fibrosis lung disease.

C. Benden, J. Pilewski, B. Moshiree, 2020, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Lumacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease homozygous for F508del-CFTR.

J. Pilewski, T. Barto, D. Waltz, 2017, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Adults with Cystic Fibrosis

J. Pilewski, A. Venkat, 2011 .

Syndecan-2 Is a Novel Target of Insulin-Like Growth Factor Binding Protein-3 and Is Over-Expressed in Fibrosis

Y. Yamaguchi, J. Pilewski, C. Feghali-Bostwick, 2012, PloS one.

Chaperone displacement from mutant cystic fibrosis transmembrane conductance regulator restores its function in human airway epithelia

P. Robbins, J. Pilewski, R. Frizzell, 2008, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.

Gene therapy for airway diseases: continued progress toward identifying and overcoming barriers to efficiency.

J. Pilewski, 2002, American journal of respiratory cell and molecular biology.

Lung transplantation for pulmonary hypertension

J. Pilewski, H. Champion, M. George, 2011, Pulmonary circulation.

Na+ transport in normal and CF human bronchial epithelial cells is inhibited by BAY 39-9437.

J. Pilewski, R. Bridges, D. Devor, 2001, American journal of physiology. Lung cellular and molecular physiology.

Egr-1 Regulates Autophagy in Cigarette Smoke-Induced Chronic Obstructive Pulmonary Disease

Janet S. Lee, S. Ryter, R. Dhir, 2008, PloS one.

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation.

J. Clancy, S. Freedman, F. Accurso, 2010, The New England journal of medicine.

Role of IL-17A, IL-17F, and the IL-17 Receptor in Regulating Growth-Related Oncogene-α and Granulocyte Colony-Stimulating Factor in Bronchial Epithelium: Implications for Airway Inflammation in Cystic Fibrosis 1

J. Kolls, J. Pilewski, F. McAllister, 2005, The Journal of Immunology.

Mechanical Ventilation and Extracorporeal Membrane Oxygenation as a Bridging Strategy to Lung Transplantation: Significant Gains in Survival

A. Hayanga, J. Pilewski, K. Joubert, 2018, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Looking Beyond Respiratory Cultures: Microbiome‐Cytokine Signatures of Bacterial Pneumonia and Tracheobronchitis in Lung Transplant Recipients

Kevin J. McHugh, J. Alcorn, W. Nierman, 2016, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Prostasin expression is regulated by airway surface liquid volume and is increased in cystic fibrosis.

M. Myerburg, J. Pilewski, R. Frizzell, 2008, American journal of physiology. Lung cellular and molecular physiology.

Expression of integrin cell adhesion receptors during human airway epithelial repair in vivo.

J. Pilewski, S. Albelda, J. Latoche, 1997, The American journal of physiology.

Palliative care and location of death in decedents with idiopathic pulmonary fibrosis.

N. Kaminski, M. Saul, L. Hoffman, 2015, Chest.

Outcomes in Lung Transplant Recipients With Mycobacterium abscessus Infection: A 15-Year Experience From a Large Tertiary Care Center.

Yasir Hamad, J. Pilewski, J. D’Cunha, 2019, Transplantation proceedings.

Donor Smoking History and Age in Lung Transplantation: A Revisit

J. Pilewski, Y. Toyoda, C. Bermudez, 2013, Transplantation.

Epidemiology and Outcomes of Deep Surgical Site Infections Following Lung Transplantation

J. Pilewski, Y. Toyoda, C. Bermudez, 2013, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Activated CD47 promotes pulmonary arterial hypertension through targeting caveolin-1.

N. Rogers, J. Pilewski, B. Zuckerbraun, 2012, Cardiovascular research.

Provider Attitudes and Practices toward Sexual and Reproductive Health Care for Young Women with Cystic Fibrosis.

Kaleab Z. Abebe, G. Sawicki, S. Borrero, 2017, Journal of pediatric and adolescent gynecology.

Acidic Microenvironment Determines Antibiotic Susceptibility and Biofilm Formation of Pseudomonas aeruginosa

J. Pilewski, Y. Di, Q. Lin, 2021, Frontiers in Microbiology.

Cystic Fibrosis Acidic Microenvironment Determines Antibiotic Susceptibility and Biofilm Formation of Pseudomonas aeruginosa

J. Pilewski, Y. Di, Q. Lin, 2020, bioRxiv.

Lung Transplantation After Lung Volume Reduction Surgery

J. Pilewski, S. Gilbert, C. Bermudez, 2013, Transplantation.

Advanced Lung Disease and Lung Transplantation 2-1-2011 The HLA Class II Allele Allele DRB 1 * 15 is over-represented in patients with Idiopathic Pulmonary Fibrosis

I. Noth, G. Rosen, F. Sciurba, 2013 .

The HLA Class II Allele DRB1*1501 Is Over-Represented in Patients with Idiopathic Pulmonary Fibrosis

I. Noth, G. Rosen, F. Sciurba, 2011, PloS one.

The HLA Class II Allele DRB 1 * 1501 Is Over-Represented in Patients with Idiopathic Pulmonary Fibrosis

I. Noth, G. Rosen, F. Sciurba, 2011 .

Cellular and Humoral Autoreactivity in Idiopathic Pulmonary Fibrosis1

N. Kaminski, A. Choi, J. Pilewski, 2007, The Journal of Immunology.

Insulin-like growth factor-binding protein-5 induces pulmonary fibrosis and triggers mononuclear cellular infiltration.

A. Choi, T. Oury, J. Pilewski, 2006, The American journal of pathology.

Intracellular Heat Shock Protein 70 Deficiency in Pulmonary Fibrosis.

K. Veraldi, M. Rojas, J. Pilewski, 2019, American journal of respiratory cell and molecular biology.

Enhancing Autophagy with Drugs or Lung-directed Gene Therapy Reverses the Pathological Effects of Respiratory Epithelial Cell Proteinopathy*

A. M. Houghton, J. Alcorn, N. Brunetti‐Pierri, 2015, The Journal of Biological Chemistry.

Insulin-like growth factor (IGF)-II- mediated fibrosis in pathogenic lung conditions

J. Pilewski, C. Feghali-Bostwick, S. Garrett, 2019, PloS one.

The HLA Class II Allele Allele DRB 1 * 15 is over-represented in patients with Idiopathic Pulmonary Fibrosis

I. Noth, G. Rosen, F. Sciurba, 2017 .

Staphylococcus aureus Biofilm Growth on Cystic Fibrosis Airway Epithelial Cells Is Enhanced during Respiratory Syncytial Virus Coinfection

M. Myerburg, J. Pilewski, J. Bomberger, 2018, mSphere.

Extracorporeal membrane oxygenation for primary graft dysfunction after lung transplantation: long-term survival.

