R. Montgomery

M. Fishbein, R. Colvin, M. Mihatsch, 2003, American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons.

Interaction of AP-2, a monoclonal antibody specific for the human platelet glycoprotein IIb-IIIa complex, with intact platelets.

J. Bennett, R. Montgomery, D. Pidard, 1983, The Journal of biological chemistry.

Life in the shadow of a dominant partner: the FVIII-VWF association and its clinical implications for hemophilia A.

P. Lenting, R. Montgomery, S. Pipe, 2016, Blood.

Third Åland islands conference on von Willebrand disease, 26–28 September 2012: meeting report

V. Jiménez‐Yuste, M. Morfini, M. Makris, 2013, Haemophilia : the official journal of the World Federation of Hemophilia.

Targeting factor VIII expression to platelets for hemophilia A gene therapy does not induce an apparent thrombotic risk in mice

R. Montgomery, Q. Shi, J. G. Mattson, 2017, Journal of thrombosis and haemostasis : JTH.

Relative antithrombotic effects of monoclonal antibodies targeting different platelet glycoprotein-adhesive molecule interactions in nonhuman primates.

S. Hanson, R. Montgomery, L. Harker, 1994, Blood.

Bleeding assessment tools in the diagnosis of VWD in adults and children: a systematic review and meta-analysis of test accuracy

R. Mustafa, J. Eikenboom, R. Montgomery, 2021, Blood advances.

Increased adhesion of erythrocytes to components of the extracellular matrix: isolation and characterization of a red blood cell lipid that binds thrombospondin and laminin.

J. Scott, R. Montgomery, C. Hillery, 1996, Blood.

Acquired Inhibitors of Coagulation

J. Scott, R. Montgomery, 2011 .

Molecular pathogenesis and heterogeneity in type 3 VWD families in U.S. Zimmerman program

D. Bellissimo, R. Montgomery, P. Christopherson, 2022, Journal of thrombosis and haemostasis : JTH.

T-lymphocyte subpopulations in patients with classic hemophilia treated with cryoprecipitate and lyophilized concentrates.

R. Aster, J. Williams, R. Montgomery, 1983, The New England journal of medicine.

Incidence and outcomes of BK virus allograft nephropathy among ABO- and HLA-incompatible kidney transplant recipients.

G. Gupta, R. Montgomery, A. Sharif, 2012, Clinical journal of the American Society of Nephrology : CJASN.

Screening for von Willebrand disease does not impact posttonsillectomy bleeding in a low‐risk population

P. Simpson, R. Montgomery, P. Christopherson, 2021, Pediatric blood & cancer.

Laboratory variability in the diagnosis of type 2 VWD variants

R. Montgomery, P. Christopherson, T. Abshire, 2020, Journal of thrombosis and haemostasis : JTH.

von Willebrand factor variant D1472H has no effect in mice with humanized VWF-platelet interactions.

R. Montgomery, S. Haberichter, V. Flood, 2020, Blood advances.

von Willebrand factor binding to myosin assists in coagulation.

P. Simpson, R. Montgomery, S. Fahs, 2020, Blood advances.

Low VWF levels in children and lack of association with bleeding in children undergoing tonsillectomy.

P. Simpson, R. Montgomery, J. Gill, 2020, Blood advances.

Von Willebrand disease in the United States: perspective from the Zimmerman program.

R. Montgomery, P. Christopherson, J. Cox Gill, 2018, Annals of blood.

Rapid discrimination of the phenotypic variants of von Willebrand disease.

R. Hoffmann, R. Montgomery, J. Gill, 2016, Blood.

What have we learned from large population studies of von Willebrand disease?

R. Montgomery, V. Flood, 2016, Hematology. American Society of Hematology. Education Program.

Platelet‐dependent von Willebrand factor activity. Nomenclature and methodology: communication from the SSC of the ISTH

J. Eikenboom, R. Montgomery, J. Di Paola, 2015, Journal of thrombosis and haemostasis : JTH.

von Willebrand Disease: Biological Diagnosis

R. Montgomery, V. Flood, 2014 .

THROMBOSIS AND HEMOSTASIS No increase in bleeding identi fi ed in type 1 VWD subjects with D 1472 H sequence variation

R. Hoffmann, C. Leissinger, R. Montgomery, 2013 .

von Willebrand's disease: a report from a meeting in the Åland islands

M. Laffan, R. Montgomery, A. Federici, 2012, Haemophilia : the official journal of the World Federation of Hemophilia.

von Willebrand Disease in the United States: A Perspective from Wisconsin

D. Bellissimo, R. Montgomery, J. Gill, 2011, Seminars in thrombosis and hemostasis.

Von Willebrand Disease

J. Scott, R. Montgomery, 2011 .

Absent collagen binding in a VWF A3 domain mutant: utility of the VWF:CB in diagnosis of VWD

R. Hoffmann, R. Montgomery, P. Christopherson, 2010, Journal of thrombosis and haemostasis : JTH.

von Willebrand Disease: Biologic Diagnosis

R. Montgomery, V. Flood, 2010 .

Loss of the largest von Willebrand factor multimers from the plasma of patients with congenital cardiac defects.

