I. Sternlieb

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Diagnosis and phenotypic classification of Wilson disease 1

D. Cox, G. Loudianos, F. Berr, 2003, Liver international : official journal of the International Association for the Study of the Liver.

Neuropathological findings in penicillamine-treated patients with Wilson's disease.

I. Sternlieb, D. Horoupian, I. Scheinberg, 1988, Clinical neuropathology.

Eight closely linked loci place the Wilson disease locus within 13q14-q21.

A. Bowcock, L. Farrer, H. Scheffer, 1988, American journal of human genetics.

Mapping, cloning and genetic characterization of the region containing the Wilson disease gene

J. Ott, T. Gilliam, M. Devoto, 1993, Nature Genetics.

The role of radiocopper in the diagnosis of Wilson's disease.

I. Sternlieb, I. Scheinberg, 1979, Gastroenterology.

Identification and analysis of mutations in the Wilson disease gene (ATP7B): population frequencies, genotype-phenotype correlation, and functional analyses.

T. Gilliam, G. Penchaszadeh, O. Evgrafov, 1997, American journal of human genetics.

Heavy metals and lysosomes.

I. Sternlieb, S. Goldfischer, 1976, Frontiers of biology.

ORTHOTOPIC LIVER TRANSPLANTATION FOR WILSON’S DISEASE: A SINGLE-CENTER EXPERIENCE

S. Thung, I. Sternlieb, M. Schilsky, 2001, Transplantation.

THE INCORPORATION OF COPPER INTO CERULOPLASMIN IN VIVO: STUDIES WITH COPPER AND COPPER.

I. Sternlieb, A. Morell, I. Scheinberg, 1961, The Journal of clinical investigation.

Measurement of gastrointestinal protein loss using ceruloplasmin labeled with copper.

T. Waldmann, I. Sternlieb, A. Morell, 1967, The Journal of clinical investigation.

The use of trientine in preventing the effects of interrupting penicillamine therapy in Wilson's disease.

I. Sternlieb, I. Scheinberg, M. Jaffe, 1987, New England Journal of Medicine.

PENICILLAMINE MAY DETOXIFY COPPER IN WILSON'S DISEASE

I. Sternlieb, M. Schilsky, I. Scheinberg, 1987, The Lancet.

Metabolic Diseases of the Liver

U. Meyer, I. Sternlieb, C. M. Leevy, 1975 .

The application of laser microprobe mass analysis to the study of biological material

D. Perl, P. Good, I. Sternlieb, 2004, Biometals.

Copper and the liver.

I. Sternlieb, Irmin Sternlieb, Irmin Sternlieb, 1980, Gastroenterology.

CYTOPLASMIC COPPER AND ITS TOXIC EFFECTS STUDIES IN INDIAN CHILDHOOD CIRRHOSIS

H. Popper, I. Sternlieb, N. Nayak, 1979, The Lancet.

The significance of variations in the distribution of copper in liver disease.

H. Popper, I. Sternlieb, S. Goldfischer, 1980, The American journal of pathology.

The liver in Wilson's disease.

I. Sternlieb, I. Scheinberg, 1959, Gastroenterology.

Defective urinary acidification in Wilson's disease.

I. Sternlieb, I. Scheinberg, M. Fulop, 1968, Annals of internal medicine.

IgA interaction with the asialoglycoprotein receptor.

J. C. Collins, I. Sternlieb, A. Morell, 1982, Proceedings of the National Academy of Sciences of the United States of America.

Endocytosis of asialoglycoprotein-enzyme conjugates by hepatocytes.

P. Novikoff, I. Sternlieb, A. Novikoff, 1980, Laboratory investigation; a journal of technical methods and pathology.

Wilson disease and idiopathic copper toxicosis.

I. Sternlieb, I. Scheinberg, 1996, The American journal of clinical nutrition.

Fraternal concordance of types of abnormal hepatocellular mitochondria in Wilson's disease

I. Sternlieb, 1992, Hepatology.

Identification of B10, an alkaline phosphodiesterase of the apical plasma membrane of hepatocytes and biliary cells, in rat serum: Increased levels following bile duct ligation and during the development of cholangiocarcinoma

I. Sternlieb, M. Schilsky, G. Feldmann, 1998, Hepatology.

The Effects of Two New Inotropic Agents on Microsomal Liver Function in Patients with Congestive Heart Failur

T. LeJemtel, I. Sternlieb, C. Maskin, 1986, The American journal of the medical sciences.

Perspectives on Wilson's disease

I. Sternlieb, 1990, Hepatology.

Hepatocellular copper toxicity and its attenuation by zinc.