J. Pilewski, Y. Toyoda, C. Bermudez, 2009, The Annals of thoracic surgery.

Type‐1 immunity and endogenous immune regulators predominate in the airway transcriptome during chronic lung allograft dysfunction

Joyce S Lee, J. Golden, W. Xu, 2020, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Early Major Neurologic Complications After Lung Transplantation: Incidence, Risk Factors, and Outcome

R. Sclabassi, J. Pilewski, C. Bermudez, 2013, Transplantation.

De novo donor-specific HLA antibodies are associated with early and high-grade bronchiolitis obliterans syndrome and death after lung transplantation.

S. Yousem, J. Pilewski, C. Ensor, 2014, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Call for Changes in Lung Allocation to Reduce Transplant Wait-List Mortality for Cystic Fibrosis

J. Pilewski, E. Nolley, 2019, American journal of respiratory and critical care medicine.

Pharmacological modulation of ion transport across wild-type and DeltaF508 CFTR-expressing human bronchial epithelia.

J. Pilewski, R. Bridges, D. Devor, 2000, American journal of physiology. Cell physiology.

Thrombospondin-1 triggers macrophage IL-10 production and promotes resolution of experimental lung injury

Janet S. Lee, M. Rosengart, D. Stolz, 2013, Mucosal Immunology.

Successful adenovirus-mediated gene transfer in an in vivo model of human malignant mesothelioma.

J. Pilewski, H. Hwang, W. Smythe, 1994, The Annals of thoracic surgery.

Expression of endothelial cell adhesion molecules in human bronchial xenografts.

J. Pilewski, R. Panettieri, L. Kaiser, 1994, American journal of respiratory and critical care medicine.

Aldosterone and Epithelial Na Channels Defining an inhibitory domain in the-subunit of the epithelial sodium channel

M. Myerburg, J. Pilewski, R. Hughey, 2007 .

CALL FOR PAPERS Aldosterone and Epithelial Na (cid:1) Channels Deﬁning an inhibitory domain in the (cid:2) -subunit of the epithelial sodium channel

M. Myerburg, J. Pilewski, R. Hughey, 2007 .

Comprehensive analysis of gene expression on GOLD-2 Versus GOLD-0 smokers reveals novel genes important in the pathogenesis of COPD.

Simon C Watkins, N. Kaminski, A. Choi, 2006, Proceedings of the American Thoracic Society.

Anti-Human Leukocyte Antigen Antibodies, Vascular C4d Deposition and Increased Soluble C4d in Broncho-Alveolar Lavage of Lung Allografts

W. Baldwin, S. Yousem, J. Pilewski, 2008, Transplantation.

Efficacy of extracorporeal membrane oxygenation as a bridge to lung transplantation.

J. Pilewski, Y. Toyoda, C. Bermudez, 2013, The Journal of thoracic and cardiovascular surgery.

Impaired Cytomegalovirus Immunity in Idiopathic Pulmonary Fibrosis Lung Transplant Recipients with Short Telomeres

P. Shah, J. Pilewski, Yingze Zhang, 2019, American journal of respiratory and critical care medicine.

Associations between demographic characteristics and unmet supportive care needs in adults with cystic fibrosis

C. Goss, Kwonho Jeong, R. Arnold, 2019, BMJ Supportive & Palliative Care.

Organ Transplantation for Cystic Fibrosis

J. Pilewski, M. Morrell, S. Kiel, 2019, Seminars in Respiratory and Critical Care Medicine.

Lung Transplantation for Cystic Fibrosis.

J. Pilewski, M. Morrell, 2016, Clinics in chest medicine.

Antiinflammatory effects of bromodomain and extraterminal domain inhibition in cystic fibrosis lung inflammation.

Wei Chen, S. Wenzel, M. Myerburg, 2016, JCI insight.

Role of insulin-like growth factor binding protein-3 in allergic airway remodeling.

S. Wenzel, N. Jarjour, S. Balzar, 2009, American journal of respiratory and critical care medicine.

Hepatocyte growth factor and other fibroblast secretions modulate the phenotype of human bronchial epithelial cells.

M. Myerburg, J. Pilewski, C. Feghali-Bostwick, 2007, American journal of physiology. Lung cellular and molecular physiology.

Acute regulation of the epithelial sodium channel in airway epithelia by proteases and trafficking.

M. Myerburg, J. Pilewski, M. Butterworth, 2010, American journal of respiratory cell and molecular biology.

Interleukin-17A induces bicarbonate secretion in normal human bronchial epithelial cells.

J. Kolls, J. Pilewski, R. Lee, 2009, American journal of physiology. Lung cellular and molecular physiology.

Engineered cationic antimicrobial peptide (eCAP) prevents Pseudomonas aeruginosa biofilm growth on airway epithelial cells.

J. Pilewski, R. Montelaro, J. Bomberger, 2016, The Journal of antimicrobial chemotherapy.

Cystic fibrosis foundation consensus statements for the care of cystic fibrosis lung transplant recipients.

P. Shah, J. Pilewski, G. Visner, 2021, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Cell adhesion molecules in asthma: homing, activation, and airway remodeling.

J. Pilewski, S. Albelda, 1995, American journal of respiratory cell and molecular biology.

Atrial arrhythmias after lung transplantation: Incidence and risk factors in 652 lung transplant recipients.

J. Luketich, J. Pilewski, E. Chan, 2016, The Journal of thoracic and cardiovascular surgery.

Microbiome in lung explants of idiopathic pulmonary fibrosis: a case–control study in patients with end-stage fibrosis

B. Methé, Kelvin Li, K. Veraldi, 2017, Thorax.

Lack of Association Between ß-herpesvirus Infection and Bronchiolitis Obliterans Syndrome in Lung Transplant Recipients in the Era of Antiviral Prophylaxis

O. Manuel, Deepali Kumar, A. Humar, 2009, Transplantation.

Rescue alemtuzumab for refractory acute cellular rejection and bronchiolitis obliterans syndrome after lung transplantation

J. Pilewski, C. Ensor, J. D’Cunha, 2017, Clinical transplantation.

Lung Transplantation With Lungs From Older Donors: Recipient and Surgical Factors Affect Outcomes

J. Luketich, J. Pilewski, Y. Toyoda, 2014, Transplantation.

Delayed chest closure after lung transplantation: techniques, outcomes, and strategies.