R. Montgomery, J. Gill, A. Wilson, 1986, Blood.

Genetic Induction of a Releasable Pool of Factor VIII in Human Endothelial Cells

R. Montgomery, J. Rosenberg, J. Greengard, 2000, Arteriosclerosis, thrombosis, and vascular biology.

von Willebrand disease: a common pediatric disorder.

R. Montgomery, P. Kroner, 2001, Pediatric annals.

The defective interaction between von Willebrand factor and factor VIII in a patient with type 1 von Willebrand disease is caused by substitution of Arg19 and His54 in mature von Willebrand factor.

P. Foster, R. Montgomery, S. Fahs, 1996, Blood.

The rapid differentiation of type IIb von Willebrand's disease from platelet-type (pseudo-) von Willebrand's disease by the "neutral" monoclonal antibody binding assay.

J. Scott, R. Montgomery, J. Scott, 1991, American journal of clinical pathology.

Type 2M:Milwaukee-1 von Willebrand disease: an in-frame deletion in the Cys509-Cys695 loop of the von Willebrand factor A1 domain causes deficient binding of von Willebrand factor to platelets.

R. Montgomery, J. Gill, D. Mancuso, 1996, Blood.

Interactions between von Willebrand factor and Factor VIII: where did they first meet.

R. Montgomery, J. Gill, J. C. Gill, 2000, Journal of pediatric hematology/oncology.

A variant of von Willebrand's disease with abnormal expression of factor VIII procoagulant activity.

R. Montgomery, W. Muntean, L. Jacobson, 1982, Blood.

Molecular basis of human von Willebrand disease: analysis of platelet von Willebrand factor mRNA.

D. Ginsburg, R. Montgomery, J. Gill, 1989, Proceedings of the National Academy of Sciences of the United States of America.

Effects of monoclonal antibodies against the platelet glycoprotein IIb/IIIa complex on thrombosis and hemostasis in the baboon.

S. Hanson, R. Montgomery, L. Harker, 1988, The Journal of clinical investigation.

Effects of reagent and cell-generated hydrogen peroxide on the properties of low density lipoprotein.

C. Nathan, R. Montgomery, Z. Cohn, 1986, Proceedings of the National Academy of Sciences of the United States of America.

The immunogenicity of platelet-derived FVIII in hemophilia A mice with or without preexisting anti-FVIII immunity.

Jianda Hu, Yingyu Chen, R. Montgomery, 2014, Blood.

Platelet gene therapy corrects the hemophilic phenotype in immunocompromised hemophilia A mice transplanted with genetically manipulated human cord blood stem cells.

Yingyu Chen, R. Montgomery, S. Fahs, 2014, Blood.

THROMBOSIS AND HEMOSTASIS Platelet gene therapy corrects the hemophilic phenotype in immunocompromised hemophilia A mice transplanted with genetically manipulated human cord blood stem cells

Yingyu Chen, R. Montgomery, S. Fahs, 2013 .

Inhibition of platelet adhesion to collagen by monoclonal anti‐CD36 antibodies

M. Díaz-Ricart, R. Aster, R. Montgomery, 1996, British journal of haematology.

von Willebrand disease: proposing definitions for future research.

R. Mustafa, M. Ozelo, S. O’Brien, 2021, Blood advances.

Comparison of platelet‐derived and plasma factor VIII efficacy using a novel native whole blood thrombin generation assay

R. Montgomery, Q. Shi, H. Weiler, 2015, Journal of thrombosis and haemostasis : JTH.

Factor VIII inhibitors: von Willebrand factor makes a difference in vitro and in vivo

R. Montgomery, S. Fahs, J. Cox Gill, 2012, Journal of thrombosis and haemostasis : JTH.

Diagnosis and treatment of homozygous protein C deficiency. Report of the Working Party on Homozygous Protein C Deficiency of the Subcommittee on Protein C and Protein S, International Committee on Thrombosis and Haemostasis.

R. Marlar, R. Montgomery, A. Broekmans, 1989, The Journal of pediatrics.

PECAM-1 negatively regulates GPIb/V/IX signaling in murine platelets.