M. Czaja, M. Zern, I. Sternlieb, 1989, The Journal of clinical investigation.

Hepatic copper toxicosis

I. Sternlieb, 1989, Journal of gastroenterology and hepatology.

Canine hepatic lysosomal copper protein: identification as metallothionein.

I. Sternlieb, K. Lerch, G. F. Johnson, 1985, Archives of biochemistry and biophysics.

Radiocopper in diagnosing liver disease.

I. Sternlieb, I. Scheinberg, 1972, Seminars in nuclear medicine.

Present Status of Diagnosis and Prophylaxis of Asymptomatic Patients with Wilson’s Disease*

I. Sternlieb, 1976 .

The uniqueness of ceruloplasmin in the study of plasma protein synthesis.

I. Sternlieb, A. Morell, I. Scheinberg, 1962, Transactions of the Association of American Physicians.

Chronic hepatitis as a first manifestation of Wilson's disease.

I. Sternlieb, I. Scheinberg, 1972, Annals of internal medicine.

Clinical, morphologic, and chemical studies on copper toxicosis of Bedlington Terriers.

I. Sternlieb, S. Gilbertson, D. Twedt, 1979, Journal of the American Veterinary Medical Association.

Lysosomal defect of hepatic copper excretion in Wilson's disease (hepatolenticular degeneration).

I. Sternlieb, G. Gregoriadis, A. Morell, 1973, Gastroenterology.

Changes in the distribution of hepatic copper in relation to the progression of Wilson's disease (hepatolenticular degeneration).

I. Sternlieb, S. Goldfischer, 1968, The American journal of pathology.

The peroxisomes of human hepatocytes.

I. Sternlieb, N. Quintana, 1977, Laboratory investigation; a journal of technical methods and pathology.

The development of cirrhosis in Wilson's disease.

I. Sternlieb, 1975, Clinics in gastroenterology.

Familial cholestatic cirrhosis associated with Kayser-Fleischer rings.

I. Sternlieb, N. Javitt, C. Kaplinsky, 1980, Pediatrics.

Catabolism of desialylated ceruloplasmin in the liver.

I. Sternlieb, G. Gregoriadis, A. Morell, 1970, The Journal of biological chemistry.

Gastrointestinal copper absorption in man.

I. Sternlieb, 1967, Gastroenterology.

Evolution of the hepatic lesion in Wilson's disease (hepatolenticular degeneration).

I. Sternlieb, 1972, Progress in liver diseases.

Copper in Hepatocyte Lysosomes of the Toad, Bufo marinus L.

I. Sternlieb, S. Goldfischer, B. Schiller, 1970, Nature.

D-penicillamine induced Goodpasture's syndrome in Wilson's disease.

I. Sternlieb, I. Scheinberg, B. Bennett, 1975, Annals of internal medicine.

Decreased taste sensitivity after D-penicillamine reversed by copper administration.

R. Henkin, I. Sternlieb, I. Scheinberg, 1967, Lancet.

Pregnancy in penicillamine-treated patients with Wilson's disease.

I. Sternlieb, I. Scheinberg, 1975, The New England journal of medicine.

Wilson's disease: Transplantation when all else has failed

I. Sternlieb, 1988, Hepatology.

Wilson's disease and pregnancy

I. Sternlieb, 2000, Hepatology.

Liver transplantation for Wilson's disease: Indications and outcome

I. Sternlieb, M. Schilsky, I. Scheinberg, 1994, Hepatology.

Prognosis of Wilsonian chronic active hepatitis.

I. Sternlieb, M. Schilsky, I. Scheinberg, 1991, Gastroenterology.

The cytopathology of metal overload.

I. Sternlieb, S. Goldfischer, E. Alt, 1990, International review of experimental pathology.

Mitochondrial and fatty changes in hepatocytes of patients with Wilson's disease.

I. Sternlieb, 1968, Gastroenterology.

The American Journal of PATHOLOGY Changes in the Distribution of Hepatic Copper in Relation to the Progression of Wilson's Disease (Hepatolenticular Degeneration)

I. Sternlieb, S. Goldfischer, 2007 .

Wilson's Disease: Indications for Liver Transplants

I. Sternlieb, 1984, Hepatology.

The long term management of hepatolenticular degeneration (Wilson's disease).

