C. Ribeiro

发表

Lipopolysaccharide-Elicited Systemic Inflammation Induces Selective Vulnerability of Cerebral Cortex and Striatum of Developing Glutaryl-CoA Dehydrogenase Deficient (Gcdh−/−) Mice to Oxidative Stress

G. Leipnitz, M. Wajner, B. Seminotti, 2020, Neurotoxicity Research.

Kinetics of inhibition of firefly luciferase by oxyluciferin and dehydroluciferyl-adenylate

C. Ribeiro, J. E. D. Esteves da Silva, 2008, Photochemical & photobiological sciences : Official journal of the European Photochemistry Association and the European Society for Photobiology.

Methylmalonic acid compromises mitochondrial respiration and reduces the expression of markers of differentiation in SH-SY5Y human neuroblastoma cells

C. Ribeiro, R. T. da Costa, M. D. dos Santos, 2020, bioRxiv.

Neurochemical evidence that 3-methylglutaric acid inhibits synaptic Na+,K+-ATPase activity probably through oxidative damage in brain cortex of young rats

M. Wajner, C. Ribeiro, F. H. Hickmann, 2011, International Journal of Developmental Neuroscience.

Disruption of brain redox homeostasis in glutaryl-CoA dehydrogenase deficient mice treated with high dietary lysine supplementation.

L. Barbeito, G. Leipnitz, M. Wajner, 2013, Molecular genetics and metabolism.

Methylmalonic Acid Impairs Cell Respiration and Glutamate Uptake in C6 Rat Glioma Cells: Implications for Methylmalonic Acidemia

C. Ribeiro, D. Carrettiero, Carlos Alberto-Silva, 2021, bioRxiv.

Creatine administration prevents Na+,K+-ATPase inhibition induced by intracerebroventricular administration of isovaleric acid in cerebral cortex of young rats

G. Leipnitz, M. Wajner, B. Seminotti, 2009, Brain Research.

Bradykinin-potentiating PEPTIDE-10C, an argininosuccinate synthetase activator, protects against H2O2-induced oxidative stress in SH-SY5Y neuroblastoma cells

C. Ribeiro, Carlos Alberto-Silva, S. M. Querobino, 2018, Peptides.

Glycine Intracerebroventricular Administration Disrupts Mitochondrial Energy Homeostasis in Cerebral Cortex and Striatum of Young Rats

G. Leipnitz, M. Wajner, M. Grings, 2013, Neurotoxicity Research.

3-Methylcrotonylglycine Disrupts Mitochondrial Energy Homeostasis and Inhibits Synaptic Na+,K+-ATPase Activity in Brain of Young Rats

M. Wajner, C. Ribeiro, Â. Zanatta, 2011, Cellular and Molecular Neurobiology.

Effects of L-2-Hydroxyglutaric Acid on Various Parameters of the Glutamatergic System in Cerebral Cortex of Rats

D. Souza, M. Wajner, C. Ribeiro, 2003, Metabolic Brain Disease.

Evidence that the inhibitory effects of guanidinoacetate on the activities of the respiratory chain, Na+,K+-ATPase and creatine kinase can be differentially prevented by taurine and vitamins E and C administration in rat striatum in vivo.

M. Wajner, C. Ribeiro, A. Wyse, 2007, Biochimica et biophysica acta.

Inhibition of creatine kinase activity from rat cerebral cortex by d-2-hydroxyglutaric acid in vitro

G. Leipnitz, M. Wajner, C. Ribeiro, 2004, Neurochemistry International.

Ethylmalonic Acid Inhibits Mitochondrial Creatine Kinase Activity from Cerebral Cortex of Young Rats in Vitro

G. Leipnitz, M. Wajner, C. Ribeiro, 2003, Neurochemical Research.

Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease.

M. Wajner, C. Ribeiro, A. Wyse, 2003, Biochimica et biophysica acta.

Inhibition of Brain Energy Metabolism by the Branched-chain Amino Acids Accumulating in Maple Syrup Urine Disease

M. Wajner, C. Ribeiro, C. Dutra-filho, 2007, Neurochemical Research.

Evidence That Antioxidants Prevent the Inhibition of Na+,K+-ATPase Activity Induced by Octanoic Acid in Rat Cerebral Cortex in Vitro

C. Vargas, M. Wajner, C. Ribeiro, 2003, Neurochemical Research.

Evidence that glutaric acid reduces glutamate uptake by cerebral cortex of infant rats.

