G. Lenoir

发表

In vitroprediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study

J. Rousset, L. Bidou, I. Sermet-Gaudelus, 2007 .

Impact of polymorphism of Multidrug Resistance-associated Protein 1 (ABCC1) gene on the severity of cystic fibrosis.

P. Lebecque, K. Dahan, A. Mafficini, 2011, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Myeloperoxidase Promoter Polymorphism −463G Is Associated With More Severe Clinical Expression of Cystic Fibrosis Pulmonary Disease

I. Sermet-Gaudelus, B. Descamps-Latscha, G. Lenoir, 2006, Mediators of inflammation.

Efficacy, Safety, and Local Pharmacokinetics of Highly Concentrated Nebulized Tobramycin in Patients with Cystic Fibrosis Colonized with Pseudomonas aeruginosa

G. Lenoir, P. Moretti, G. Varoli, 2007, Paediatric drugs.

Chloride transport in nasal ciliated cells of cystic fibrosis heterozygotes.

I. Hurbain, I. Sermet-Gaudelus, J. Bresson, 2005, American journal of respiratory and critical care medicine.

In vivo correlates for Streptococcus pneumoniae penicillin resistance in acute otitis media

P. Berche, G. Lenoir, P. Géhanno, 1995, Antimicrobial agents and chemotherapy.

Insulin Responses to Intravenous Glucose and the Hyperglycemic Clamp in Cystic Fibrosis Patients with Different Degrees of Glucose Tolerance

G. Lenoir, J. Robert, B. Rakotoambinina, 1994, Pediatric Research.

In Cystic Fibrosis Homozygotes and Heterozygotes, Neutrophil Apoptosis Is Delayed and Modulated by Diamide or Roscovitine: Evidence for an Innate Neutrophil Disturbance

G. Lenoir, V. Witko-Sarsat, Sandra Moriceau, 2010, Journal of Innate Immunity.

Coronin-1 Is Associated with Neutrophil Survival and Is Cleaved during Apoptosis: Potential Implication in Neutrophils from Cystic Fibrosis Patients1

I. Guerrera, I. Sermet-Gaudelus, C. Danel, 2009, The Journal of Immunology.

Mycobacterium abscessus and Children with Cystic Fibrosis

P. Berche, I. Sermet-Gaudelus, J. Gaillard, 2003, Emerging infectious diseases.

Measurement of nasal potential difference in young children with an equivocal sweat test following newborn screening for cystic fibrosis

C. Thauvin-Robinet, I. Sermet-Gaudelus, I. Fajac, 2010, Thorax.

Antibiotic prevention of pneumococcal infections in asplenic hosts: admission of insufficiency

G. Lenoir, M. Montalembert, 2003, Annals of Hematology.

Evaluation of nasopharyngeal cultures for bacteriologic assessment of acute otitis media in children.

P. Berche, G. Lenoir, P. Géhanno, 1996, The Pediatric infectious disease journal.

Nasal polyposis and cystic fibrosis(CF): review of the literature.

C. Elie, B. Lacour, I. Sermet, 2011, Rhinology.

Induction by antitumoral drugs of proteins that functionally complement CFTR: a novel therapy for cystic fibrosis?

G. Lenoir, V. Stoven, J. Boucher, 1997, The Lancet.

Interest of colchicine for the treatment of cystic fibrosis patients. Preliminary report.

I. Sermet-Gaudelus, B. Descamps-Latscha, P. Reinert, 1999, Mediators of Inflammation.

Feasibility and efficacy of chronic transfusion for stroke prevention in children with sickle cell disease

G. Lenoir, M. Dumont, M. de Montalembert, 2010, European journal of haematology.

Does regular blood transfusion prevent progression of cerebrovascular lesions in children with sickle cell disease?

L. Hertz-Pannier, J. Bresson, G. Lenoir, 2009, Annals of Hematology.

Cystic Fibrosis Patients Potential Implication in Neutrophils from Survival and Is Cleaved during Apoptosis : Coronin-1 Is Associated with Neutrophil

I. Guerrera, I. Sermet-Gaudelus, C. Danel, 2009 .

Evaluation of MRP1-5 Gene Expression in Cystic Fibrosis Patients Homozygous for the ΔF508 Mutation

J. Bernaudin, I. Hurbain, I. Sermet-Gaudelus, 2003, Pediatric Research.

Insulin-like growth factor I correlates with lean body mass in cystic fibrosis patients

J. Souberbielle, I. Sermet-Gaudelus, G. Lenoir, 2003, Archives of disease in childhood.

Early renal changes in hemizygous and heterozygous patients with Fabry's disease.

