D. Kiely

J. Wild, A. Swift, D. Kiely, 2017, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Bayesian Inference Associates Rare KDR Variants With Specific Phenotypes in Pulmonary Arterial Hypertension

W. Chung, Yufeng Shen, M. Humbert, 2019, bioRxiv.

IodiNe Subtraction mapping in the diagnosis of Pulmonary chronIc thRomboEmbolic disease (INSPIRE): Rationale and methodology of a cross-sectional observational diagnostic study

A. Swift, D. Kiely, K. Karunasaagarar, 2019, Contemporary clinical trials communications.

BNP/NT-proBNP in pulmonary arterial hypertension: time for point-of-care testing?

Robert A. Lewis, D. Kiely, R. Condliffe, 2020, European Respiratory Review.

Identification of novel rare sequence variation underlying heritable pulmonary arterial hypertension

W. Ouwehand, M. Humbert, W. Seeger, 2018 .

Novel causative genes for heritable pulmonary arterial hypertension

W. Ouwehand, M. Humbert, W. Seeger, 2017, bioRxiv.

Management of acute pulmonary embolism.

D. Kiely, R. Condliffe, C. Elliot, 2015, British journal of hospital medicine.

Supplementation with Iron in Pulmonary Arterial Hypertension. Two Randomized Crossover Trials

A. de Marvao, P. Robbins, L. Huson, 2021, Annals of the American Thoracic Society.

Cardiopulmonary effects of endothelin-1 in man.

B. Lipworth, A. Struthers, D. Kiely, 1997, Cardiovascular research.

Idiopathic pulmonary arterial hypertension and co-existing lung disease: is this a new phenotype?

J. Lordan, P. Corris, M. Gatzoulis, 2020, Pulmonary circulation.

Long‐term outcomes of domiciliary intravenous iloprost in idiopathic and connective tissue disease‐associated pulmonary arterial hypertension

D. Kiely, R. Condliffe, C. Elliot, 2017, Respirology.

Dynamic Contrast–Enhanced Magnetic Resonance Imaging in Patients with Pulmonary Arterial Hypertension

H. Marshall, J. Wild, A. Swift, 2014, Pulmonary circulation.

Arrhythmic Burden and Outcomes in Pulmonary Arterial Hypertension

Robert A. Lewis, A. Kyriacou, D. Kiely, 2019, Front. Med..

Decreased Whole Body Endogenous Nitric Oxide Production in Patients with Primary Pulmonary Hypertension

D. Kiely, T. Higenbottam, S. Wharton, 2005, Journal of Vascular Research.

The REPAIR Study: Effects of Macitentan on RV Structure and Function in Pulmonary Arterial Hypertension.

A. Torbicki, S. Rosenkranz, A. Swift, 2021, JACC. Cardiovascular imaging.

Ventricular mass index correlates with pulmonary artery pressure and predicts survival in suspected systemic sclerosis-associated pulmonary arterial hypertension.

J. Wild, D. Kiely, C. Davies, 2009, Rheumatology.

Imaging and Risk Stratification in Pulmonary Arterial Hypertension: Time to Include Right Ventricular Assessment

S. Alabed, J. Wild, A. Swift, 2022, Frontiers in Cardiovascular Medicine.

A Systematic Review of Right Ventricular Diastolic Assessment by 4D Flow CMR

H. Kaur, J. Wild, A. Swift, 2019, BioMed research international.

Age-associated changes in 4D flow CMR derived Tricuspid Valvular Flow and Right Ventricular Blood Flow Kinetic Energy

S. Plein, J. Westenberg, R. J. van der Geest, 2020, Scientific Reports.

Bayesian Inference Associates Rare KDR Variants With Specific Phenotypes in Pulmonary Arterial Hypertension

W. Chung, Yufeng Shen, M. Humbert, 2019, bioRxiv.

Pulmonary hypertension phenotypes in patients with systemic sclerosis

A. Haque, D. Kiely, R. Condliffe, 2021, European Respiratory Review.

3D contrast-enhanced lung perfusion MRI is an effective screening tool for chronic thromboembolic pulmonary hypertension: results from the ASPIRE Registry

H. Marshall, J. Wild, A. Swift, 2013, Thorax.

Adults’ experiences of living with pulmonary hypertension: a thematic synthesis of qualitative studies

D. Kiely, A. Thompson, R. Condliffe, 2020, BMJ Open.

The CRASH report: emergency management dilemmas facing acute physicians in patients with pulmonary arterial hypertension

K. Dimopoulos, J. Lordan, P. Corris, 2017, Thorax.

Pregnancy and pulmonary hypertension: a practical approach to management

D. Kiely, R. Condliffe, C. Elliot, 2013, Obstetric medicine.

Characterization of GDF2 Mutations and Levels of BMP9 and BMP10 in Pulmonary Arterial Hypertension.

W. Ouwehand, M. Humbert, W. Seeger, 2020, American journal of respiratory and critical care medicine.

Inhibition of pyruvate dehydrogenase kinase improves pulmonary arterial hypertension in genetically susceptible patients

Richard B. Thompson, D. O’Regan, Lan Zhao, 2017, Science Translational Medicine.

Genetic determinants of risk and survival in pulmonary arterial hypertension

Lisa J. Martin, Ferhaan Ahmad, W. Ouwehand, 2018, bioRxiv.

Effects of frusemide and hypoxia on the pulmonary vascular bed in man.

B. Lipworth, D. Kiely, R. Cargill, 2003, British journal of clinical pharmacology.

Current strategies for managing chronic thromboembolic pulmonary hypertension: results of the worldwide prospective CTEPH Registry

E. Fadel, A. Ogawa, M. Madani, 2021, ERJ Open Research.

Pulmonary Hypertension in Renal Disease: Epidemiology, Potential Mechanisms and Implications

D. Kiely, C. Jackson, B. Kawar, 2013, American Journal of Nephrology.

Cardiovascular , Pulmonary , and Renal Pathology Paigen Diet – Fed Apolipoprotein E Knockout Mice Develop Severe Pulmonary Hypertension in an Interleukin-1 – Dependent Manner

A. Kennerley, N. Arnold, D. Crossman, 2011 .

Diagnostic accuracy of CT pulmonary angiography in suspected pulmonary hypertension

J. Wild, A. Swift, D. Capener, 2020, European Radiology.

Pulmonary arterial hypertension associated with congenital heart disease: Comparison of clinical and anatomic-pathophysiologic classification.