T. Nichols, R. Montgomery, C. Hillery, 2003, Blood.

Thromboelastometry assessment of hemostatic properties in various murine models with coagulopathy and the effect of factor VIII therapeutics

R. Montgomery, Juan Fang, Q. Shi, 2021, Journal of thrombosis and haemostasis : JTH.

Platelet and endothelial expression of clotting factors for the treatment of hemophilia.

R. Montgomery, Q. Shi, 2012, Thrombosis research.

Non‐myeloablative conditioning with busulfan before hematopoietic stem cell transplantation leads to phenotypic correction of murine Bernard‐Soulier syndrome

J. Ware, R. Montgomery, S. Fahs, 2014, Journal of thrombosis and haemostasis : JTH.

Platelet Activation, P-Selectin Mobilization, And Eosinophil Beta1 Integrin Activation Occur In Asthma And Are Associated With Clinical Phenotypes

W. Busse, N. Jarjour, D. Mosher, 2011, Asian Test Symposium.

The cysteine knot of platelet glycoprotein Ib beta (GPIb beta) is critical for the interaction of GPIb beta with GPIX.

P. Morateck, R. Montgomery, D. Kenny, 2002, Blood.

Diagnosis and treatment of homozygous protein C deficiency

R. Marlar, R. Montgomery, A. Broekmans, 1989 .

Characterization of Zebrafish von Willebrand Factor Reveals Conservation of Domain Structure, Multimerization, and Intracellular Storage

Andy H. Vo, J. Shavit, R. Montgomery, 2012, Advances in hematology.

Protein C survival during replacement therapy in homozygous protein C deficiency

R. Marlar, R. Montgomery, R. Sills, 1992, American journal of hematology.

Severe homozygous protein C deficiency.

R. Montgomery, R. Sills, J. Humbert, 1984, The Journal of pediatrics.

Pharmacokinetics of von Willebrand factor and factor VIIIC in patients with severe von Willebrand disease (type 3 VWD): estimation of the rate of factor VIIIC synthesis

C. Kessler, R. Montgomery, J. Gill, 1996, British journal of haematology.

Expression of human factor VIII under control of the platelet-specific alphaIIb promoter in megakaryocytic cell line as well as storage together with VWF.

R. Montgomery, S. Fahs, P. Kroner, 2003, Molecular genetics and metabolism.

Interaction of von Willebrand factor with Staphylococcus aureus.

J. Sixma, R. Montgomery, G. Peters, 1997, The Journal of infectious diseases.

Interaction of von Willebrand factor with human platelets in the plasma milieu.

J. Schullek, R. Montgomery, J. Jordan, 1984, The Journal of clinical investigation.

Mouse VWF again teaches us diversity of mechanisms

R. Montgomery, 2006 .

Acute bleeding emergencies.

R. Montgomery, W. Hathaway, 1980, Pediatric clinics of North America.

Laboratory assays of VWF activity and use of desmopressin trials in the diagnosis of VWD: a systematic review and meta-analysis

R. Mustafa, B. Konkle, J. Eikenboom, 2022, Blood advances.

allelescauses noncell-specific deletion of floxed Germ line activation of the Tie2 and SMMHC

E. Radaelli, J. Haigh, C. Sigmund, 2012 .

Alternative strategies for gene therapy of hemophilia.

R. Montgomery, Q. Shi, 2010, Hematology. American Society of Hematology. Education Program.

Endothelial Cell Processing of von Willebrand Proteins a

Y. Kawai, R. Montgomery, 1987, Annals of the New York Academy of Sciences.

Endothelial cell synthesis of von Willebrand antigen II, von Willebrand factor, and von Willebrand factor/von Willebrand antigen II complex.

R. Montgomery, E. Levin, D. McCarroll, 1985, The Journal of clinical investigation.

On the association of glycoprotein Ib and actin-binding protein in human platelets

J. Okita, R. Montgomery, P. Newman, 1985, The Journal of cell biology.

Synthesis by cultured human umbilical vein endothelial cells of two proteins structurally and immunologically related to platelet membrane glycoproteins IIb and IIIa

Y. Kawai, R. Montgomery, P. Newman, 1986, The Journal of cell biology.

von Willebrand factor and thrombotic thrombocytopenic purpura

R. Montgomery, T. Raife, R. Montgomery, 2000, Current opinion in hematology.

causes deficient binding of von Willebrand factor to platelets the Cys509-Cys695 loop of the von Willebrand factor A1 domain Type 2M:Milwaukee-1 von Willebrand disease: an in-frame deletion in

R. Montgomery, J. Gill, D. Mancuso, 2011 .

Influence of high molecular weight factor VIII on the measurement of low molecular weight factor VIII procoagulant in different assay systems

R. Montgomery, W. Muntean, W. Hathaway, 1982, British journal of haematology.

Acquired von Willebrand's disease in association with Wilm's tumor: regression following treatment.