J. Luketich, J. Pilewski, C. Bermudez, 2014, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Combining tricuspid valve repair with double lung transplantation in patients with severe pulmonary hypertension, tricuspid regurgitation, and right ventricular dysfunction.

J. Pilewski, Y. Toyoda, P. Bonde, 2011, Chest.

Postdeposition dispersion of aerosol medications using surfactant carriers.

T. Corcoran, J. Pilewski, R. Tilton, 2008, Journal of aerosol medicine and pulmonary drug delivery.

Interleukin-17 A induces bicarbonate secretion in normal human bronchial epithelial cells

J. Kolls, J. Pilewski, R. Lee, 2009 .

Finally, mice with CF lung disease

J. Pilewski, R. Frizzell, 2004, Nature Medicine.

Autoantibodies in patients with chronic obstructive pulmonary disease.

F. Sciurba, L. Otterbein, J. Pilewski, 2008, American journal of respiratory and critical care medicine.

UTP inhibits Na+ absorption in wild-type and DeltaF508 CFTR-expressing human bronchial epithelia.

J. Pilewski, D. Devor, 1999, The American journal of physiology.

UTP inhibits Na+ absorption in wild-type and ΔF508 CFTR-expressing human bronchial epithelia.

J. Pilewski, D. Devor, 1999, American journal of physiology. Cell physiology.

Surgical Strategy for Lung Transplantation in Adults With Small Chests: Lobar Transplant Versus a Pediatric Donor

J. Luketich, A. Hayanga, J. Pilewski, 2016, Transplantation.

Impact of graft volume reduction for oversized grafts after lung transplantation on outcome in recipients with end-stage restrictive pulmonary diseases.

J. Pilewski, Y. Toyoda, C. Bermudez, 2009, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Adhesion molecules in the lung. An overview.

J. Pilewski, S. Albelda, 1993, The American review of respiratory disease.

Routine deep vein thrombosis screening after lung transplantation: Incidence and risk factors.

J. Pilewski, J. D’Cunha, P. Sanchez, 2019, The Journal of thoracic and cardiovascular surgery.

Lobar lung transplantation: a relevant surgical option in the current era of lung allocation score.

J. Luketich, J. Pilewski, Ashraf Abou el ela, 2013, The Annals of thoracic surgery.

Age-specific complications among lung transplant recipients 60 years and older.

J. Pilewski, Y. Toyoda, C. Bermudez, 2011, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Inflammation in Cystic Fibrosis Epithelium : Implications for Airway Colony-Stimulating Factor in Bronchial and Granulocyte α Oncogene-Receptor in Regulating Growth-Related Role of IL-17 A , IL-17 F , and the IL-17

J. Kolls, J. Pilewski, F. McAllister, 2005 .

First Successful Lung Transplantation for Sickle Cell Disease with Severe Pulmonary Arterial Hypertension and Pulmonary Veno-Occlusive Disease

M. Gladwin, S. Yousem, J. Pilewski, 2013, Pulmonary circulation.

Antireflux surgery preserves lung function in patients with gastroesophageal reflux disease and end-stage lung disease before and after lung transplantation.

J. Hunter, J. Luketich, J. Pilewski, 2011, Archives of surgery.

Human Lung Resident Macrophages Co-localize with and Provide Co-stimulation to PD1hi Tissue Resident Memory T Cells.

M. Rojas, M. Myerburg, J. Pilewski, 2020, American journal of respiratory and critical care medicine.

Intrapulmonary Disposition of Amphotericin B After Aerosolized Delivery of Amphotericin B Lipid Complex (Abelcet; ABLC) in Lung Transplant Recipients

D. Pakstis, D. Paterson, K. Shutt, 2010, Transplantation.

Challenges in the use of highly effective modulator treatment for cystic fibrosis.

J. Pilewski, J. Taylor-Cousar, K. Ramos, 2021, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Effect of lumacaftor-ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis: Results from the PROSPECT MCC sub-study.

T. Corcoran, J. Pilewski, A. Ceppe, 2021, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Nitrite modulates bacterial antibiotic susceptibility and biofilm formation in association with airway epithelial cells.

M. Gladwin, J. Pilewski, J. Bomberger, 2014, Free radical biology & medicine.

Effect of ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis patients with G551D-CFTR.

T. Corcoran, M. Myerburg, J. Pilewski, 2018, JCI insight.

Preoperative Evaluation and Preparation for Lung Transplantation

J. Pilewski, M. Morrell, 2017 .

Extracorporeal membrane oxygenation as a bridge to lung transplant: midterm outcomes.

J. Pilewski, Y. Toyoda, A. Boujoukos, 2011, The Annals of thoracic surgery.

Comprehensive gene expression profiles reveal pathways related to the pathogenesis of chronic obstructive pulmonary disease.

Naftali Kaminski, Simon C Watkins, Frank C Sciurba, 2004, Proceedings of the National Academy of Sciences of the United States of America.

Immunogenicity of COVID-19 Vaccination in Immunocompromised Patients: An Observational, Prospective Cohort Study Interim Analysis

J. Luketich, J. Mellors, D. Angus, 2021, medRxiv.

ICAM-1 expression on bronchial epithelium after recombinant adenovirus infection.

J. Pilewski, J. Wilson, S. Albelda, 1995, American journal of respiratory cell and molecular biology.

Posaconazole Serum Concentrations among Cardiothoracic Transplant Recipients: Factors Impacting Trough Levels and Correlation with Clinical Response to Therapy

J. Pilewski, Y. Toyoda, C. Bermudez, 2010, Antimicrobial Agents and Chemotherapy.

Vitamin D supplementation decreases Aspergillus fumigatus specific Th2 responses in CF patients with aspergillus sensitization: a phase one open-label study

J. Alcorn, J. Celedón, J. Kolls, 2015, Asthma Research and Practice.

Microbiology, safety, and pharmacokinetics of aztreonam lysinate for inhalation in patients with cystic fibrosis

R. Gibson, J. Pilewski, S. Mcnamara, 2006, Pediatric pulmonology.

Selective toxicity of engineered lentivirus lytic peptides in a CF airway cell model

Simon C Watkins, D. Stolz, J. Pilewski, 2003, Peptides.

Platelets inhibit apoptotic lung epithelial cell death and protect mice against infection-induced lung injury

Janet S. Lee, R. Mallampalli, A. Ray, 2019, Blood advances.