D. Kiely, R. Condliffe, C. Elliot, 2016, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Diagnostic accuracy of contrast-enhanced MR angiography and unenhanced proton MR imaging compared with CT pulmonary angiography in chronic thromboembolic pulmonary hypertension

J. Wild, A. Swift, D. Capener, 2012, European Radiology.

Computed tomography and magnetic resonance imaging of pulmonary hypertension: Pulmonary vessels and right ventricle

E. V. van Beek, S. Ley, J. Wild, 2010, Journal of magnetic resonance imaging : JMRI.

Comparison of the Diagnostic Utility of Cardiac Magnetic Resonance Imaging, Computed Tomography, and Echocardiography in Assessment of Suspected Pulmonary Arterial Hypertension in Patients with Connective Tissue Disease

J. Wild, A. Swift, D. Capener, 2012, The Journal of Rheumatology.

Black blood MRI has diagnostic and prognostic value in the assessment of patients with pulmonary hypertension

H. Marshall, J. Wild, A. Swift, 2012, European Radiology.

Severe pulmonary hypertension associated with lung disease is characterised by a loss of small pulmonary vessels on quantitative computed tomography

J. Tschirren, S. Alabed, J. Wild, 2022, ERJ Open Research.

Cavitating lung lesions in chronic thromboembolic pulmonary hypertension.

E. V. van Beek, D. Kiely, C. Davies, 2008, Journal of radiology case reports.

CT Pulmonary Angiography Combined With Echocardiography In Suspected Systemic Sclerosis-Associated Pulmonary Arterial Hypertension

E. V. Beek, A. Swift, D. Kiely, 2011, ATS 2011.

Comparison of MRI and VQ-SPECT as a Screening Test for Patients With Suspected CTEPH: CHANGE-MRI Study Design and Rationale

T. Derlin, G. Krombach, F. Rengier, 2020, Frontiers in Cardiovascular Medicine.

Elevated levels of natriuretic peptides in patients with pulmonary thromboembolism.

B. Lipworth, O. Pirzada, A. Struthers, 2005, Respiratory medicine.

Improved outcomes in medically and surgically treated chronic thromboembolic pulmonary hypertension.

P. Corris, D. Kiely, R. Condliffe, 2008, American journal of respiratory and critical care medicine.

Right ventricular remodelling in pulmonary arterial hypertension predicts treatment response

S. Alabed, J. Wild, A. Swift, 2022, Heart.

Validation of Artificial Intelligence Cardiac MRI Measurements: Relationship to Heart Catheterization and Mortality Prediction

D. O’Regan, S. Alabed, R. J. van der Geest, 2022, Radiology.

LGE patterns in pulmonary hypertension do not impact overall mortality.

J. Wild, A. Swift, D. Capener, 2014, JACC. Cardiovascular imaging.

Whole genome sequencing of a sporadic primary immunodeficiency cohort

William J. Astle, Sri V. V. Deevi, Kenneth G. C. Smith, 2018, Nature.

A multicenter study of anticoagulation in operable chronic thromboembolic pulmonary hypertension

P. Corris, S. Villar, D. Kiely, 2019, Journal of thrombosis and haemostasis : JTH.

Genetic determinants of risk and survival in pulmonary arterial hypertension

Lisa J. Martin, Ferhaan Ahmad, W. Ouwehand, 2018, bioRxiv.

CT pulmonary angiography combined with echocardiography in suspected systemic sclerosis-associated pulmonary arterial hypertension.

E. V. van Beek, A. Swift, D. Kiely, 2011, Rheumatology.

Diagnostic and prognostic significance of cardiovascular magnetic resonance native myocardial T1 mapping in patients with pulmonary hypertension

M. Graves, J. Wild, A. Swift, 2018, Journal of Cardiovascular Magnetic Resonance.

Perioperative management of patients with pulmonary hypertension undergoing non-cardiothoracic, non-obstetric surgery: a systematic review and expert consensus statement.

K. Dimopoulos, J. Lordan, S. Kemp, 2021, British journal of anaesthesia.

Connective tissue disease-associated pulmonary arterial hypertension in the modern treatment era.

P. Corris, D. Kiely, R. Condliffe, 2009, American journal of respiratory and critical care medicine.

Eplerenone attenuates pathological pulmonary vascular rather than right ventricular remodeling in pulmonary arterial hypertension

W. Seeger, H. Ghofrani, N. Weissmann, 2018, BMC Pulmonary Medicine.

Mendelian randomisation and experimental medicine approaches to interleukin-6 as a drug target in pulmonary arterial hypertension

R. Kittles, M. Humbert, L. Harbaum, 2021, European Respiratory Journal.

Pulmonary Artery Denervation Reduces Pulmonary Artery Pressure and Induces Histological Changes in an Acute Porcine Model of Pulmonary Hypertension

J. Gunn, N. Arnold, A. Swift, 2015, Circulation. Cardiovascular interventions.

Autologous haematopoietic stem cell transplantation (aHSCT) for severe resistant autoimmune and inflammatory diseases – a guide for the generalist

B. Sharrack, J. Snowden, A. Lobo, 2018, Clinical medicine.

Improving safety in autologous HSCT for systemic sclerosis

J. Snowden, D. Kiely, M. Akil, 2013, The Lancet.

Screening strategies for pulmonary arterial hypertension

M. Humbert, D. Kiely, A. Lawrie, 2019, European heart journal supplements : journal of the European Society of Cardiology.

Three Element Windkessel Model to Non-Invasively Assess PAH Patients: One Year Follow-up

D. Hose, A. Lungu, J. Wild, 2017 .

ASPIRE registry: Assessing the Spectrum of Pulmonary hypertension Identified at a REferral centre

J. Wild, D. Capener, D. Kiely, 2011, European Respiratory Journal.

Adverse effects of hypoxaemia on diastolic filling in humans.