I. Sternlieb, I. Scheinberg, 1960, The American journal of medicine.

Immunohistochemical analysis of Mallory bodies in Wilsonian and non‐Wilsonian hepatic copper toxicosis

K. Zatloukal, H. Denk, C. Langner, 2004, Hepatology.

Molecular studies of ceruloplasmin deficiency in Wilson's disease.

M. Koschinsky, D. V. van Thiel, M. Czaja, 1987, The Journal of clinical investigation.

OPTICAL DIFFRACTION STUDIES OF CRYSTALLINE STRUCTURES IN ELECTRON MICROGRAPHS

I. Sternlieb, J. E. Berger, Irmin Sternlieb, 1969, The Journal of cell biology.

Chronic hepatitis and hepatic failure in a 14‐year‐old girl

J. Ludwig, G. Farr, I. Sternlieb, 1995, Hepatology.

Wilson's disease.

I. Sternlieb, 1998, Clinics in liver disease.

Salicylazosulfapyridine in inflammatory bowel disease

I. Sternlieb, K. Das, 1975, The American Journal of Digestive Diseases.

The diagnosis of Wilson's disease in asymptomatic patients.

I. Sternlieb, I. Scheinberg, 1963, JAMA.

CERULOPLASMIN IN HEALTH AND DISEASE *

I. Sternlieb, I. Scheinberg, 1961 .

The pathogenesis and clinical significance of the liver disease in hepatolenticular degeneration (Wilson's disease).

I. Sternlieb, I. Scheinberg, 1960, The Medical clinics of North America.

PENICILLAMINE THERAPY FOR HEPATOLENTICULAR DEGENERATION.

I. Sternlieb, I. Scheinberg, 1964, JAMA.

Hepatic peroxisomal abnormalities in abetalipoproteinemia.

I. Sternlieb, I. Scheinberg, D. Giblin, 1989, Gastroenterology.

Skeletal changes in Wilson's disease. A radiological study.

M. Elkin, I. Sternlieb, R. Mindelzun, 1970, Radiology.

Third International Congress of Histochemistry and Cytochemistry: August 18–22, 1968, New York, N.Y.

W. D. Selles, W. W. Doane, J. E. Kephart, 1968 .

Third International Congress of Histochemistry and Cytochemistry

Richard E. Cornell, W. D. Selles, W. W. Doane, 1968 .

Cytochemical Detection of Inherited Copper Toxicosis of Bedlington Terriers

I. Sternlieb, S. Gilbertson, S. Goldfischer, 1984, Veterinary pathology.

Copper metallothionein in patients with hepatic copper overload

I. Sternlieb, P. Hunziker, 1991, European journal of clinical investigation.

Biliary Excretion of Cæruloplasmin Copper

P. Aisen, I. Sternlieb, A. Morell, 1964, Nature.

Is non-Indian childhood cirrhosis caused by excess dietary copper?

I. Sternlieb, I. Scheinberg, 1994, The Lancet.

The canine copper toxicosis gene MURR1 does not cause non-Wilsonian hepatic copper toxicosis.

A. Zhernakova, C. Wijmenga, E. van Binsbergen, 2003, Journal of hepatology.

Copper metabolism.

I. Sternlieb, I. Scheinberg, 1960, Pharmacological reviews.

Elastosis perforans serpiginosa during penicillamine therapy for Wilson disease.

F. Pass, I. Sternlieb, I. Scheinberg, 1973, Archives of dermatology.

HEPATOCELLUAR CHANGES IN WILSON'S DISEASE HISTOCHEMICAL AND ELECTRON MICROSCOPIC STUDIES

F. Schaffner, I. Sternlieb, Tmor Barka, 2007 .

Physical and chemical studies on ceruloplasmin. V. Metabolic studies on sialic acid-free ceruloplasmin in vivo.

I. Sternlieb, A. Morell, I. Scheinberg, 1968, The Journal of biological chemistry.

Lipolysosomes in human liver: distribution in livers with fatty infiltration.

D. Winship, I. Sternlieb, H. Hayashi, 1977, Gastroenterology.

Lipolysosomes in human hepatocytes. Ultrastructural and cytochemical studies of patients with Wilson's disease.