J. Scott, R. Montgomery, T. Hays, 1981, Blood.

A NEW PLASMA AND PLATELET ANTIGEN DEFICIENT IN SEVERE VON WILLEBRAND'S DISEASE

R. Montgomery, T. Zimmerman, 2022 .

Evaluation of von Willebrand Factor and von Willebrand Factor Propeptide in Models of Vascular Endothelial Cell Activation, Perturbation, and/or Injury

R. Montgomery, Heath C. Thomas, R. Richardson, 2014, Toxicologic pathology.

Cleavage of human von Willebrand factor by platelet calcium-activated protease.

J. Schullek, R. Montgomery, T. Kunicki, 1985, Blood.

Platelet hyperreactivity explains the bleeding abnormality and macrothrombocytopenia in a murine model of sitosterolemia.

T. Kanaji, R. Montgomery, P. Newman, 2013, Blood.

VWF mutations and new sequence variations identified in healthy controls are more frequent in the African-American population.

D. Bellissimo, C. Leissinger, R. Montgomery, 2012, Blood.

Report on the Diagnosis and Treatment of Homozygous Protein C Deficiency

R. Marlar, R. Montgomery, R. Marlar, 1989, Thrombosis and Haemostasis.

Collagen binding provides a sensitive screen for variant von Willebrand disease.

R. Hoffmann, R. Montgomery, J. Gill, 2013, Clinical chemistry.

Critical von Willebrand factor A1 domain residues influence type VI collagen binding

D. Bellissimo, R. Montgomery, J. Gill, 2012, Journal of thrombosis and haemostasis : JTH.

Comparison of type I, type III and type VI collagen binding assays in diagnosis of von Willebrand disease

R. Hoffmann, R. Montgomery, J. Gill, 2012, Journal of thrombosis and haemostasis : JTH.

von Willebrand’s disease diagnosis and laboratory issues

R. Montgomery, G. Castaman, S. Haberichter, 2010, Haemophilia : the official journal of the World Federation of Hemophilia.

Clinical and physiologic studies of two siblings with prekallikrein (Fletcher factor) deficiency.

R. Rivers, R. Montgomery, K. Wuepper, 1976, The American journal of medicine.

The effect of DDAVP on plasma levels of von Willebrand antigen II in normal individuals and patients with von Willebrand's disease.

R. Montgomery, Z. Ruggeri, D. McCarroll, 1984, Blood.

Correction of murine Bernard-Soulier syndrome by lentivirus-mediated gene therapy.

J. Ware, R. Montgomery, S. Fahs, 2010, Molecular therapy : the journal of the American Society of Gene Therapy.

Standardization of von Willebrand factor propeptide: value assignment to the WHO 6th IS Factor VIII/von Willebrand factor, plasma (07/316)

M. Hamill, R. Montgomery, K. Mertens, 2012, Journal of thrombosis and haemostasis : JTH.

Update on the pathophysiology and classification of von Willebrand disease: a report of the Subcommittee on von Willebrand Factor

P. Mannucci, J. Eikenboom, R. Montgomery, 2006, Journal of thrombosis and haemostasis : JTH.

Lentivirus‐mediated platelet gene therapy of murine hemophilia A with pre‐existing anti‐factor VIII immunity

Yingyu Chen, R. Montgomery, S. Fahs, 2012, Journal of thrombosis and haemostasis : JTH.

Hereditary Clotting Factor Deficiencies (Bleeding Disorders)

J. Scott, R. Montgomery, 2011 .

Bleeding disorders: A common cause of menorrhagia in adolescents.

J. Scott, J. Bevan, R. Montgomery, 2001, The Journal of pediatrics.

Low-molecular-weight heparin in thrombotic disease in children and adolescents.

J. Scott, R. Montgomery, J. Gill, 2000, Journal of pediatric hematology/oncology.

Von Willebrand Factor Structure and Function

R. Montgomery, S. Haberichter, 2011 .

More on: are randomized clinical trials the only truth? Not always

P. Mannucci, C. Kessler, P. Monahan, 2006, Journal of thrombosis and haemostasis : JTH.

von Willebrand disease – the relevance of history

R. Montgomery, Robert R. Montgomery, 2005, Journal of thrombosis and haemostasis : JTH.

Regulated release of VWF and FVIII and the biologic implications

R. Montgomery, Q. Shi, S. Haberichter, 2006, Pediatric blood & cancer.

Intravascular recovery of VWF and FVIII following intraperitoneal injection and differences from intravenous and subcutaneous injection in mice

R. Montgomery, S. Fahs, Q. Shi, 2012, Haemophilia : the official journal of the World Federation of Hemophilia.

hemostasis to hemophilia A mice with preexisting FVIII immunity genetically modified to express factor VIII in platelets restores Syngeneic transplantation of hematopoietic stem cells that are

P. Morateck, R. Montgomery, S. Fahs, 2013 .

Syngeneic transplantation of hematopoietic stem cells that are genetically modified to express factor VIII in platelets restores hemostasis to hemophilia A mice with preexisting FVIII immunity.