D. Souza, M. Wajner, C. Ribeiro, 2007, Life sciences.

Mitochondrial Dysfunction in Cardiorenal Syndrome 3: Renocardiac Effect of Vitamin C

C. Ribeiro, A. Seabra, J. C. Pieretti, 2021, Cells.

Methylmalonic Acid Compromises Respiration and Reduces the Expression of Differentiation Markers of SH-SY5Y Human Neuroblastoma Cells.

C. Ribeiro, R. T. da Costa, M. D. dos Santos, 2021, ACS chemical neuroscience.

Striatal neuronal death mediated by astrocytes from the Gcdh-/- mouse model of glutaric acidemia type I.

Cheryl Tatano Beck, D. Souza, L. Barbeito, 2015, Human molecular genetics.

3-Hydroxy-3-methylglutaric and 3-methylglutaric acids impair redox status and energy production and transfer in rat heart: relevance for the pathophysiology of cardiac dysfunction in 3-hydroxy-3-methylglutaryl-coenzyme A lyase deficiency

G. Leipnitz, M. Wajner, B. Seminotti, 2016, Free radical research.

Disruption of redox homeostasis in cerebral cortex of developing rats by acylcarnitines accumulating in medium-chain acyl-CoA dehydrogenase deficiency

G. Leipnitz, M. Wajner, M. Grings, 2012, International Journal of Developmental Neuroscience.

Evidence that 3-hydroxyglutaric acid interacts with NMDA receptors in synaptic plasma membranes from cerebral cortex of young rats

D. Souza, M. Wajner, C. Ribeiro, 2004, Neurochemistry International.

Disruption of oxidative phosphorylation and synaptic Na(+), K(+)-ATPase activity by pristanic acid in cerebellum of young rats.

M. Wajner, C. Ribeiro, Â. Zanatta, 2014, Life sciences.

Marked inhibition of Na+, K+ - ATPase activity and the respiratory chain by phytanic acid in cerebellum from young rats: possible underlying mechanisms of cerebellar ataxia in Refsum disease

G. Leipnitz, C. Vargas, M. Wajner, 2013, Journal of Bioenergetics and Biomembranes.

Isovaleric Acid Reduces Na+, K+-ATPase Activity in Synaptic Membranes from Cerebral Cortex of Young Rats

M. Wajner, C. Ribeiro, Vanessa Grando, 2007, Cellular and Molecular Neurobiology.

The effect of WIN 55,212-2 suggests a cannabinoid-sensitive component in the early toxicity induced by organic acids accumulating in glutaric acidemia type I and in related disorders of propionate metabolism in rat brain synaptosomes

D. Souza, G. Leipnitz, M. Wajner, 2015, Neuroscience.

Experimental Evidence that 3-Methylglutaric Acid Disturbs Mitochondrial Function and Induced Oxidative Stress in Rat Brain Synaptosomes: New Converging Mechanisms

D. Souza, G. Leipnitz, M. Wajner, 2016, Neurochemical Research.

Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver

G. Leipnitz, C. Vargas, M. Wajner, 2009, International Journal of Developmental Neuroscience.

Marked reduction of Na(+), K(+)-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice.

M. Wajner, C. Fernandes, B. Seminotti, 2012, Molecular genetics and metabolism.

Glutaric Acid Administration Impairs Energy Metabolism in Midbrain and Skeletal Muscle of Young Rats

C. Vargas, M. Wajner, C. Ribeiro, 2005, Neurochemical Research.

l-2-Hydroxyglutaric acid inhibits mitochondrial creatine kinase activity from cerebellum of developing rats

G. Leipnitz, M. Wajner, C. Ribeiro, 2003, International Journal of Developmental Neuroscience.

Toxic synergism between quinolinic acid and organic acids accumulating in glutaric acidemia type I and in disorders of propionate metabolism in rat brain synaptosomes: Relevance for metabolic acidemias

D. Souza, G. Leipnitz, M. Wajner, 2015, Neuroscience.

D‐2‐Hydroxyglutaric acid inhibits creatine kinase activity from cardiac and skeletal muscle of young rats

G. Leipnitz, M. Wajner, C. Ribeiro, 2003, European journal of clinical investigation.

3-Hydroxyglutaric acid enhances glutamate uptake into astrocytes from cerebral cortex of young rats

D. Souza, M. Wajner, C. Ribeiro, 2004, Neurochemistry International.

Ethylmalonic acid impairs brain mitochondrial succinate and malate transport.