Insulin Therapy to Improve BMI in Cystic Fibrosis–Related Diabetes Without Fasting Hyperglycemia

J. Pilewski, T. Liou, E. Tullis, 2009, Diabetes Care.

Five-year outcomes with alemtuzumab induction after lung transplantation.

M. Dew, A. D. DeVito Dabbs, J. Pilewski, 2011, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Vitamin D 3 attenuates Th 2 responses to Aspergillus fumigatus mounted by CD 4 + T cells from cystic fibrosis patients with allergic bronchopulmonary aspergillosis

H. Rockette, J. Alcorn, A. Ray, 2010 .

Interleukin-22 Inhibits Respiratory Syncytial Virus Production by Blocking Virus-Mediated Subversion of Cellular Autophagy

S. Wenzel, A. Ray, P. Ray, 2020, iScience.

The CFTR trafficking mutation F508del inhibits the constitutive activity of SLC26A9.

D. Madden, J. Pilewski, R. Frizzell, 2017, American journal of physiology. Lung cellular and molecular physiology.

Up-regulation of AMP-activated Kinase by Dysfunctional Cystic Fibrosis Transmembrane Conductance Regulator in Cystic Fibrosis Airway Epithelial Cells Mitigates Excessive Inflammation*

J. Clancy, P. Reynolds, K. Hallows, 2006, Journal of Biological Chemistry.

Adenovirus-mediated gene transfer to human bronchial submucosal glands using xenografts.

J. Bavaria, J. Pilewski, J. Wilson, 1995, The American journal of physiology.

Prolonged Use of the Hemolung Respiratory Assist System as a Bridge to Redo Lung Transplantation.

J. Pilewski, M. Fan, C. Bermudez, 2015, The Annals of thoracic surgery.

Update on Lung Transplantation for Cystic Fibrosis.

J. Pilewski, 2022, Clinics in chest medicine.

Long-Term Ivacaftor in People Aged 6 Years and Older with Cystic Fibrosis with Ivacaftor-Responsive Mutations

J. Nick, J. Pilewski, R. Moss, 2020, Pulmonary Therapy.

Airway Surface Liquid Volume Regulates ENaC by Altering the Serine Protease-Protease Inhibitor Balance

M. Myerburg, J. Pilewski, R. Frizzell, 2006, Journal of Biological Chemistry.

Simkania Negevensis in Bronchoalveolar Lavage of Lung Transplant Recipients: A Possible Association with Acute Rejection

D. Greenberg, D. Paterson, D. Wolf, 2007, Transplantation.

High IFN-g and low SLPI mark severe asthma in mice and humans

S. Wenzel, J. Milošević, A. Ray, 2019 .

Vitamin D3 attenuates Th2 responses to Aspergillus fumigatus mounted by CD4+ T cells from cystic fibrosis patients with allergic bronchopulmonary aspergillosis.

H. Rockette, J. Alcorn, A. Ray, 2010, The Journal of clinical investigation.

Prospective, Observational Study of Voriconazole Therapeutic Drug Monitoring among Lung Transplant Recipients Receiving Prophylaxis: Factors Impacting Levels of and Associations between Serum Troughs, Efficacy, and Toxicity

J. Pilewski, Y. Toyoda, C. Bermudez, 2012, Antimicrobial Agents and Chemotherapy.

Closing the Loop: Engaging Leaders and Front-Line Physicians to Promote Physician Wellness.

J. Pilewski, B. McVerry, I. Barbash, 2019, Annals of the American Thoracic Society.

Effect of aerosolized antipseudomonals on Pseudomonas positivity and bronchiolitis obliterans syndrome after lung transplantation

K. M. Robinson, J. Pilewski, C. Ensor, 2017, Transplant infectious disease : an official journal of the Transplantation Society.

Quantitative imaging of airway liquid absorption in cystic fibrosis

R. Parker, T. Corcoran, M. Myerburg, 2014, European Respiratory Journal.

Liquid hyper-absorption as a cause of increased DTPA clearance in the cystic fibrosis airway

T. Corcoran, M. Myerburg, J. Pilewski, 2013, EJNMMI Research.

The Epithelial Na+ Channel Is Inhibited by a Peptide Derived from Proteolytic Processing of Its α Subunit*

J. Pilewski, R. Hughey, J. B. Bruns, 2006, Journal of Biological Chemistry.

Sexual and reproductive health behaviors and experiences reported by young women with cystic fibrosis.

Kaleab Z. Abebe, G. Sawicki, S. Borrero, 2018, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Multiprobe Nuclear Imaging of the Cystic Fibrosis Lung as a Biomarker of Therapeutic Effect.

T. Corcoran, M. Myerburg, J. Pilewski, 2019, Journal of aerosol medicine and pulmonary drug delivery.

IL-22 mediates mucosal host defense against Gram-negative bacterial pneumonia

M. Fei, Y. Iwakura, M. Myerburg, 2008, Nature Medicine.

Hepatocyte growth factor promotes tumor growth in a novel in vivo model of human lung cancer.

J. Siegfried, J. Pilewski, T. S. Bumbalo, 2001, American journal of respiratory cell and molecular biology.

Leukocyte recruitment into human skin transplanted onto severe combined immunodeficient mice induced by TNF-alpha is dependent on E-selectin.

H. DeLisser, J. Pilewski, S. Albelda, 1994, Journal of immunology.

High mortality rates among solid organ transplant recipients infected with extensively drug-resistant Acinetobacter baumannii: using in vitro antibiotic combination testing to identify the combination of a carbapenem and colistin as an effective treatment regimen.

J. Pilewski, Y. Toyoda, Y. Doi, 2011, Diagnostic microbiology and infectious disease.

Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines.

J. Pilewski, A. Faro, Patrick J. Smith, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Provider and Patient Attitudes Regarding Sexual Health in Young Women With Cystic Fibrosis

S. Borrero, J. Pilewski, D. Orenstein, 2016, Pediatrics.

Sexual and reproductive health care utilization and preferences reported by young women with cystic fibrosis.

Kaleab Z. Abebe, G. Sawicki, S. Borrero, 2018, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Aerosol Deposition of Lipid Complex Amphotericin‐B (Abelcet) in Lung Transplant Recipients

D. Paterson, J. Pilewski, K. McCurry, 2006, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Effect of apical hyperosmotic sodium challenge and amiloride on sodium transport in human bronchial epithelial cells from cystic fibrosis donors.