P. Morateck, R. Montgomery, S. Fahs, 2008, Blood.

Factor IX ectopically expressed in platelets can be stored in alpha-granules and corrects the phenotype of hemophilia B mice.

R. Montgomery, S. Fahs, Q. Shi, 2010, Blood.

Lentivirus‐mediated platelet‐derived factor VIII gene therapy in murine haemophilia A

R. Montgomery, S. Fahs, Q. Shi, 2007, Journal of thrombosis and haemostasis : JTH.

Factor VIII ectopically targeted to platelets is therapeutic in hemophilia A with high-titer inhibitory antibodies.

J. Gorski, P. Morateck, R. Montgomery, 2006, The Journal of clinical investigation.

Crucial role for the VWF A1 domain in binding to type IV collagen.

D. Bellissimo, R. Hoffmann, R. Montgomery, 2015, Blood.

von Willebrand Disease: a Report from a Meeting in the Åland Islands 2012 Summary of a Nordic Symposium on von Willebrand Disease, 26–28 September 2012, Mariehamn, Åland, Finland

V. Jiménez‐Yuste, M. Morfini, M. Makris, 2013 .

Platelets as delivery systems for disease treatments.

R. Montgomery, Q. Shi, 2010, Advanced drug delivery reviews.

Platelet-Targeted Expression of Human BDD-FVIII Reduces Bleeding in Canine Hemophilia A.

T. Nichols, R. Montgomery, Juan Fang, 2009 .

The effect of ABO blood group on the diagnosis of von Willebrand disease.

W. Marks, R. Montgomery, J. Gill, 1987, Blood.

Generalized lymphadenopathy and T cell abnormalities in hemophilia A.

R. Aster, R. Montgomery, J. Gill, 1983, The Journal of pediatrics.

The impact of GPIbα on platelet‐targeted FVIII gene therapy in hemophilia A mice with pre‐existing anti‐FVIII immunity

R. Montgomery, Q. Shi, J. Schroeder, 2019, Journal of thrombosis and haemostasis : JTH.

How we approach: Training pediatric coagulationists

C. Thornburg, R. Montgomery, S. Pipe, 2019, Pediatric blood & cancer.

The biology of von Willebrand factor and factor VIII-regulated release

R. Montgomery, Q. Shi, S. Haberichter, 2009 .

Contribution of platelet vs. endothelial VWF to platelet adhesion and hemostasis

R. Montgomery, S. Fahs, Q. Shi, 2012, Journal of thrombosis and haemostasis : JTH.

Comparison of von Willebrand factor platelet‐binding activity assays: ELISA overreads type 2B with loss of HMW multimers

R. Montgomery, G. Castaman, F. Peyvandi, 2020, Journal of thrombosis and haemostasis : JTH.

An international collaborative study to compare different von Willebrand factor glycoprotein Ib binding activity assays: the COMPASS‐VWF study

R. Montgomery, G. Castaman, F. Peyvandi, 2018, Journal of thrombosis and haemostasis : JTH.

Detection of VWF Copy Number Variations by Microarray Analysis in Von Willebrand Disease Type 3 Index Cases

D. Bellissimo, M. Hegde, R. Montgomery, 2011 .

Gain-of-function GPIb ELISA assay for VWF activity in the Zimmerman Program for the Molecular and Clinical Biology of VWD.

R. Hoffmann, P. Morateck, R. Montgomery, 2011, Blood.

Von Willebrand Disease: Basic and Clinical Aspects

Christine A. Lee, R. Montgomery, A. Federici, 2011 .

Clinical and laboratory diagnosis of von Willebrand disease: A synopsis of the 2008 NHLBI/NIH guidelines

B. Yawn, T. Ortel, R. Montgomery, 2009, American journal of hematology.

Normal range of bleeding scores for the ISTH‐BAT: adult and pediatric data from the merging project

Shamim A. Mollah, B. Coller, R. Montgomery, 2014, Haemophilia : the official journal of the World Federation of Hemophilia.

Common VWF exon 28 polymorphisms in African Americans affecting the VWF activity assay by ristocetin cofactor.

R. Hoffmann, C. Leissinger, P. Morateck, 2010, Blood.

When it comes to von Willebrand disease, does 1 + 1 = 3?