B. Lipworth, D. Kiely, R. Cargill, 1995, Clinical science.

The effect of nitric oxide inhibition on the renin response to frusemide, in man.

A. Struthers, D. Kiely, W. Coutie, 1999, British journal of clinical pharmacology.

Pulmonary arteriovenous malformations emerge from the shadows

C. Shovlin, D. Kiely, R. Condliffe, 2017, Thorax.

Current and future treatments of pulmonary arterial hypertension

S. Rosenkranz, H. Ghofrani, O. Sitbon, 2020, British journal of pharmacology.

Whole-Blood RNA Profiles Associated with Pulmonary Arterial Hypertension and Clinical Outcome

M. Dunning, M. Humbert, D. Trégouët, 2020, American journal of respiratory and critical care medicine.

Cardiac magnetic resonance identifies raised left ventricular filling pressure: prognostic implications

S. Alabed, J. Wild, A. Swift, 2022, European heart journal.

A therapeutic antibody targeting osteoprotegerin attenuates severe experimental pulmonary arterial hypertension

N. Arnold, D. Crossman, N. Morrell, 2019, Nature Communications.

Central venous catheter-related blood stream infections in patients receiving intravenous iloprost for pulmonary hypertension

D. Kiely, R. Condliffe, R. Condliffe, 2013, European Journal of Clinical Microbiology & Infectious Diseases.

Computed tomography lung parenchymal descriptions in routine radiological reporting have diagnostic and prognostic utility in patients with idiopathic pulmonary arterial hypertension and pulmonary hypertension associated with lung disease

Robert A. Lewis, S. Alabed, J. Wild, 2022, ERJ Open Research.

Mild parenchymal lung disease is still lung disease

Robert A. Lewis, D. Kiely, R. Condliffe, 2020, European Respiratory Journal.

Critical care outcomes in patients with pre-existing pulmonary hypertension: insights from the ASPIRE registry

G. Mills, D. Kiely, R. Condliffe, 2021, ERJ Open Research.

The impact of patient choice on survival in chronic thromboembolic pulmonary hypertension

J. Wild, A. Swift, D. Kiely, 2018, European Respiratory Journal.

Intravascular Ultrasound Pulmonary Artery Denervation to Treat Pulmonary Arterial Hypertension (TROPHY1): Multicenter, Early Feasibility Study.

E. Mahmud, A. Kirtane, M. Leon, 2020, JACC. Cardiovascular interventions.

Quantitative CT Evaluation of Small Pulmonary Vessels Has Functional and Prognostic Value in Pulmonary Hypertension.

J. Tschirren, S. Alabed, J. Wild, 2022, Radiology.

2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension.

M. Humbert, G. Meszaros, S. Rosenkranz, 2022, European heart journal.

2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension

M. Humbert, G. Meszaros, S. Rosenkranz, 2022, European Respiratory Journal.

Survival in portopulmonary hypertension: Outcomes of the United Kingdom National Pulmonary Arterial Hypertension Registry.

K. Dimopoulos, J. Lordan, P. Corris, 2017, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

Myocardial T1-mapping and extracellular volume in pulmonary arterial hypertension: A systematic review and meta-analysis.

E. Nagel, S. Alabed, J. Wild, 2021, Magnetic resonance imaging.

Pathophysiology and Diagnosis of Pulmonary Hypertension Due to Left Heart Disease

Robert A. Lewis, D. Kiely, R. Condliffe, 2018, Front. Med..

Diagnosis of Pulmonary Hypertension with Cardiac MRI: Derivation and Validation of Regression Models

J. Wild, A. Swift, D. Kiely, 2018, Radiology.

Pulmonary hypertension: diagnosis and treatment.

D. Kiely, C. Elliot, 2004, Clinical medicine.

Cardiovascular magnetic resonance predicts all-cause mortality in pulmonary hypertension associated with heart failure with preserved ejection fraction

J. Wild, A. Swift, D. Capener, 2021, The International Journal of Cardiovascular Imaging.

Cardiac-MRI Predicts Clinical Worsening and Mortality in Pulmonary Arterial Hypertension

Robert A. Lewis, S. Alabed, J. Wild, 2020, JACC: Cardiovascular Imaging.

A machine learning cardiac magnetic resonance approach to extract disease features and automate pulmonary arterial hypertension diagnosis

S. Alabed, J. Wild, A. Swift, 2020, European heart journal cardiovascular Imaging.

Hypoxaemia and release of endothelin-1.

B. Lipworth, D. Kiely, R. Clark, 1995, Thorax.

Effects of hypercapnia on hemodynamic, inotropic, lusitropic, and electrophysiologic indices in humans.

B. Lipworth, D. Kiely, R. Cargill, 1996, Chest.

Serum osteoprotegerin is increased and predicts survival in idiopathic pulmonary arterial hypertension

A. Morton, D. Crossman, N. Morrell, 2012, Pulmonary circulation.

Supplementation of iron in pulmonary hypertension: Rationale and design of a phase II clinical trial in idiopathic pulmonary arterial hypertension

P. Robbins, D. Ashby, N. Morrell, 2013, Pulmonary circulation.

Feasibility and safety of a telemetric pulmonary artery pressure monitoring system in acute and chronic porcine models of pulmonary hypertension

J. Gunn, O. Forouzan, N. Arnold, 2020, bioRxiv.

Idiopathic and Systemic Sclerosis‐Associated Pulmonary Arterial Hypertension: A Comparison of Demographic, Hemodynamic, and MRI Characteristics and Outcomes

A. Swift, D. Kiely, R. Condliffe, 2017, Chest.

Cardiopulmonary interactions of salbutamol and hypoxaemia in healthy young volunteers.

B. Lipworth, D. Kiely, R. Cargill, 1995, British journal of clinical pharmacology.

Oral treprostinil for the treatment of pulmonary arterial hypertension in patients receiving background endothelin receptor antagonist and phosphodiesterase type 5 inhibitor therapy (the FREEDOM-C2 study): a randomized controlled trial.