S. Randell, J. Pilewski, R. Bridges, 2013, American journal of physiology. Cell physiology.

Elevated CXCL10 (IP-10) in Bronchoalveolar Lavage Fluid Is Associated With Acute Cellular Rejection After Human Lung Transplantation

W. Liles, S. Keshavjee, J. Kolls, 2014, Transplantation.

Prospective Evaluation of Coronavirus Disease 2019 (COVID-19) Vaccine Responses Across a Broad Spectrum of Immunocompromising Conditions: the COVID-19 Vaccination in the Immunocompromised Study (COVICS)

D. Angus, J. Luketich, M. Schwartz, 2022, Clinical Infectious Diseases: An Official Publication of the Infectious Diseases Society of America.

Symptom Burden and Unmet Existential Needs in Adults With Cystic Fibrosis

Kwonho Jeong, R. Arnold, J. Pilewski, 2019, Western journal of nursing research.

Absorptive clearance of DTPA as an aerosol-based biomarker in the cystic fibrosis airway

T. Corcoran, M. Myerburg, J. Pilewski, 2009, European Respiratory Journal.

Human/severe combined immunodeficient mouse chimeras. An experimental in vivo model system to study the regulation of human endothelial cell-leukocyte adhesion molecules.

M. Herlyn, J. Pilewski, S. Albelda, 1993, The Journal of clinical investigation.

Lung transplantation for pulmonary alveolar microlithiasis.

J. Pilewski, Y. Toyoda, C. Bermudez, 2010, The Journal of thoracic and cardiovascular surgery.

Lung Transplant in Patients with Scleroderma Compared with Pulmonary Fibrosis. Short- and Long-Term Outcomes.

M. Dew, J. Pilewski, T. Richards, 2016, Annals of the American Thoracic Society.

Voriconazole exposure and geographic location are independent risk factors for squamous cell carcinoma of the skin among lung transplant recipients.

J. Pilewski, Y. Toyoda, C. Bermudez, 2010, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Voriconazole Prophylaxis in Lung Transplant Recipients

D. Pakstis, D. Paterson, K. Shutt, 2006, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Patients with cystic fibrosis have inducible IL-17+IL-22+ memory cells in lung draining lymph nodes.

A. Ray, P. Ray, J. Kolls, 2013, The Journal of allergy and clinical immunology.

Comparison of an Aspergillus real-time polymerase chain reaction assay with galactomannan testing of bronchoalvelolar lavage fluid for the diagnosis of invasive pulmonary aspergillosis in lung transplant recipients.

D. Pakstis, J. Pilewski, Y. Toyoda, 2011, Clinical infectious diseases : an official publication of the Infectious Diseases Society of America.

Aspergillus Galactomannan Antigen in the Bronchoalveolar Lavage Fluid for the Diagnosis of Invasive Aspergillosis in Lung Transplant Recipients

Nina Singh, D. Paterson, J. Pilewski, 2007, Transplantation.

Experience With Immune Monitoring in Lung Transplant Recipients: Correlation of Low Immune Function With Infection

D. Pakstis, K. Shutt, J. Pilewski, 2009, Transplantation.

Impact of various infectious syndromes on the immune function profile in lung transplant recipients

D. Paterson, J. Pilewski, K. McCurry, 2007 .

66: Risk of pulmonary aspergillosis after bronchial stent placement in lung transplant (LTx) recipients

J. Pilewski, K. McCurry, K. Raza, 2006 .

Ganciclovir-Resistant Cytomegalovirus Infections among Lung Transplant Recipients Are Associated with Poor Outcomes despite Treatment with Foscarnet-Containing Regimens

J. Pilewski, Y. Toyoda, C. Bermudez, 2013, Antimicrobial Agents and Chemotherapy.

Lung transplantation for patients with high lung allocation score: single-center experience.

J. Pilewski, Y. Toyoda, C. Bermudez, 2012, The Annals of thoracic surgery.

Detrimental Association of Hypogammaglobulinemia With Chronic Lung Allograft Dysfunction and Death Is Not Mitigated by On-Demand Immunoglobulin G Replacement After Lung Transplantation

J. Pilewski, C. Ensor, J. D’Cunha, 2018, Progress in transplantation.

A Prospective Observational Study of Hypogammaglobulinemia in the First Year After Lung Transplantation

D. Landsittel, J. Pilewski, C. Ensor, 2018, Transplantation direct.

Subcutaneous IgG replacement therapy is safe and well tolerated in lung transplant recipients.

J. Pilewski, F. Silveira, M. Crespo, 2013, International immunopharmacology.

Simkania negevensis and acute cellular rejection in lung transplant recipients

W. Liles, S. Keshavjee, J. Kolls, 2015, Clinical transplantation.

Post-transplant colonization with non-Aspergillus molds and risk of development of invasive fungal disease in lung transplant recipients.

D. Paterson, J. Pilewski, K. McCurry, 2008, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Staphylococcus aureus infections in the early period after lung transplantation: epidemiology, risk factors, and outcomes.

J. Pilewski, Y. Toyoda, C. Bermudez, 2012, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Role of CFTR in airway disease.

J. Pilewski, R. Frizzell, R A Frizzell, 1999, Physiological reviews.

Elexacaftor-Tezacaftor- Ivacaftor improves sinonasal outcomes in cystic fibrosis.

J. Pilewski, A. Kimple, Amber D. Shaffer, 2022, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

SLC26A9 is a constitutively active, CFTR-regulated anion conductance in human bronchial epithelia

J. Pilewski, R. Frizzell, Ruilin Zhang, 2009, The Journal of general physiology.

Glycosylation differences between a cystic fibrosis and rescued airway cell line are not CFTR dependent.

O. Weisz, J. Pilewski, W. Hill, 1997, American journal of physiology. Lung cellular and molecular physiology.

Glycosylation differences between a cystic fibrosis and rescued airway cell line are not CFTR dependent.

O. Weisz, J. Pilewski, X. Jiang, 1997, The American journal of physiology.

c-Cbl Facilitates Endocytosis and Lysosomal Degradation of Cystic Fibrosis Transmembrane Conductance Regulator in Human Airway Epithelial Cells*

D. Stolz, S. Ye, J. Pilewski, 2010, The Journal of Biological Chemistry.

Thrombospondin-1 protects against pathogen-induced lung injury by limiting extracellular matrix proteolysis.

Janet S. Lee, Jongyoon Han, V. Cooper, 2018, JCI insight.