R. Montgomery, R. Montgomery, 2006, Journal of thrombosis and haemostasis : JTH.

regression following treatment Acquired von Willebrand's disease in association with Wilm's tumor:

R. Montgomery, T. Hays, D. Tubergen, 2011 .

The Prevalence of Reduced VWF Survival Phenotype (Type 1C VWD) in Type 1 Index Cases Recruited into the TS Zimmerman Program for the Molecular and Clinical Biology of VWD (ZPMCB - VWD).

D. Bellissimo, C. Leissinger, R. Montgomery, 2007 .

Common VWF Haplotypes in Normal African-Americans and Caucasians Recruited into the ZPMCB-VWD and Their Impact on VWF Laboratory Testing.

D. Bellissimo, C. Leissinger, R. Montgomery, 2007 .

Targeting FVIII expression to endothelial cells regenerates a releasable pool of FVIII and restores hemostasis in a mouse model of hemophilia A.

R. Montgomery, S. Fahs, Q. Shi, 2010, Blood.

Low-dose aspirin protects against lipid accumulation in primate vein bypass grafts.

A. Kissebah, R. Montgomery, G. Olinger, 1987, The Journal of thoracic and cardiovascular surgery.

Afibrinogenemia With Intracerebral Hematoma

S. Natelson, R. Montgomery, 1977 .

Diagnosis of Bernard-Soulier syndrome and Glanzmann's thrombasthenia with a monoclonal assay on whole blood.

R. Montgomery, D. Pidard, T. Kunicki, 1983, The Journal of clinical investigation.

Autoantibodies against platelet glycoprotein Ib in patients with chronic immune thrombocytopenic purpura.

R. Montgomery, P. Tani, R. Mcmillan, 1984, Blood.

von Willebrand's disease antigen II. A new plasma and platelet antigen deficient in severe von Willebrand's disease.

R. Montgomery, T. Zimmerman, 1978, The Journal of clinical investigation.

Type 2M von Willebrand Disease: F606I and I662F Mutations in the Glycoprotein Ib Binding Domain Selectively Impair Ristocetin- but not Botrocetin-Mediated Binding of von Willebrand Factor to Platelets

J. Ponder, J. Scott, R. Montgomery, 1998 .

Neutropenia in a patient with type IB glycogen storage disease: in vitro response to lithium chloride.

E. McCabe, R. Montgomery, D. O'brien, 1980, The Journal of pediatrics.

At least Type VWD2B is a discrete variant of VWD, isn’t it?

N. Mackman, R. Montgomery, 2009 .

the VWF activity assay by ristocetin cofactor Common VWF exon 28 polymorphisms in African Americans affecting

R. Hoffmann, C. Leissinger, P. Morateck, 2012 .

Re-establishment of VWF-dependent Weibel-Palade bodies in VWD endothelial cells.

Sandra L Haberichter, Elizabeth P Merricks, Scot A Fahs, 2005, Blood.

Variable content of von Willebrand factor mutant monomer drives the phenotypic variability in a family with von Willebrand disease.

Junmei Chen, R. Montgomery, Jesse Hinckley, 2015, Blood.

Targeting platelet GPIbα transgene expression to human megakaryocytes and forming a complete complex with endogenous GPIbβ and GPIX

P. Morateck, R. Montgomery, D. Kenny, 2004 .

Platelet and Blood Vessel Disorders

J. Scott, R. Montgomery, 2011 .

Homozygous protein C deficiency: observations on the nature of the molecular abnormality and the effectiveness of warfarin therapy.

R. Marlar, R. Montgomery, W. Zinkham, 1988, Pediatrics.

Newborn Factor VIII Complex: Elevated Activities in Term Infants and Alterations in Electrophoretic Mobility Related to Illness and Activated Coagulatio

R. Montgomery, W. Hathaway, Scott S. Johnson, 1981, British journal of haematology.

Comparative response of plasma VWF in dogs to up-regulation of VWF mRNA by interleukin-11 versus Weibel-Palade body release by desmopressin (DDAVP).

T. Fischer, R. Schaub, J. Keith, 2003, Blood.

HTLV-III serology in hemophilia: relationship with immunologic abnormalities.

R. Montgomery, J. Gill, C. Wood, 1986, The Journal of pediatrics.

Risk for BK viremia and nephropathy after desensitization.

R. Montgomery, A. Sharif, L. Racusen, 2014, Transplantation.

Therapy of von Willebrand Disease

J. Scott, R. Montgomery, J. Scott, 1993, Seminars in thrombosis and hemostasis.

Specific factor VIII-related antigen fragmentation: an in vivo and in vitro phenomenon.