Z. Jing, Kaifeng Xu, D. Kiely, 2013, Chest.

Decision-making in pulmonary endarterectomy surgery

D. Kiely, R. Condliffe, I. Armstrong, 2019, European Respiratory Journal.

Exploring a physiotherapy well-being review to deliver community-based rehabilitation in patients with pulmonary hypertension

K. Sage, D. Kiely, I. Armstrong, 2019, Pulmonary circulation.

Phenotyping of idiopathic pulmonary arterial hypertension: a registry analysis

Robert A. Lewis, S. Rosenkranz, H. Ghofrani, 2022, The Lancet. Respiratory medicine.

Positive Predictors for Response to Ambrisentan Combination Therapy in Pulmonary Arterial Hypertension.

D. Kiely, K. Abe, M. Hatano, 2022, International heart journal.

Unenhanced computed tomography as a diagnostic tool in suspected pulmonary hypertension: a retrospective cross-sectional pilot study

A. Swift, D. Kiely, S. Rajaram, 2021, Wellcome Open Research.

EmPHasis-10 health-related quality of life score predicts outcomes in patients with idiopathic and connective tissue disease-associated pulmonary arterial hypertension: results from a UK multicentre study

K. Dimopoulos, A. Peacock, J. Yorke, 2020, European Respiratory Journal.

Phenotypes of idiopathic pulmonary arterial hypertension - Authors' reply.

M. Hoeper, D. Kiely, A. Vonk-Noordegraaf, 2022, The Lancet. Respiratory medicine.

A ploidy-agnostic method for estimating telomere length from whole genome sequencing data.

Ania, Eleanor, Dewhurst, 2018 .

High levels of healthcare utilization prior to diagnosis in idiopathic pulmonary arterial hypertension support the feasibility of an early diagnosis algorithm: the SPHInX project

R. Bergemann, D. Kiely, Y. Samyshkin, 2018, Pulmonary circulation.

Abnormal myocardial repolarisation in response to hypoxaemia and fenoterol.

B. Lipworth, A. Struthers, D. Kiely, 1995, Thorax.

Identifying At-Risk Patients with Combined Pre- and Postcapillary Pulmonary Hypertension Using Interventricular Septal Angle at Cardiac MRI

J. Wild, A. Swift, D. Capener, 2018, Radiology.

Safety Experience With Bosentan in 146 Children 2–11 Years Old With Pulmonary Arterial Hypertension: Results from the European Postmarketing Surveillance Program

M. Humbert, M. Hoeper, D. Kiely, 2008, Pediatric Research.

Examining the impact of pulmonary hypertension on nonprofessional caregivers: A mixed‐methods systematic review

D. Kiely, A. Thompson, R. Condliffe, 2022, Pulmonary circulation.

Elective lower limb orthopedic arthroplasty surgery in patients with pulmonary hypertension

Robert A. Lewis, D. Kiely, R. Condliffe, 2021, Pulmonary circulation.

Breathlessness in an ex-miner: an unusual consideration

D. Kiely, S. Rajaram, Amanda T. Goodwin, 2016, Thorax.

The patient experience of pulmonary hypertension: a large cross-sectional study of UK patients

J. Yorke, D. Kiely, W. Gin-Sing, 2019, BMC Pulmonary Medicine.

Ambrisentan therapy in pulmonary hypertension: clinical use and tolerability in a referral centre

D. Kiely, R. Condliffe, C. Elliot, 2014, Therapeutic advances in respiratory disease.

Nitric oxide: an important role in the maintenance of systemic and pulmonary vascular tone in man.

B. Lipworth, A. Struthers, D. Kiely, 1998, British journal of clinical pharmacology.

Use of Pulsed-Wave Doppler Echocardiography to Measure Changes in MPAP: To the Editor

B. Lipworth, D. Kiely, 1997 .

Fully automatic cardiac four chamber and great vessel segmentation on CT pulmonary angiography using deep learning

D. O’Regan, S. Alabed, R. J. van der Geest, 2022, Frontiers in Cardiovascular Medicine.

MRI Prediction of Precapillary Pulmonary Hypertension according to the Sixth World Symposium on Pulmonary Hypertension.

J. Wild, A. Swift, D. Kiely, 2019, Radiology.

Prognostic and aetiological factors in chronic thromboembolic pulmonary hypertension

P. Corris, A. Peacock, D. Kiely, 2008, European Respiratory Journal.

Editorial: Pulmonary Hypertension: Mechanisms and Management, History and Future

M. Wilkins, J. Wild, D. Kiely, 2020, Frontiers in Medicine.

Atrial flutter and fibrillation in patients with pulmonary arterial hypertension or chronic thromboembolic pulmonary hypertension in the ASPIRE registry: Comparison of rate versus rhythm control approaches.

Robert A. Lewis, D. Kiely, R. Condliffe, 2022, International journal of cardiology.

Treat-to-target approach in pulmonary arterial hypertension: a consensus-based proposal

S. Rosenkranz, F. Bauer, O. Sitbon, 2012, European Respiratory Review.

CT derived left atrial size identifies left heart disease in suspected pulmonary hypertension: Derivation and validation of predictive thresholds

A. Swift, D. Kiely, P. Garg, 2018, International journal of cardiology.

Using the Plasma Proteome for Risk Stratifying Patients with Pulmonary Arterial Hypertension.

M. Humbert, L. Harbaum, J. Lordan, 2022, American journal of respiratory and critical care medicine.

Repeatability and sensitivity to change of non-invasive end points in PAH: the RESPIRE study

S. Alabed, J. Wild, A. Swift, 2021, Thorax.

Survival in pulmonary hypertension registries: the importance of incident cases.