D. Droz, M. Gubler, J. Grünfeld, 1978, Kidney international.

An Original hypercalcemic infantile renal tumor without bone metastasis: Heterotransplantation to nude mice report of two cases

G. Lenoir, S. Avril, C. Nezelof, 1982, Cancer.

Low bone mineral density in young children with cystic fibrosis.

J. Souberbielle, I. Sermet-Gaudelus, G. Lenoir, 2007, American journal of respiratory and critical care medicine.

Effects of 25-hydroxycholecalciferol on bone lesions of children with terminal renal failure.

G. Lenoir, G. Witmer, O. Fontaine, 1976, Kidney international.

Synthesis of intrathecal interferon in systemic lupus erythematosus with neurological complications.

P. Lebon, G. Lenoir, A. Lagrue, 1983, British medical journal.

Glutathione S-transferases related to P. aeruginosa lung infection in cystic fibrosis children: preliminary study.

M. Loriot, P. Beaune, B. Lacour, 2009, Clinical biochemistry.

Glucose tolerance and insulin secretion, morbidity, and death in patients with cystic fibrosis.

G. Velho, I. Sermet, E. Bismuth, 2008, The Journal of pediatrics.

Pain in children and adults with cystic fibrosis: a comparative study.

I. Sermet-Gaudelus, G. Lenoir, D. Dusser, 2009, Journal of pain and symptom management.

Ultrastructure of muscle and sensory nerve in Fabry's disease

G. Lenoir, M. Fardeau, F. Tomé, 1977, Acta Neuropathologica.

Nasal potential difference in cystic fibrosis diagnosis of very young children.

I. Sermet-Gaudelus, E. Girodon, G. Lenoir, 2007, The Journal of pediatrics.

The CF-CIRC study: a French collaborative study to assess the accuracy of Cystic Fibrosis diagnosis in neonatal screening

P. Reix, G. Bellon, I. Sermet-Gaudelus, 2006, BMC pediatrics.

Localization of the gene for fibrodysplasia ossificans progressiva (FOP) to chromosome 17q21-22.

G. Lenoir, K. Fontaine, G. Lucotte, 2000, Genetic counseling.

Sputum Itraconazole Concentrations in Cystic Fibrosis Patients

P. Berche, I. Sermet-Gaudelus, C. Hennequin, 2001, Antimicrobial Agents and Chemotherapy.

[Circulating metabolites of vitamin D in 14 children with hypercalcemia].

G. Lenoir, E. Jacqz, M. Garabédian, 1985, Archives francaises de pediatrie.

Effects of long-term maintenance therapy with a new glucocorticoid, deflazacort, on mineral metabolism and statural growth

G. Lenoir, A. Bourdeau, S. Balsan, 1987, Calcified Tissue International.

Characterization of the monoamine uptake system in catecholamine storage vesicles isolated from a pheochromocytoma taken from a child.

M. Roisin, J. Henry, G. Lenoir, 1984, Biochemical pharmacology.

Nebulized Antibiotics in Cystic Fibrosis

I. Sermet-Gaudelus, G. Lenoir, A. Ferroni, 2002, Paediatric drugs.

A Double-Blind Comparison of RU-41740 (‘Biostim’) and Placebo in Recurrent Upper Respiratory Tract Infections in Children with Cystic Fibrosis

G. Lenoir, J. Derelle, D. Olive, 1991 .

Elevated plasma 1,25-dihydroxyvitamin D concentrations in infants with hypercalcemia and an elfin facies.

G. Lenoir, E. Jacqz, M. Garabédian, 1985, The New England journal of medicine.

Mutations of the noggin (NOG) and of the activin A type I receptor (ACVR1) genes in a series of twenty-seven French fibrodysplasia ossificans progressiva (FOP) patients.

G. Lenoir, G. Lucotte, A. Houzet, 2009, Genetic counseling.

Endoscopic and CT-scan evaluation of rhinosinusitis in cystic fibrosis.

G. Lenoir, A. Coste, R. Peynègre, 1995, Rhinology.

Use of 16S rRNA Gene Sequencing for Identification of Nonfermenting Gram-Negative Bacilli Recovered from Patients Attending a Single Cystic Fibrosis Center

P. Berche, E. Abachin, I. Sermet-Gaudelus, 2002, Journal of Clinical Microbiology.

Primary cytomegalovirus infection, atypical Kawasaki disease, and coronary aneurysms in 2 infants.

J. Casanova, P. Quartier, G. Lenoir, 2005, Clinical infectious diseases : an official publication of the Infectious Diseases Society of America.