G. Leipnitz, M. Wajner, A. U. Amaral, 2012, Molecular genetics and metabolism.

Experimental evidence that bioenergetics disruption is not mainly involved in the brain injury of glutaryl-CoA dehydrogenase deficient mice submitted to lysine overload

M. Wajner, B. Seminotti, A. U. Amaral, 2015, Brain Research.

Inhibition of energy metabolism in cerebral cortex of young rats by the medium-chain fatty acids accumulating in MCAD deficiency

M. Wajner, C. Ribeiro, A. Wyse, 2004, Brain Research.

Long Lasting High Lysine Diet Aggravates White Matter Injury in Glutaryl-CoA Dehydrogenase Deficient (Gcdh−/−) Mice

D. Souza, L. Barbeito, G. Leipnitz, 2018, Molecular Neurobiology.

Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid

M. Wajner, C. Ribeiro, A. Wyse, 2002, Neurochemistry International.

Evidence that quinolinic acid severely impairs energy metabolism through activation of NMDA receptors in striatum from developing rats

M. Wajner, C. Ribeiro, C. Wannmacher, 2006, Journal of neurochemistry.

Glycine Intracerebroventricular Administration Disrupts Mitochondrial Energy Homeostasis in Cerebral Cortex and Striatum of Young Rats

G. Leipnitz, M. Wajner, M. Grings, 2013, Neurotoxicity Research.

3-Methylcrotonylglycine Disrupts Mitochondrial Energy Homeostasis and Inhibits Synaptic Na+,K+-ATPase Activity in Brain of Young Rats

M. Wajner, C. Ribeiro, Â. Zanatta, 2012, Cellular and Molecular Neurobiology.

Chronic early postnatal glutaric acid administration causes cognitive deficits in the water maze

M. Wajner, C. Ribeiro, G. C. Ferreira, 2008, Behavioural Brain Research.

Reactive nitrogen species mediate oxidative stress and astrogliosis provoked by in vivo administration of phytanic acid in cerebellum of adolescent rats: A potential contributing pathomechanism of cerebellar injury in peroxisomal disorders

G. Leipnitz, C. Vargas, M. Wajner, 2015, Neuroscience.

Inhibition of Creatine Kinase Activity in Vitro by Ethylmalonic Acid in Cerebral Cortex of Young Rats

G. Leipnitz, M. Wajner, C. Ribeiro, 2002, Neurochemical Research.

Disturbance of energy and redox homeostasis and reduction of Na+,K+-ATPase activity provoked by in vivo intracerebral administration of ethylmalonic acid to young rats.

A. Sitta, M. Wajner, A. U. Amaral, 2015, Biochimica et biophysica acta.

Inhibition of cytochrome c oxidase activity in rat cerebral cortex and human skeletal muscle by D-2-hydroxyglutaric acid in vitro.

G. Leipnitz, M. Wajner, C. Ribeiro, 2002, Biochimica et biophysica acta.

Pristanic Acid Provokes Lipid, Protein, and DNA Oxidative Damage and Reduces the Antioxidant Defenses in Cerebellum of Young Rats

D. Souza, C. Vargas, M. Wajner, 2014, The Cerebellum.

Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats

G. Leipnitz, M. Wajner, C. Ribeiro, 2005, Journal of Inherited Metabolic Disease.

Neurochemical Evidence that the Metabolites Accumulating in 3-Methylcrotonyl-CoA Carboxylase Deficiency Induce Oxidative Damage in Cerebral Cortex of Young Rats

G. Leipnitz, M. Wajner, M. Grings, 2012, Cellular and Molecular Neurobiology.

Long Lasting High Lysine Diet Aggravates White Matter Injury in Glutaryl-CoA Dehydrogenase Deficient (Gcdh−/−) Mice

D. Souza, L. Barbeito, G. Leipnitz, 2018, Molecular Neurobiology.

Myelin Disruption, Neuroinflammation, and Oxidative Stress Induced by Sulfite in the Striatum of Rats Are Mitigated by the pan-PPAR agonist Bezafibrate

J. Vockley, G. Leipnitz, B. Seminotti, 2023, Cells.

Inhibition of brain energy metabolism by the α-keto acids accumulating in maple syrup urine disease

M. Wajner, C. Ribeiro, A. Wyse, 2003 .

G. Leipnitz, M. Wajner, B. Seminotti, 2016, Free radical research.