P. Corris, D. Kiely, R. Condliffe, 2011, Chest.

Systemic Sclerosis and the Lung

D. Kiely, R. Condliffe, 2021, Hematopoietic Stem Cell Transplantation and Cellular Therapies for Autoimmune Diseases.

ERS statement on exercise training and rehabilitation in patients with severe chronic pulmonary hypertension

J. Barberà, P. Corris, S. Ghio, 2019, European Respiratory Journal.

Healthcare resource utilization and quality of life in patients with sarcoidosis‐associated pulmonary hypertension

R. Sauter, D. Kiely, A. Beaudet, 2022, Pulmonary circulation.

Reversible pulmonary artery perfusion abnormalities in the postpartum period as a precursor to the development of pulmonary arterial hypertension

D. Kiely, B. O'driscoll, D. O'Riordan, 2018, Pulmonary circulation.

Partial anomalous pulmonary venous drainage in patients presenting with suspected pulmonary hypertension: A series of 90 patients from the ASPIRE registry

Robert A. Lewis, K. English, A. Swift, 2020, Respirology.

Plasma Metabolomics Implicates Modified Transfer RNAs and Altered Bioenergetics in the Outcomes of Pulmonary Arterial Hypertension

P. Corris, M. Haimel, M. Bleda, 2017, Circulation.

Bedside tracer gas technique accurately predicts outcome in aspiration of spontaneous pneumothorax

D. Kiely, S. Ansari, D. Seaton, 2001, Thorax.

Changing demographics, epidemiology, and survival of incident pulmonary arterial hypertension: results from the pulmonary hypertension registry of the United Kingdom and Ireland.

J. Lordan, P. Corris, M. Gatzoulis, 2012, American journal of respiratory and critical care medicine.

S72 Prediction of survival in pulmonary arterial hypertension using survival equations. Results from the pulmonary hypertension registry of the UK and Ireland

J. Lordan, P. Corris, M. Gatzoulis, 2011, Thorax.

Late-breaking abstract: Demographic trends and changes In long term outcome of incident idiopathic, heritable and anorexigen-associated pulmonary arterial hypertension between 2001 to 2009. Results from the Pulmonary Hypertension Registry of the United Kingdom and Ireland

J. Lordan, P. Corris, M. Gatzoulis, 2011 .

Repeatability and Sensitivity to change of right ventricular analysis methods using cardiac magnetic resonance imaging in PAH: results from the RESPIRE Study

J. Wild, A. Swift, D. Kiely, 2019, Imaging.

FREEDOM-C2: Efficacy And Safety Of Oral Treprostinil Diethanolamine In Combination With An ERA And/Or A PDE5 Inhibitor In Patients With Pulmonary Arterial Hypertension

Z. Jing, Kaifeng Xu, D. Kiely, 2012, ATS 2012.

Pulmonary Vascular Research Institute GoDeep: A meta‐registry merging deep phenotyping datafrom international PH reference centers

H. Ghofrani, F. Grimminger, S. Orfanos, 2022, Pulmonary circulation.

Characteristics And Outcomes In Pulmonary Hypertension Associated With COPD/ Emphysema: Results From The ASPIRE Registry

J. Wild, A. Swift, D. Kiely, 2012, ATS 2012.

Biological heterogeneity in idiopathic pulmonary arterial hypertension identified through unsupervised transcriptomic profiling of whole blood

M. Dunning, M. Humbert, P. Corris, 2021, Nature Communications.

Plasma proteome analysis in patients with pulmonary arterial hypertension: an observational cohort study

M. Humbert, H. Ghofrani, R. Schermuly, 2017, The Lancet. Respiratory medicine.

Pulmonary hypertension: diagnosis and management

D. Kiely, R. Condliffe, C. Elliot, 2013, BMJ : British Medical Journal.

De Novo Truncating Mutations in WASF1 Cause Intellectual Disability with Seizures

Henning Gall, Fengyuan Hu, Kevin Rue-Albrecht, 2018, American journal of human genetics.

Whole-genome sequencing of patients with rare diseases in a national health system

Keith W. Muir, William J. Astle, Mark I. McCarthy, 2020, Nature.

British Thoracic Society Clinical Statement on Pulmonary Arteriovenous Malformations

C. Shovlin, D. Kiely, R. Condliffe, 2017, Thorax.

Identification of Long Noncoding RNA H19 as a New Biomarker and Therapeutic Target in Right Ventricular Failure in Pulmonary Arterial Hypertension

S. Archer, S. Breuils-bonnet, È. Tremblay, 2020, Circulation.

Autologous haematopoietic stem cell transplantation and other cellular therapy in multiple sclerosis and immune-mediated neurological diseases: updated guidelines and recommendations from the EBMT Autoimmune Diseases Working Party (ADWP) and the Joint Accreditation Committee of EBMT and ISCT (JACIE)

M. Sormani, J. D. de Vries-Bouwstra, B. Sharrack, 2019, Bone Marrow Transplantation.

Whole-genome sequencing of a sporadic primary immunodeficiency cohort

William J. Astle, Sri V. V. Deevi, Kenneth G. C. Smith, 2020, Nature.

Reduced microRNA-150 is associated with poor survival in pulmonary arterial hypertension.

L. Huson, H. Ghofrani, R. Schermuly, 2013, American journal of respiratory and critical care medicine.

Genetic determinants of risk in pulmonary arterial hypertension: international genome-wide association studies and meta-analysis

Lisa J. Martin, Keith A. Marsolo, Ferhaan Ahmad, 2018, bioRxiv.

Consensus statement on the management of pulmonary hypertension in clinical practice in the UK and Ireland

G. MacGowan, P. Corris, M. Gatzoulis, 2008, Heart.

A diagnostic miRNA signature for pulmonary arterial hypertension using a consensus machine learning approach

Dennis Wang, N. Morrell, J. Wharton, 2021, EBioMedicine.

Cardiopulmonary interactions of hypoxia and hypercapnia and the role of vasoactive mediators in the pulmonary circulation in man

D. Kiely, 2000 .

The role of vasopressin in cardiorespiratory arrest and pulmonary hypertension.

D. Kiely, K. Channer, A. M. Smith, 2006, QJM : monthly journal of the Association of Physicians.

Left ventricular systolic performance during acute hypoxemia.

B. Lipworth, D. Kiely, R. I. Cargill, 1995, Chest.

Elevated Plasma CXCL12α Is Associated with a Poorer Prognosis in Pulmonary Arterial Hypertension

A. Morton, Caroline O'Connell, Lili Li, 2015, PloS one.

Whole-genome sequencing of patients with rare diseases in a national health system

William J. Astle, Sri V. V. Deevi, Kenneth G. C. Smith, 2020, Nature.