In vitro susceptibilities to amphotericin B, itraconazole, and miconazole of filamentous fungi isolated from patients with cystic fibrosis

P. Berche, J. Gaillard, C. Hennequin, 1997, Antimicrobial agents and chemotherapy.

Proteinase 3, a potent secretagogue in airways, is present in cystic fibrosis sputum.

J. Nadel, I. Ueki, B. Descamps-Latscha, 1999, American journal of respiratory cell and molecular biology.

110 Head-to-head comparison of two inhaled tobramycin solutions in cystic fibrosis (CF) patients with chronic Pseudomonas aeruginosa (Pa) infection

A. Chuchalin, G. Lenoir, G. Gandini, 2011 .

Gonadal effects of chlorambucil given to prepubertal and pubertal boys for nephrotic syndrome.

G. Lenoir, P. Guesry, M. Broyer, 1978, The Journal of pediatrics.

High-cost benefit of chlorambucil in frequent relapsing neprhosis.

G. Lenoir, P. Guesry, M. Broyer, 1977, The New England journal of medicine.

Basic protocol for transepithelial nasal potential difference measurements.

Michael R Knowles, Jean Lebacq, Patrick Lebecque, 2004, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Increased PIVKA-II concentrations in patients with cystic fibrosis.

G. Lenoir, J. Lefrère, M. Montalembert, 1992, Journal of clinical pathology.

Myocardial ischaemia in children with sickle cell disease

C. Maunoury, P. Acar, G. Lenoir, 2004, Archives of Disease in Childhood.

Valproic acid: a possible cause of proximal tubular renal syndrome.

M. Gubler, G. Lenoir, J. Pérignon, 1981, The Journal of pediatrics.

6q1 monosomy: a distinctive syndrome

M. Cabanis, G. Lenoir, C. Turleau, 1988, Clinical genetics.

Insight into cystic fibrosis by structural modelling of CFTR first nucleotide binding fold (NBF1).

S. Blanquet, G. Lenoir, F. Bontems, 1997, Comptes rendus de l'Academie des sciences. Serie III, Sciences de la vie.

Correction to: In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study

J. Rousset, L. Bidou, I. Sermet-Gaudelus, 2018, BMC Medicine.

[Neonatal primary hyperparathyroidism caused by clear cell hyperplasia].

G. Lenoir, G. Chomette, G. Chéron, 1985, Pediatrie.

Studies of variations of subcutaneously infused desferrioxamine and iron movements in thalassaemia children

P. Houzé, G. Lenoir, R. Girot, 1989, European Journal of Pediatrics.

Priming of blood neutrophils in children with cystic fibrosis: correlation between functional and phenotypic expression of opsonin receptors before and after platelet-activating factor priming.

R. Allen, I. Sermet-Gaudelus, B. Descamps-Latscha, 1999, The Journal of infectious diseases.

Cutis laxa and the Costello syndrome

J. Kaplan, T. Bienvenu, N. Fonknechten, 2022 .

[Body temperature measurement in daily practice].

I. Sermet-Gaudelus, G. Lenoir, I. Chadelat, 2005, Archives de pediatrie : organe officiel de la Societe francaise de pediatrie.

Cardiac Involvement in Cystic Fibrosis Revealed by a Ventricular Arrhythmia

G. Lenoir, G. Chéron, D. Stéru, 1984, Acta paediatrica Scandinavica.

Four new haplotypes observed in Algerian β-thalassemia patients

D. Labie, G. Lenoir, C. Beldjord, 2004, Human Genetics.

Cystic fibrosis patients' B‐lymphocyte response is resistant to the in vitro enhancing effect of corticosteroids

M. Auffredou, J. Dayer, G. Lenoir, 1990, European journal of clinical investigation.

[Joint tolerance of pefloxacin and ofloxacin in children and adolescents with cystic fibrosis].

C. Menkes, G. Lenoir, E. Pertuiset, 1989, Revue du rhumatisme et des maladies osteo-articulaires.

Diffuse arterial calcified elastopathy--a new cause of renovascular hypertension in children.

C. Antignac, M. Gubler, L. Garel, 1985, The International journal of pediatric nephrology.

Plasmodium falciparum malaria after three years in a non-endemic area.

G. Lenoir, A. Datry, M. Daniš, 1988, Transactions of the Royal Society of Tropical Medicine and Hygiene.

December 2002 Fellowships Grants and Awards

I. Sermet-Gaudelus, B. Descamps-Latscha, G. Lenoir, 2002, Environmental Health Perspectives.

Coexistence of antenatal, infantile, and juvenile nephrotic syndrome in a single family.