R. Montgomery, J. Johnson, 1982, Blood.

Intracellular trafficking of factor VIII to von Willebrand factor storage granules.

R. Kaufman, P. Foster, R. Montgomery, 1998, The Journal of clinical investigation.

Use of monoclonal antibody to increase the sensitivity and specificity of precipitating immunoassays and cell surface binding immunoassays.

R. Montgomery, T. Kunicki, L. Glodé, 1986, Methods in enzymology.

Use of monoclonal antibody to increase sensitivity and specificity in quantitative immunodiffusion assays.

R. Montgomery, C. G. Smith, L. Glodé, 1982, Journal of immunological methods.

The impact of aberrant von Willebrand factor-GPIbα interaction on megakaryopoiesis and platelets in humanized type 2B von Willebrand disease model mouse

T. Kanaji, R. Montgomery, Y. Morodomi, 2022, Haematologica.

von Willebrand factor storage and multimerization: 2 independent intracellular processes.

R. Montgomery, S. Fahs, S. Haberichter, 2000, Blood.

Common VWF sequence variants associated with higher VWF and FVIII are less frequent in subjects diagnosed with type 1 VWD

D. Bellissimo, J. Johnsen, R. Montgomery, 2018, Research and practice in thrombosis and haemostasis.

Markers of vascular perturbation correlate with airway structural change in asthma.

Stanley J Kruger, W. Busse, S. Fain, 2013, American journal of respiratory and critical care medicine.

Inherited absence of OKT4 lymphocyte antigen in a chronically transfused patient with homozygous sickle cell disease.

R. Montgomery, J. Gill, J. Casper, 1985, Jornal de Pediatria.

Persistence and Progression of Immunologic Abnormalities in Haemophilia

R. Aster, R. Montgomery, J. Casper, 1985, Thrombosis and Haemostasis.

von Willebrand factor levels in the diagnosis of von Willebrand disease: a systematic review and meta-analysis

R. Mustafa, J. Eikenboom, R. Montgomery, 2021, Blood advances.

von Willebrand factor antigen levels are associated with burden of rare nonsynonymous variants in the VWF gene

R. Montgomery, P. Christopherson, J. Di Paola, 2021, Blood.

Fine Mapping of Monoclonal Antibody Epitopes on Human von Willebrand Factor Using a Recombinant Peptide Library

P. Foster, D. Ginsburg, R. Montgomery, 1992, Thrombosis and Haemostasis.

Protein C deficiency.

V. Speights, R. Marlar, R. Montgomery, 1987, Southern medical journal.

THROMBOSIS AND HEMOSTASIS Crucial role for the VWF A 1 domain in binding to type IV collagen

D. Bellissimo, R. Hoffmann, R. Montgomery, 2015 .

Title: Crucial Role for the VWF A1 Domain In Binding to Type IV Collagen Short title: VWF Binds Collagen IV

D. Bellissimo, R. Hoffmann, R. Montgomery, 2015 .

von Willebrand factor binding to myosin assists in coagulation.

P. Simpson, R. Montgomery, S. Fahs, 2018, Blood Advances.

The role of the D1 domain of the von Willebrand factor propeptide in multimerization of VWF.

Y. Kawai, R. Montgomery, S. Fahs, 2002, Blood.

Critical independent regions in the VWF propeptide and mature VWF that enable normal VWF storage.

R. Montgomery, S. Haberichter, P. Jacobi, 2003, Blood.

protease Cleavage of human von Willebrand factor by platelet calcium-activated

J. Schullek, R. Montgomery, T. Kunicki, 2011 .

Platelet von Willebrand's Antigen II: Active Release by Aggregating Agents and a Marker of Platelet Release Reaction In Vivo

R. Montgomery, J. Scott, 1981 .

The endothelial cell receptor stabilin-2 regulates VWF-FVIII complex half-life and immunogenicity

S. Goerdt, R. Montgomery, P. James, 2018, The Journal of clinical investigation.

The heads and the tails of malaria and VWF.

R. Montgomery, 2016, Blood.

Native Whole Blood Thrombin Generation Assay Evaluates Therapeutic Efficacy Of Plasma and Platelet-Derived FVIII

R. Montgomery, Q. Shi, C. Baumgartner, 2013 .

Longitudinal bleeding assessment in von Willebrand disease utilizing an interim bleeding score

R. Montgomery, P. Christopherson, P. James, 2022, Journal of thrombosis and haemostasis : JTH.

β2-GPI dampening of VWF-GPIb interaction

R. Montgomery, 2007 .

Type 2B von Willebrand Disease Associated With the Release of Platelet Agglutinates From Megakaryocytes in the Bone Marrow

A. Rivers, R. Montgomery, K. Friedman, 2008, Journal of pediatric hematology/oncology.

β2-Glycoprotein I inhibits von Willebrand factor-dependent platelet adhesion and aggregation. Commentary

P. Lenting, R. Montgomery, R. Derksen, 2007 .

von Willebrand factor (VWF) propeptide binding to VWF D'D3 domain attenuates platelet activation and adhesion.