Pulmonary hypertension in COPD: results from the ASPIRE registry

J. Wild, A. Swift, D. Kiely, 2012, European Respiratory Journal.

Statement on Pregnancy in Pulmonary Hypertension from the Pulmonary Vascular Research Institute

T. Lahm, D. Kiely, A. Hemnes, 2015, Pulmonary circulation.

Mining the Plasma Proteome for Insights into the Molecular Pathology of Pulmonary Arterial Hypertension.

M. Humbert, L. Harbaum, R. Schermuly, 2022, American journal of respiratory and critical care medicine.

Traffic exposures, air pollution and outcomes in pulmonary arterial hypertension: a UK cohort study analysis

J. Lordan, P. Corris, M. Haimel, 2019, European Respiratory Journal.

Angiotensin IIReceptor Blockade and Effects on Pulmonary Hemodynamics andHypoxic Pulmonary

D. Kiely, R. Cargill, 2015 .

Haemodynamic and endocrine effects of type 1 angiotensin II receptor blockade in patients with hypoxaemic cor pulmonale.

B. Lipworth, D. Kiely, W. Coutie, 1997, Cardiovascular research.

Angiotensin II receptor blockade and effects on pulmonary hemodynamics and hypoxic pulmonary vasoconstriction in humans.

B. Lipworth, D. Kiely, R. Cargill, 1996, Chest.

Cardiopulmonary assessment of patients with systemic sclerosis for hematopoietic stem cell transplantation: recommendations from the European Society for Blood and Marrow Transplantation Autoimmune Diseases Working Party and collaborating partners

Daniel C. Lee, Sanjiv J. Shah, É. Mousseaux, 2017, Bone Marrow Transplantation.

The use of iloprost in early pregnancy in patients with pulmonary arterial hypertension

G. Mills, D. Kiely, F. Bu'Lock, 2005, European Respiratory Journal.

Inhaled iloprost for severe pulmonary hypertension.

W. Seeger, R. Speich, P. Corris, 2002, The New England journal of medicine.

Combining creative writing and narrative analysis to deliver new insights into the impact of pulmonary hypertension

D. Kiely, R. Condliffe, C. Elliot, 2017, BMJ Open Respiratory Research.

emPHasis-10: development of a health-related quality of life measure in pulmonary hypertension

P. Corris, J. Yorke, D. Kiely, 2013, European Respiratory Journal.

Establishing expert consensus for the optimal approach to holistic risk-management in pulmonary arterial hypertension: a Delphi process and narrative review

J. Lordan, D. Kiely, R. Condliffe, 2021, Expert review of respiratory medicine.

Symptom severity and its effect on health-related quality of life over time in patients with pulmonary hypertension: a multisite longitudinal cohort study

J. Yorke, D. Kiely, M. Campbell, 2018, BMJ Open Respiratory Research.

Pulmonary Artery Size in Interstitial Lung Disease and Pulmonary Hypertension: Association with Interstitial Lung Disease Severity and Diagnostic Utility

J. Wild, A. Swift, D. Kiely, 2018, Front. Cardiovasc. Med..

Multiparametric Magnetic Resonance Imaging in Pulmonary Hypertension

H. Marshall, J. Wild, A. Swift, 2015, Current Cardiovascular Imaging Reports.

Pulmonary Artery Relative Area Change Detects Mild Elevations in Pulmonary Vascular Resistance and Predicts Adverse Outcome in Pulmonary Hypertension

J. Wild, A. Swift, D. Capener, 2012, Investigative radiology.

Semi-automatic thresholding of RV trabeculation improves repeatability and diagnostic value in suspected pulmonary hypertension

S. Alabed, J. Wild, A. Swift, 2023, Frontiers in Cardiovascular Medicine.

Magnetic Resonance Imaging in the Prognostic Evaluation of Patients with Pulmonary Arterial Hypertension

J. Wild, A. Swift, D. Capener, 2017, American journal of respiratory and critical care medicine.

Loss-of-Function ABCC8 Mutations in Pulmonary Arterial Hypertension

W. Chung, Yufeng Shen, F. Dewey, 2018, Circulation Genomic and Precision Medicine.

Dynamic Risk Stratification of Patient Long-Term Outcome After Pulmonary Endarterectomy: Results From the United Kingdom National Cohort

J. Lordan, P. Corris, D. Kiely, 2016, Circulation.

Phenotypic Characterization of EIF2AK4 Mutation Carriers in a Large Cohort of Patients Diagnosed Clinically With Pulmonary Arterial Hypertension

Fengyuan Hu, Kevin Rue-Albrecht, Patrick Deegan, 2017, Circulation.

Critical care management of pulmonary hypertension

David G. Kiely, D. Kiely, R. Condliffe, 2017 .

Maximal Exercise Testing Using the Incremental Shuttle Walking Test Can Be Used to Risk-Stratify Patients with Pulmonary Arterial Hypertension

J. Wild, A. Swift, D. Kiely, 2020, Annals of the American Thoracic Society.

Mild parenchymal lung disease and/or low diffusion capacity impacts survival and treatment response in patients diagnosed with idiopathic pulmonary arterial hypertension

Robert A. Lewis, A. Swift, D. Kiely, 2020, European Respiratory Journal.

Identification of Cardiac Magnetic Resonance Imaging Thresholds for Risk Stratification in Pulmonary Arterial Hypertension

Robert A. Lewis, J. Wild, A. Swift, 2020, American journal of respiratory and critical care medicine.

Utilising artificial intelligence to determine patients at risk of a rare disease: idiopathic pulmonary arterial hypertension

R. Bergemann, V. Salvatelli, O. Doyle, 2019, Pulmonary circulation.

Current and emerging imaging techniques in the diagnosis and assessment of pulmonary hypertension

Jim M. Wild, David G. Kiely, J. Wild, 2018, Expert review of respiratory medicine.