HLA-C and KIR permutations influence chronic obstructive pulmonary disease risk

A. Gaggar, G. Criner, M. Cho, 2021, JCI insight.

CX3CL1 up-regulation is associated with recruitment of CX3CR1+ mononuclear phagocytes and T lymphocytes in the lungs during cigarette smoke-induced emphysema.

Simon C Watkins, Janet S. Lee, A. Choi, 2008, The American journal of pathology.

Insulin‐like growth factor binding protein‐4 exerts antifibrotic activity by reducing levels of connective tissue growth factor and the C‐X‐C chemokine receptor 4

S. Hoffman, J. Pilewski, C. Feghali-Bostwick, 2019, FASEB bioAdvances.

Localized expression of tenascin in systemic sclerosis-associated pulmonary fibrosis and its regulation by insulin-like growth factor binding protein 3.

T. Medsger, K. Veraldi, J. Pilewski, 2012, Arthritis and rheumatism.

Lung tissues in patients with systemic sclerosis have gene expression patterns unique to pulmonary fibrosis and pulmonary hypertension.

James Lyons-Weiler, J. Pilewski, R. Jordan, 2011, Arthritis and rheumatism.

Gene therapy approaches for inherited and acquired lung diseases.

D. Curiel, J. Pilewski, S. Albelda, 1996, American journal of respiratory cell and molecular biology.

Expression of mRNA for gastrin-releasing peptide receptor by human bronchial epithelial cells. Association with prolonged tobacco exposure and responsiveness to bombesin-like peptides.

J. Siegfried, J. Pilewski, J. D. Hunt, 1997, American journal of respiratory and critical care medicine.

Cytomegalovirus disease among donor-positive/recipient-negative lung transplant recipients in the era of valganciclovir prophylaxis.

J. Pilewski, Y. Toyoda, C. Bermudez, 2010, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

ytomegalovirus disease among donor-positive / ecipient-negative lung transplant recipients in the ra of valganciclovir prophylaxis

J. Pilewski, Y. Toyoda, C. Bermudez, 2022 .

Elastase Activity from Pseudomonas aeruginosa Respiratory Isolates and ICU Mortality.

Janet S. Lee, J. Pilewski, J. Bomberger, 2021, Chest.

A polymorphism linked to elevated levels of interferon-γ is associated with an increased risk of cytomegalovirus disease among Caucasian lung transplant recipients at a single center.

J. Pilewski, Y. Toyoda, J. Bhama, 2011, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Distribution of integrin cell adhesion receptors on normal bronchial epithelial cells and lung cancer cells in vitro and in vivo.

J. Pilewski, S. Albelda, C. Buck, 1993, American journal of respiratory cell and molecular biology.

E3 Ligase Subunit Fbxo15 and PINK1 Kinase Regulate Cardiolipin Synthase 1 Stability and Mitochondrial Function in Pneumonia

Bill B. Chen, R. Mallampalli, A. Ray, 2014, Cell reports.

Prevalence of unmet palliative care needs in adults with cystic fibrosis.

Kwonho Jeong, R. Arnold, J. Pilewski, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Donor-specific antibody characteristics, including persistence and complement-binding capacity, increase risk for chronic lung allograft dysfunction.

J. Pilewski, C. Ensor, M. Morrell, 2020, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Epithelial Na+ Channels Are Fully Activated by Furin- and Prostasin-dependent Release of an Inhibitory Peptide from the γ-Subunit*

O. Weisz, J. Pilewski, R. Hughey, 2007, Journal of Biological Chemistry.

CD4+ T cell lymphopenia and dysfunction in severe COVID-19 disease is autocrine TNF-α/TNFRI-dependent

Bill B. Chen, M. Saul, J. Pilewski, 2021, bioRxiv.

Targeting the IL-22/IL-22BP axis enhances tight junctions and reduces inflammation during influenza infection

N. Mclaughlin, J. Kolls, J. Pilewski, 2019, Mucosal Immunology.

Defining an inhibitory domain in the alpha-subunit of the epithelial sodium channel.

M. Myerburg, J. Pilewski, R. Hughey, 2008, American journal of physiology. Renal physiology.

High IFN-γ and low SLPI mark severe asthma in mice and humans.

S. Wenzel, J. Milošević, A. Ray, 2015, The Journal of clinical investigation.

Intracellular Na+ Regulates Epithelial Na+ Channel Maturation*

M. Myerburg, J. Pilewski, R. Hughey, 2015, The Journal of Biological Chemistry.

Exploring the meaning of chronic rejection after lung transplantation and its impact on clinical management and caregiving.

R. Arnold, A. D. DeVito Dabbs, J. Pilewski, 2010, Journal of pain and symptom management.

Successful Outcome of Human Metapneumovirus (hMPV) Pneumonia in a Lung Transplant Recipient Treated With Intravenous Ribavirin

C. Rinaldo, D. Paterson, J. Pilewski, 2007, The Journal of Heart and Lung Transplantation.

ATP12A promotes mucus dysfunction during Type 2 airway inflammation

S. Wenzel, T. Corcoran, M. Myerburg, 2018, Scientific Reports.

Malignancies incidentally detected at lung transplantation: radiologic and pathologic features.

S. Dacic, J. Pilewski, D. Strollo, 2013, AJR. American journal of roentgenology.

Gastrin-releasing peptide receptor expression in non-cancerous bronchial epithelia is associated with lung cancer: a case-control study

York E Miller, Yongli Shuai, Y. Miller, 2012, Respiratory Research.

Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del‐CFTR or F508del/G551D‐CFTR

J. Pilewski, S. Donaldson, J. Davies, 2018, American journal of respiratory and critical care medicine.

Allele-specific transactivation of matrix metalloproteinase 7 by FOXA2 and correlation with plasma levels in idiopathic pulmonary fibrosis.

Simon C Watkins, N. Kaminski, A. Choi, 2012, American journal of physiology. Lung cellular and molecular physiology.

Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis.

R. Tal-Singer, E. Kerem, J. Pilewski, 2013, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Outcomes of intraoperative venoarterial extracorporeal membrane oxygenation versus cardiopulmonary bypass during lung transplantation.

J. Pilewski, A. Shiose, T. Richards, 2014, The Annals of thoracic surgery.

Lung Transplantation in Patients With Prior Cardiothoracic Surgical Procedures

J. Pilewski, Y. Toyoda, C. Bermudez, 2012, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Plasma B Lymphocyte Stimulator and B Cell Differentiation in Idiopathic Pulmonary Fibrosis Patients

F. Sciurba, N. Kaminski, L. Otterbein, 2013, The Journal of Immunology.

Patients with idiopathic pulmonary fibrosis with antibodies to heat shock protein 70 have poor prognoses.