I. Sternlieb, H. Hayashi, 1975, Laboratory investigation; a journal of technical methods and pathology.

Physical and Chemical Studies on Ceruloplasmin: Crystallization of Desialized Human Ceruloplasmin Asialoceruloplasmin

I. Sternlieb, A. Morell, I. Scheinberg, 1969, Science.

Penicillamine and the Nephrotic Syndrome: Results in Patients With Hepatolenticular Degeneration

I. Sternlieb, 1966 .

Systemic Absorption of Intrauterine Copper

I. Sternlieb, A. Morell, I. Scheinberg, 1972, Science.

Hepatocellular changes in Wilson's disease. Histochemical and electron microscopic studies.

H. Popper, F. Schaffner, I. Sternlieb, 1962, The American journal of pathology.

Cytoplasmic crystals in human hepatocytes.

I. Sternlieb, N. Quintana, L. Biempica, 1971, Laboratory investigation; a journal of technical methods and pathology.

Effects of anticopper therapy on hepatocellular mitochondria in patients with Wilson's disease: an ultrastructural and stereological study.

G. Feldmann, I. Sternlieb, 1976, Gastroenterology.

Wilson disease and idiopathic copper toxicosis : Copper nutrition in humans : Essentiality and toxicity

I. Sternlieb, I. Scheinberg, 1996 .

Electron microscopy of mitochondria and peroxisomes of human hepatocytes.

I. Sternlieb, 1979, Progress in liver diseases.

BLEEDING ŒSOPHAGEAL VARICES IN PATIENTS WITH WILSON'S DISEASE

I. Sternlieb, I. Scheinberg, J. Walshe, 1970 .

Wilson's disease and the concentration of caeruloplasmin in serum.

I. Sternlieb, I. Scheinberg, 1963, Lancet.

Special article: functional implications of human portal and bile ductular ultrastructure.

I. Sternlieb, Irmin Sternlieb, 1972, Gastroenterology.

Origins of Biliary Copper

I. Sternlieb, A. Morell, R. Stockert, 1984, Hepatology.

An array of mitochondrial alterations in the hepatocytes of long‐evans cinnamon rats

I. Sternlieb, M. Schilsky, I. Volenberg, 1995, Hepatology.

The Wilson disease gene is a copper transporting ATPase with homology to the Menkes disease gene

J. Peppercorn, L. Pavone, B. Honig, 1993, Nature Genetics.

Predictive testing for Wilson's disease using tightly linked and flanking DNA markers

L. Cavalli-Sforza, L. Cavalli-Sforza, J. Hebert, 1991, Neurology.

The remarkable selectivity of hepatocytes in the uptake of glycoproteins.

I. Sternlieb, A. Morell, I. Scheinberg, 1973, Gastroenterology.

Biliary proteins and ductular ultrastructure

I. Sternlieb, N. Quintana, Irmin Sternlieb, 1985, Hepatology.

Mitochondrion-desmosome complexes in human hepatocytes

I. Sternlieb, 1968, Zeitschrift für Zellforschung und Mikroskopische Anatomie.

ACTH and cortisone therapy in ulcerative colitis

I. Sternlieb, A. Winkelstein, A. Richman, 1956, The American Journal of Digestive Diseases.

Orthotopic liver transplantation for Wilson's disease.

I. Sternlieb, D. Rodgerson, I. Scheinberg, 1971, Lancet.

Prevention of Wilson's disease in asymptomatic patients.

I. Sternlieb, I. Scheinberg, I Sternlieb, 1968, The New England journal of medicine.

Chronic active hepatitis in Doberman pinschers.

I. Sternlieb, S. Gilbertson, Zawie Da, 1982, Journal of the American Veterinary Medical Association.

Diagnosis of Wilson's disease.

I. Sternlieb, 1978, Gastroenterology.

ABSORPTION OF COPPER IN MALABSORPTION SYNDROMES.

I. Sternlieb, H. Janowitz, 1964, The Journal of clinical investigation.

Intensive Therapy of Wilson's Disease.