Vascular compression and pulmonary hypertension: the occupational context

D. Kiely, D. Fishwick, 2022, Occupational and Environmental Medicine.

Positioning imatinib for pulmonary arterial hypertension: A phase I/II design comprising dose finding and single-arm efficacy

L. Harbaum, S. Villar, M. Wilkins, 2021, Pulmonary circulation.

Pulmonary Hypertension in Association with Lung Disease: Quantitative CT and Artificial Intelligence to the Rescue? State-of-the-Art Review

E. Hoffman, S. Alabed, J. Wild, 2021, Diagnostics.

A social‐technological epistemology of clinical decision‐making as mediated by imaging

A. Carusi, Sophie van Baalen, D. Kiely, 2016, Journal of evaluation in clinical practice.

Noninvasive estimation of PA pressure, flow, and resistance with CMR imaging: derivation and prospective validation study from the ASPIRE registry.

A. Morton, J. Wild, A. Swift, 2013, JACC. Cardiovascular imaging.

Diagnostic accuracy of cardiovascular magnetic resonance imaging of right ventricular morphology and function in the assessment of suspected pulmonary hypertension results from the ASPIRE registry

Jim M Wild, J. Wild, A. Swift, 2012, Journal of Cardiovascular Magnetic Resonance.

Machine learning cardiac-MRI features predict mortality in newly diagnosed pulmonary arterial hypertension

S. Alabed, R. J. van der Geest, J. Wild, 2022, European heart journal. Digital health.

Pulmonary Hypertension in Patients with Heart Failure and Preserved Ejection Fraction: Differential Diagnosis and Management

A. Swift, D. Kiely, R. Condliffe, 2016, Pulmonary circulation.

Novel imaging techniques in pulmonary hypertension

A. Swift, D. Kiely, C. Johns, 2018, Current opinion in cardiology.

Central venous catheter-related blood stream infections in patients receiving intravenous iloprost for pulmonary hypertension

D. Kiely, R. Condliffe, J. Hurdman, 2013, European Journal of Clinical Microbiology & Infectious Diseases.

Medical artificial intelligence is as much social as it is technological

F. Ciravegna, A. Carusi, D. Kiely, 2023, Nature Machine Intelligence.

Computational platform for doctor–artificial intelligence cooperation in pulmonary arterial hypertension prognostication: a pilot study

A. Sweatt, K. Stenmark, M. Gomberg-Maitland, 2023, ERJ Open Research.

Inhibition of tumor necrosis factor–related apoptosis-inducing ligand (TRAIL) reverses experimental pulmonary hypertension

S. Cross, N. Arnold, D. Crossman, 2012, The Journal of experimental medicine.

Autoimmunity Is a Significant Feature of Idiopathic Pulmonary Arterial Hypertension

C. Wallace, J. Lordan, P. Corris, 2021, American journal of respiratory and critical care medicine.

Longitudinal and Transverse Right Ventricular Function in Pulmonary Hypertension: Cardiovascular Magnetic Resonance Imaging Study from the ASPIRE Registry

Jim M Wild, J. Wild, A. Swift, 2015, Pulmonary circulation.

Integrated Cardiopulmonary MRI Assessment of Pulmonary Hypertension

E. V. van Beek, H. Marshall, S. Alabed, 2021, Journal of magnetic resonance imaging : JMRI.

Lung perfusion: MRI vs. SPECT for screening in suspected chronic thromboembolic pulmonary hypertension

J. Wild, A. Swift, D. Capener, 2017, Journal of magnetic resonance imaging : JMRI.

Pulmonary Artery Strain Predicts Prognosis in Pulmonary Arterial Hypertension.

S. Alabed, L. Zhong, J. Tan, 2023, JACC. Cardiovascular imaging.

CMR Measures of Left Atrial Volume Index and Right Ventricular Function Have Prognostic Value in Chronic Thromboembolic Pulmonary Hypertension

S. Alabed, J. Wild, A. Swift, 2022, Frontiers in Medicine.

Acute hypoxic pulmonary vasoconstriction in man is attenuated by type I angiotensin II receptor blockade.

B. Lipworth, D. Kiely, R. Cargill, 1995, Cardiovascular research.

Hypoxaemia and the renin-angiotensin system: new answers for old questions.

B. Lipworth, D. Kiely, R. I. Cargill, 1994, Pulmonary pharmacology.

Response to: ‘CT assessment for pulmonary hypertension requires systematic assessment of cardiac, vascular and parenchymal signs’ by Marloes et al

D. Kiely, S. Rajaram, J. Wild, 2015, Thorax.

Validation of Artificial Intelligence Cardiac MRI Measurements: Relationship to Heart Catheterization and Mortality Prediction.

D. O’Regan, S. Alabed, R. J. van der Geest, 2022, Radiology.

Non-invasive detection of severe PH in lung disease using magnetic resonance imaging

S. Alabed, J. Wild, A. Swift, 2023, Frontiers in Cardiovascular Medicine.

Assessing pulmonary hypertension severity in lung disease is a key step to improving outcomes: embrace resistance and don't be pressurised to go with the flow

D. Kiely, R. Condliffe, 2021, European Respiratory Journal.

Effects ofHypercapnia on Hemodynamic, Inotropic, Lusitropic, and Electrophysiolog ic

D. Kiely, 2017 .

Assessment of Right Ventricular Function—a State of the Art

S. Alabed, A. Swift, D. Kiely, 2023, Current Heart Failure Reports.

Septal angle on MRI predicts combined pre- and post-capillary pulmonary hypertension

J. Wild, A. Swift, D. Capener, 2017 .

Bosutinib therapy resulting in severe deterioration of pre-existing pulmonary arterial hypertension

D. Kiely, R. Condliffe, C. Elliot, 2016, European Respiratory Journal.

P116 Effects of macitentan on right ventricular remodeling in pulmonary arterial hypertension – results from the REPAIR study interim analysis

A. Torbicki, D. Kiely, A. Tawakol, 2019, Pulmonary hypertension: advances in diagnosis and treatment.

Plasma Metabolomics Implicate Modified Transfer RNAs and Altered Bioenergetics in the Outcome of Pulmonary Arterial Hypertension. 2 Dynamic Risk Stratification of Patient Long-Term Outcome After Pulmonary Endarterectomy: Results From the United Kingdom National Cohort. 2 Initial combination therapy

P. Corris, M. Haimel, M. Bleda, 2016 .

Experimental validation of the hyperpolarized 129Xe chemical shift saturation recovery technique in healthy volunteers and subjects with interstitial lung disease

Jan Wolber, Paul D Griffiths, Helen Marshall, 2015, Magnetic resonance in medicine.