F. Sciurba, N. Kaminski, L. Otterbein, 2013, American journal of respiratory and critical care medicine.

Transcriptomic responses to Ivacaftor and prediction of Ivacaftor clinical responsiveness.

Wei Chen, J. Kolls, J. Pilewski, 2019, American journal of respiratory cell and molecular biology.

Stimulation of Cl(-) secretion by chlorzoxazone.

J. Pilewski, A. K. Singh, Ashvani K. Singh, 2000, The Journal of pharmacology and experimental therapeutics.

Stimulation of Cl 2 Secretion by Chlorzoxazone 1

J. Pilewski, Ashvani K. Singh, R. Bridges, 2000 .

T lymphocytes adhere to airway smooth muscle cells via integrins and CD44 and induce smooth muscle cell DNA synthesis

E. Puré, J. Pilewski, R. Panettieri, 1994, The Journal of experimental medicine.

Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation

J. Clancy, M. Ballmann, F. Accurso, 2011, Thorax.

Position paper: Models of post-transplant care for individuals with cystic fibrosis.

M. Anstead, J. Pilewski, J. Blatter, 2023, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

CFTR Modulators to the Rescue of Individuals with Cystic Fibrosis and Advanced Lung Disease

M. Myerburg, J. Pilewski, 2021, American journal of respiratory and critical care medicine.

Clinical predictors of cystic fibrosis chronic rhinosinusitis severity

J. Pilewski, S. Nouraie, J. Bomberger, 2019, International forum of allergy & rhinology.

Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis.

John R Yates, Gerard Manning, Yoshihiro Matsumura, 2010, Nature chemical biology.

CALL FOR PAPERS Aldosterone and Epithelial Na (cid:1) Channels Deﬁning an inhibitory domain in the (cid:2) -subunit of the epithelial sodium channel

M. Myerburg, J. Pilewski, R. Hughey, 2007 .

Modulation of adhesion molecules by cytokinesin vivo using human/severe combined immunodeficient (SCID) mouse chimeras

John S. Williams, J. Pilewski, S. Albelda, 1995, Journal of Clinical Immunology.

Successful lung transplantation from a hepatitis C RNA-positive donor to a hepatitis C treatment-experienced recipient with cystic fibrosis.

J. Pilewski, J. D’Cunha, M. Morrell, 2019, The Journal of thoracic and cardiovascular surgery.

Successful lung transplantation in an octogenarian.

J. Pilewski, Y. Toyoda, C. Bermudez, 2010, The Journal of thoracic and cardiovascular surgery.

Nature and correlates of post-traumatic stress symptomatology in lung transplant recipients.

C. Goss, M. Dew, A. D. DeVito Dabbs, 2013, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Long‐Term Follow‐up of a Randomized Controlled Trial Evaluating a Mobile Health Intervention for Self‐Management in Lung Transplant Recipients

D. Landsittel, M. Dew, A. D. DeVito Dabbs, 2017, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Airway Transcriptome Analysis and Immune Proteome Profiling of the Lung Allograft Reveals Novel Immune Signatures in Chronic Lung Allograft Dysfunction

J. Pilewski, Yingze Zhang, Kong Chen, 2019, The Journal of Heart and Lung Transplantation.

Does simultaneous lung-liver transplantation provide an immunologic advantage compared with isolated lung transplantation?

J. Pilewski, Y. Toyoda, C. Bermudez, 2011, The Journal of thoracic and cardiovascular surgery.

Psychiatric Predictors of Long-term Transplant-Related Outcomes in Lung Transplant Recipients

M. Dew, A. D. DeVito Dabbs, J. Pilewski, 2016, Transplantation.

UNDERWEIGHT PATIENTS WITH CYSTIC FIBROSIS HAVE ACCEPTABLE SURVIVAL AFTER LUNG TRANSPLANTATION: A UNOS REGISTRY STUDY.

C. Goss, J. Pilewski, M. Bradford, 2020, Chest.

Risk factors of bronchial dehiscence after primary lung transplantation

J. Pilewski, E. Chan, R. Rivosecchi, 2022, Journal of cardiac surgery.

116: Lung Transplantation with Lungs from Donors 55 Years or Older

J. Pilewski, S. Gilbert, P. Bonde, 2010 .

Successful Lung Transplantation in a Patient with Chronic Granulomatous Disease

Janet S. Lee, J. Pilewski, N. Shigemura, 2019, Journal of Clinical Immunology.

Impact of a Mobile Health Intervention on Long-term Nonadherence After Lung Transplantation: Follow-up After a Randomized Controlled Trial

M. Dew, L. Myaskovsky, A. D. DeVito Dabbs, 2020, Transplantation.

A Randomized Controlled Trial of a Mobile Health Intervention to Promote Self‐Management After Lung Transplantation

M. Dew, R. Hawkins, A. D. DeVito Dabbs, 2016, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Impaired CMV Immunity in Idiopathic Pulmonary Fibrosis Lung Transplant Recipients with Short Telomeres.

P. Shah, J. Pilewski, Yingze Zhang, 2018 .

WS7.3 VX-661, an investigational CFTR corrector, in combination with ivacaftor, a CFTR potentiator, in patients with CF and homozygous for the F508Del-CFTR mutation: Interim analysis

J. Pilewski, S. Donaldson, M. Griese, 2013 .

Incorporating patient and caregiver feedback into lung transplant referral guidelines for individuals with cystic fibrosis—Preliminary findings from a novel paradigm

J. Pilewski, A. Faro, J. Dunitz, 2020, Clinical transplantation.

AIM2 Inflammasome Is Critical for Influenza-Induced Lung Injury and Mortality

J. Alcorn, Wei Chen, S. Fan, 2017, The Journal of Immunology.

Autoreactivity to Glucose Regulated Protein 78 Links Emphysema and Osteoporosis in Smokers

F. Sciurba, C. Fuhrman, G. Roodman, 2014, PloS one.

Imaging the postdeposition dispersion of an inhaled surfactant aerosol.

T. Corcoran, J. Pilewski, R. Tilton, 2012, Journal of aerosol medicine and pulmonary drug delivery.

Utilizing centralized biorepository samples for biomarkers of cystic fibrosis lung disease severity.

J. Clancy, K. Setchell, J. Pilewski, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Overnight delivery of hypertonic saline by nasal cannula aerosol for cystic fibrosis

T. Corcoran, M. Myerburg, J. Pilewski, 2017, Pediatric pulmonology.

EVALUATION OF HUMORAL IMMUNITY IN END-STAGE LUNG DISEASE.