I. Sternlieb, I. Scheinberg, 1963 .

A prospective clinical trial of D‐penicillamine in the treatment of primary biliary cirrhosis

F. Klion, F. Schaffner, I. Sternlieb, 1985, Hepatology.

An international symposium on Wilson's and Menkes' diseases

S. Packman, J. Gitlin, R. Sokol, 1996, Hepatology.

Role of Intestinal Lymphatics in Copper Absorption

I. Sternlieb, C. Hamer, S. Alpert, 1967, Nature.

Turner's syndrome associated with carcinoma of the rectosigmoid.

I. Sternlieb, J. Zendel, L. Wilson, 1954, New York state journal of medicine.

Penicillamine and the nephrotic syndrome.

I. Sternlieb, 1966, JAMA.

Inheritance of copper toxicosis in Bedlington terriers.

I. Sternlieb, I. Scheinberg, D. Twedt, 1980, American journal of veterinary research.

[34] Purification of canine hepatic lysosomal copper-metallothionein

I. Sternlieb, A. Morell, R. Stockert, 1991 .

Environmental treatment of a hereditary illness: Wilson's disease.

I. Sternlieb, I. Scheinberg, 1960, Annals of internal medicine.

Hepatic lysosomal copper protein in dogs with an inherited copper toxicosis

I. Sternlieb, A. Morell, R. Stockert, 1981, Hepatology.

Morphologic and chemical studies on a murine mutation (toxic milk mice) resulting in hepatic copper toxicosis.

I. Sternlieb, N. Quintana, L. Biempica, 1988, Laboratory investigation; a journal of technical methods and pathology.

Spontaneous cholangiofibrosis in Long-Evans Cinnamon rats: a rodent model for Wilson's disease.

I. Sternlieb, M. Schilsky, I. Volenberg, 1998, Laboratory animal science.

Clinical aspects of Wilson's disease.

R. Schoen, I. Sternlieb, 1990, The American journal of gastroenterology.

WILSON'S DISEASE.

I. Sternlieb, I. Scheinberg, 2000, Annual review of medicine.

The outlook for the diagnosis of Wilson's disease.

I. Sternlieb, 1993, Journal of hepatology.

Treatment of the neurologic manifestations of Wilson's disease.

I. Sternlieb, I. Scheinberg, 1995, Archives of neurology.

Light‐ and electron‐microscopical study of a case of gold salt—induced hepatotoxicity

I. Sternlieb, G. Fleischner, T. Hanaichi, 1991, Hepatology.

The cardiomyopathy of Wilson's disease

S. Factor, I. Sternlieb, I. Scheinberg, 2004, Virchows Archiv A.

Overcoming obstacles to the diagnosis of Wilson's disease.

I. Sternlieb, M. Schilsky, 1997, Gastroenterology.

Nonceruloplasmin copper in rheumatoid arthritis.

I. Sternlieb, A. Morell, I. Scheinberg, 1969, Arthritis & Rheumatism.

R-bodies of human rectal epithelial cells.

I. Sternlieb, L. Biempica, M. Ali, 1976, Archives of pathology & laboratory medicine.

Excess zinc associated with cholestasis

I. Sternlieb, I. Scheinberg, 1996, The Lancet.

The dual role of the liver in Wilson's disease.

I. Sternlieb, I. Scheinberg, 1963, The Medical clinics of North America.

Dosimetry of copper radionuclides.

I. Sternlieb, L. R. Chervu, 1974, Journal of nuclear medicine : official publication, Society of Nuclear Medicine.

Wilson's disease and pregnancy

I. Sternlieb, 2000, Hepatology.

Detection of multiple forms of human ceruloplasmin. A novel Mr 200,000 form.

M. Sato, I. Sternlieb, M. Schilsky, 1990, The Journal of biological chemistry.

Pleiotropic effect of LEC mutation: a rodent model of Wilson's disease.

I. Sternlieb, M. Schilsky, R. Stockert, 1993, The American journal of physiology.

Inherited Copper Toxicity of the Liver in Bedlington Terriers

I. Sternlieb, S. Gilbertson, I. Scheinberg, 1977, Proceedings of the Royal Society of Medicine.

Follow‐up of “What is it?” Case 1, 1987

S. Fahn, I. Sternlieb, H. Shale, 1988 .

An array of mitochondrial alterations in the hepatocytes of long‐evans cinnamon rats

I. Sternlieb, M. Schilsky, I. Volenberg, 1995, Hepatology.

Animal models of copper toxicosis.

I. Sternlieb, M. Schilsky, 1993, Advances in veterinary science and comparative medicine.