Primary pulmonary artery sarcoma and coexisting chronic thromboembolic pulmonary hypertension.

M. Goddard, J. Wild, A. Swift, 2013, American journal of respiratory and critical care medicine.

Magnetic resonance imaging of ventilation and perfusion changes in response to pulmonary endarterectomy in chronic thromboembolic pulmonary hypertension.

E. V. van Beek, H. Marshall, J. Wild, 2014, American journal of respiratory and critical care medicine.

Results of European post-marketing surveillance of bosentan in pulmonary hypertension

M. Humbert, D. Kiely, J. Carlsen, 2007, European Respiratory Journal.

Combination Therapy with Oral Treprostinil for Pulmonary Arterial Hypertension A Double-Blind Placebo-controlled Clinical Trial

M. Yigla, Akram Khan, C. Bao, 2020 .

Comprehensive Rare Variant Analysis via Whole-Genome Sequencing to Determine the Molecular Pathology of Inherited Retinal Disease.

Dorothy A. Thompson, Sri V. V. Deevi, Eleanor F. Dewhurst, 2017, American journal of human genetics.

Combination Therapy with Oral Treprostinil for Pulmonary Arterial Hypertension. A Double-Blind Placebo-controlled Clinical Trial

M. Yigla, Akram Khan, C. Bao, 2019, American journal of respiratory and critical care medicine.

Statement on imaging and pulmonary hypertension from the Pulmonary Vascular Research Ins9tute (PVRI)

A. Lungu, M. Schiebler, M. Tawhai, 2019 .

Patterns of thromboembolic pulmonary vascular disease in COVID-19

J. Wild, A. Swift, D. Kiely, 2020, Pulmonary circulation.

Telomerecat: A ploidy-agnostic method for estimating telomere length from whole genome sequencing data

Andy G Lynch, Sri V. V. Deevi, Eleanor F. Dewhurst, 2017, Scientific Reports.

Non-invasive methods for estimating mPAP in COPD using cardiovascular magnetic resonance imaging

J. Wild, A. Swift, D. Capener, 2017, European Radiology.

Deprivation and prognosis in patients with pulmonary arterial hypertension: missing the effect of deprivation on a rare disease?

J. Lordan, N. Morrell, M. Wilkins, 2020, European Respiratory Journal.

Age-associated changes in 4D flow CMR derived Tricuspid Valvular Flow and Right Ventricular Blood Flow Kinetic Energy

S. Plein, J. Westenberg, R. J. van der Geest, 2020, Scientific Reports.

Paigen diet-fed apolipoprotein E knockout mice develop severe pulmonary hypertension in an interleukin-1-dependent manner.

D. Crossman, D. Kiely, J. Chamberlain, 2011, The American journal of pathology.

Pulmonary Hypertension and Pregnancy

D. Kiely, L. ten Klooster, V. Wilson, 2020, Respiratory Disease in Pregnancy.

A multicenter study of anticoagulation in operable chronic thromboembolic pulmonary hypertension

P. Corris, S. Villar, D. Kiely, 2019, Journal of thrombosis and haemostasis : JTH.

Telomerecat: A ploidy-agnostic method for estimating telomere length from whole genome sequencing data

Sri V. V. Deevi, Eleanor F. Dewhurst, Courtney E. French, 2017, Scientific Reports.

Acute hypoxic pulmonary vasoconstriction in man is attenuated by type I angiotensin II receptor blockade.

B. Lipworth, D. Kiely, R. I. Cargill, 1995, Cardiovascular research.

CT features of pulmonary arterial hypertension and its major subtypes: a systematic CT evaluation of 292 patients from the ASPIRE Registry

A. Swift, D. Kiely, S. Rajaram, 2014, Thorax.

Computational platform for doctor–artificial intelligence cooperation in pulmonary arterial hypertension prognostication: a pilot study

A. Sweatt, K. Stenmark, M. Gomberg-Maitland, 2022, ERJ Open Research.

Reduced microRNA-150 is associated with poor survival in pulmonary arterial hypertension.

L. Huson, H. Ghofrani, R. Schermuly, 2013, American journal of respiratory and critical care medicine.

Surgery and Anesthesia in Patients with Pulmonary Hypertension

D. Kiely, R. Condliffe, V. Wilson, 2023, Seminars in Respiratory and Critical Care Medicine.

Identification of rare sequence variation underlying heritable pulmonary arterial hypertension

N. Soranzo, Q. Waisfisz, M. Haimel, 2018, Nature Communications.

Improving Prognostication in Pulmonary Hypertension Using AI-quantified Fibrosis and Radiologic Severity Scoring at Baseline CT.

S. Alabed, D. Kiely, S. Rajaram, 2024, Radiology.

Predictors of outcomes in mild pulmonary hypertension according to 2022 ESC/ERS Guidelines: the EVIDENCE-PAH UK study

V. Muthurangu, D. Kiely, L. Howard, 2023, European heart journal.

A transparent artificial intelligence framework to assess lung disease in pulmonary hypertension

S. Alabed, A. Swift, D. Kiely, 2023, Scientific Reports.

Phenotypic Characterization of EIF2AK4 Mutation Carriers in a Large Cohort of Patients Diagnosed Clinically With Pulmonary Arterial Hypertension

Sri V. V. Deevi, Eleanor F. Dewhurst, Lorena E. Lorenzo, 2017, Circulation.

Pulmonary hypertension associated with lung disease: new insights into pathomechanisms, diagnosis, and management.

D. Montani, T. Corte, D. Kiely, 2023, The Lancet. Respiratory medicine.

Comparison of cardiac magnetic resonance imaging, functional and haemodynamic variables in pulmonary arterial hypertension: insights from REPAIR

J. Marcus, D. Kiely, N. Galiè, 2024, ERJ open research.