J. Pilewski, Russell S. Traister, R. Sorensen, 2020, The journal of allergy and clinical immunology. In practice.

Secreted and Transmembrane Mucins Inhibit Gene Transfer with AAV4 More Efficiently than AAV5*

J. Chiorini, J. Pilewski, J. Zabner, 2002, The Journal of Biological Chemistry.

Localization of multiple functional domains on human PECAM-1 (CD31) by monoclonal antibody epitope mapping.

H. DeLisser, L. Romer, J. Pilewski, 1995, Cell adhesion and communication.

Cystic Fibrosis: Recent Successes Present New Challenges

D. Taichman, J. Pilewski, 2014, Annals of Internal Medicine.

Improvement in ion transport biomarkers and spirometry with the investigational CFTR potentiator VX-770 in subjects with cystic fibrosis and the G551D-CFTR mutation

J. Clancy, F. Accurso, J. Pilewski, 2010 .

Metabolomic Profiling Reveals Biochemical Pathways and Biomarkers Associated with Pathogenesis in Cystic Fibrosis Cells

Lining Guo, M. Milburn, J. Ryals, 2010, The Journal of Biological Chemistry.

Pattern and Predictors of Hospital Readmission During the First Year After Lung Transplantation

M. Dew, S. Sereika, A. D. DeVito Dabbs, 2017, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

55 Lumacaftor/ivacaftor (LUM/IVA) in patients (pts) with cystic fibrosis (CF) and advanced lung disease homozygous for F508del-CFTR: a 24-week open-label study

J. Pilewski, T. Barto, D. Waltz, 2017 .

Clinical trials of health information technology interventions intended for patient use: Unique issues and considerations

Mi-Kyung Song, Annette DeVito Dabbs, Ruosha Li, 2013, Clinical trials.

The ripple effect of a complication in lung transplantation: Evidence for increased long-term survival risk.

J. Luketich, J. Pilewski, E. Chan, 2016, The Journal of thoracic and cardiovascular surgery.

A Physiologically-Motivated Compartment-Based Model of the Effect of Inhaled Hypertonic Saline on Mucociliary Clearance and Liquid Transport in Cystic Fibrosis

R. Parker, T. Corcoran, M. Myerburg, 2014, PloS one.

315 Donors with Smoking History Have Better Long-Term Outcomes Than with No Smoking History in Adult Lung Transplantation

J. Pilewski, Y. Toyoda, P. Bonde, 2011 .

Sexual and Reproductive Health Care Utilization and Preferences of Young Women With Cystic Fibrosis

Kaleab Z. Abebe, G. Sawicki, S. Borrero, 2017 .

Cystic fibrosis program directors’ attitudes toward sexual and reproductive health in young women with CF

S. Borrero, J. Pilewski, D. Orenstein, 2016, Pediatric pulmonology.

ATP12A promotes mucus dysfunction during Type 2 airway inflammation

S. Wenzel, T. Corcoran, M. Myerburg, 2018, Scientific Reports.

Advancing the pipeline of cystic fibrosis clinical trials: a new roadmap with a global trial network perspective.

J. Pilewski, S. Donaldson, M. Konstan, 2023, The Lancet. Respiratory medicine.

Acute regulation of the epithelial sodium channel in airway epithelia by proteases and trafficking.

M. Myerburg, J. Pilewski, M. Butterworth, 2010, American journal of respiratory cell and molecular biology.

Comprehensive gene expression profiles reveal pathways related to the pathogenesis of chronic obstructive pulmonary disease.

Simon C Watkins, F. Sciurba, N. Kaminski, 2004, Proceedings of the National Academy of Sciences of the United States of America.

Allele-specific transactivation of matrix metalloproteinase 7 by FOXA2 and correlation with plasma levels in idiopathic pulmonary fibrosis.

Simon C Watkins, N. Kaminski, A. Choi, 2012, American journal of physiology. Lung cellular and molecular physiology.

Prolonged Use of the Hemolung Respiratory Assist System as a Bridge to Redo Lung Transplantation.

J. Pilewski, M. Fan, C. Bermudez, 2015, The Annals of thoracic surgery.

Efficacy of extracorporeal membrane oxygenation as a bridge to lung transplantation.

J. Pilewski, C. Bermudez, J. Bhama, 2013, The Journal of thoracic and cardiovascular surgery.

Five-year outcomes with alemtuzumab induction after lung transplantation.

M. Dew, A. D. DeVito Dabbs, J. Pilewski, 2011, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

WS01.4 VX-661 in combination with ivacaftor in patients with cystic fibrosis and the F508del-CFTR mutation

J. Pilewski, S. Donaldson, J. Cooke, 2015 .

Proteasome Inhibitor Carfilzomib‐Based Therapy for Antibody‐Mediated Rejection of the Pulmonary Allograft: Use and Short‐Term Findings

S. Yousem, J. Pilewski, C. Ensor, 2017, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Ganciclovir-Resistant Cytomegalovirus Infections among Lung Transplant Recipients Are Associated with Poor Outcomes despite Treatment with Foscarnet-Containing Regimens

J. Pilewski, C. Bermudez, J. Bhama, 2013, Antimicrobial Agents and Chemotherapy.

SLC26A9 is a constitutively active, CFTR-regulated anion conductance in human bronchial epithelia

J. Pilewski, R. Frizzell, Ruilin Zhang, 2009, The Journal of general physiology.

How do cystic fibrosis transmembrane conductance regulator mutations produce lung disease?

J. Pilewski, R. Frizzell, 1995, Current opinion in pulmonary medicine.

Sexual and reproductive health behaviors and experiences reported by young women with cystic fibrosis.

Kaleab Z. Abebe, G. Sawicki, S. Borrero, 2018, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Cystic fibrosis program directors’ attitudes toward sexual and reproductive health in young women with CF

S. Borrero, J. Pilewski, D. Orenstein, 2016, Pediatric pulmonology.

Pseudomonas infection and mucociliary and absorptive clearance in the cystic fibrosis lung

R. Parker, T. Corcoran, M. Myerburg, 2016, European Respiratory Journal.

Phase 2 studies reveal additive effects of VX-661, an investigational CFTR corrector and ivacaftor, a CFTR potentiator, in patients with CF who carry the d508-CFTR mutation

J. Pilewski, S. Donaldson, J. Cooke, 2014 .