S. Neelamegham, R. Montgomery, T. E. Ryan, 2012, Blood.

Von Willebrand Factor propeptide ( VWFpp ) binding to VWF D ’ D 3 domain attenuates platelet activation and adhesion

S. Neelamegham, R. Montgomery, T. E. Ryan, 2012 .

Functional Assay of VWF Measured by Its Interaction with Platelet GPIb without the Use of Ristocetin.

D. Bellissimo, R. Montgomery, D. Kenny, 2007 .

Ristocetin dependent cofactor activity in von Willebrand disease diagnosis: Limitations of relying on a single measure

R. Montgomery, P. Christopherson, T. Abshire, 2022, Research and practice in thrombosis and haemostasis.

No increase in bleeding identified in type 1 VWD subjects with D1472H sequence variation.

R. Hoffmann, C. Leissinger, R. Montgomery, 2013, Blood.

Hypoprothrombinemia: case report

R. Montgomery, W. Hathaway, A. Otsuka, 1978 .

Afibrinogenemia with intracerebral hematoma. Report of a successfully treated case.

S. Natelson, R. Montgomery, 1977, American journal of diseases of children.

Prepooled cryoprecipltate for treatment of hemophilia A *

R. Aster, R. Montgomery, J. Gill, 1983, Transfusion.

PECAM-1 negatively regulates GPIb/V/IX signaling in murine platelets.

T. Nichols, R. Montgomery, C. Hillery, 2003, Blood.

Responsiveness of patients with VWD to DDAVP

R. Montgomery, 2004 .

Fourteen Percent of Healthy African Americans Participating In the Zimmerman Program for the Molecular and Clinical Biology of VWD (ZPMCB VWD) Are Heterozygous for the VWF Gene Mutation H817Q Associated with Type 2N Von Willebrand Disease

D. Bellissimo, R. Montgomery, J. Gill, 2010 .

Quantitative Analysis of Von Willebrand Factor (VWF) Multimers in Von Willebrand Disease (VWD) Patients Recruited through the Zimmerman Program for the Molecular and Clinical Biology of VWD

R. Montgomery, J. Gill, P. Christopherson, 2017 .

Platelets as delivery systems for disease treatments.

R. Montgomery, Q. Shi, 2010, Advanced drug delivery reviews.

Sustained Phenotypic Correction of Murine Hemophilia A with Pre-Existing Anti-FVIII Immunity Using Lentivirus-Mediated Platelet-Specific FVIII Gene Transfer.

R. Montgomery, S. Fahs, Q. Shi, 2009 .

Endothelial and Platelet FVIII/VWF Expression - Divergence in Clinical Effect in Murine Models of Hemophilia A with and without FVIII Inhibitory Antibodies.

R. Montgomery, S. Fahs, Q. Shi, 2006 .

Intracellular interaction of von Willebrand factor and factor VIII depends on cellular context: lessons from platelet-expressed factor VIII.

P. Nurden, M. Poncz, R. Montgomery, 2005, Blood.

Incidence and outcomes of BK virus allograft nephropathy among ABO- and HLA-incompatible kidney transplant recipients.

G. Gupta, R. Montgomery, A. Sharif, 2012, Clinical journal of the American Society of Nephrology : CJASN.

Correlation between circulating levels of von Willebrand's antigen II and von Willebrand factor: discrimination between type I and type II von Willebrand's disease.

R. Montgomery, Z. Ruggeri, D. McCarroll, 1984, The Journal of laboratory and clinical medicine.

Contribution of the glycoprotein Ia 807TT, methylene tetrahydrofolate reductase 677TT and prothrombin 20210GA genotypes to prothrombotic risk among factor V 1691GA (Leiden) carriers

M. Hessner, R. Montgomery, K. Friedman, 1999, British journal of haematology.

A package for VWD endothelial cells

R. Montgomery, 2006 .

Platelet hyperreactivity explains the bleeding abnormality and macrothrombocytopenia in a murine model of sitosterolemia.

T. Kanaji, R. Montgomery, P. Newman, 2013, Blood.

At least type VWD2B is a discrete variant of VWD, isn't it?

R. Montgomery, 2009, Blood.

Specific Factor VIII Fragmentation in Commercial Factor VIII Concentrates

R. Montgomery, 1979, Thrombosis and Haemostasis.