G. Lenoir, M. Broyer, R. Habib, 1981, The Journal of pediatrics.

Normal Function of the Cystic Fibrosis Conductance Regulator Protein Can Be Associated with Homozygous ΔF508 Mutation

J. Bernaudin, I. Sermet-Gaudelus, J. Bresson, 2002, Pediatric Research.

Nyctohemeral Rhythm of Plasma Renin Activity and Plasma Aldosterone in Children

G. Lenoir, J. Limal, M. Déchaux, 1982, Pediatric Research.

FAMILIAL NEPHROSIS (FN)

M. Gubler, G. Lenoir, M. Broyer, 1980, Pediatric Research.

[Isolated primary nocturnal enuresis: international evidence based management. Consensus recommendations by French expert group].

G. Lenoir, E. Bérard, H. Lottmann, 2010, Progres en urologie : journal de l'Association francaise d'urologie et de la Societe francaise d'urologie.

Absence of Modifications of the Enzyme Defense System against Oxygen Toxicity in Cystic Fibrosis

G. Lenoir, P. Sinet, A. Nicole, 1983, Pediatric Research.

Clinical phenotype and genotype of children with borderline sweat test and abnormal nasal epithelial chloride transport.

Milan Macek, Gérard Lenoir, J. Sarles, 2010, American journal of respiratory and critical care medicine.

Bacterial contamination in the environment of hospitalised children with cystic fibrosis.

P. Berche, I. Sermet-Gaudelus, G. Lenoir, 2008, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Cystic fibrosis arthritis. A report of five cases.

C. Menkes, G. Lenoir, E. Pertuiset, 1992, British journal of rheumatology.

Nucleotide sequence polymorphism in a hotspot mutation region of the p53 gene.

C. Theillet, H. Lynch, P. Jeanteur, 1992, Oncogene.

A new mutation of the noggin gene in a French Fibrodysplasia ossificans progressiva (FOP) family.

G. Lenoir, K. Fontaine, G. Lucotte, 2005, Genetic counseling.

Inflammation and CFTR: might neutrophils be the key in cystic fibrosis?

I. Sermet-Gaudelus, B. Descamps-Latscha, G. Lenoir, 1999, Mediators of inflammation.

Novel CFTR mutations in black cystic fibrosis patients

J. Steffann, I. Sermet, G. Lenoir, 2004, Clinical genetics.

[Cystic fibrosis in an African child. Apropos of a case].

G. Lenoir, G. Chéron, P. Challier, 1984, Archives francaises de pediatrie.

184 Aerosolized tobramycin in the treatment of patients with Cystic Fibrosis and Pseudomonas aeruginosa infection

G. Lenoir, G. Varoli, N. Aryayev, 2006 .

Effect of mutator P. aeruginosa on antibiotic resistance acquisition and respiratory function in cystic fibrosis

F. Taddei, P. Berche, I. Sermet-Gaudelus, 2009, Pediatric pulmonology.

[Fabry's disease in ophthalmology (author's transl)].

M. Gubler, G. Lenoir, J. Dufier, 1980, Journal francais d'ophtalmologie.

French multicenter randomized double‐blind placebo‐controlled trial on nebulized amiloride in cystic fibrosis patients

P. Chaumet‐Riffaud, J. Navarro, G. Lenoir, 2000, Pediatric pulmonology.

therapy products gene and protein cystic fibrosis and inducing a glutathione transporter function

J. Annereau, G. Lenoir, J. Lallemand, 1997 .

Disturbed myeloperoxidase-dependent activity of neutrophils in cystic fibrosis homozygotes and heterozygotes, and its correction by amiloride.

R. Allen, B. Descamps-Latscha, M. Paulais, 1996, Journal of immunology.

Sandimmun neoral improves the bioavailability of cyclosporin A and decreases inter-individual variations in patients affected with cystic fibrosis.

F. Gottrand, G. Bellon, G. Lenoir, 1995, Transplantation proceedings.

Correlation between activity of beta-lactam agents in vitro and bacteriological outcome in acute pulmonary exacerbations of cystic fibrosis

C. Delacourt, P. Cahen, G. Lenoir, 1995, European Journal of Clinical Microbiology and Infectious Diseases.

Rapid Improvement of Intracranial Tuberculomas After Addition of Ofloxacin to First-Line Antituberculosis Treatment

I. Sermet-Gaudelus, J. Gaillard, G. Lenoir, 1999, European Journal of Clinical Microbiology and Infectious Diseases.

[Fabry's disease. Carbamazepine therapy in acrodyniform syndrome].

M. Gubler, G. Lenoir, F. Tomé, 1977, Archives francaises de pediatrie.

Exhaled nitric oxide in cystic fibrosis: relationships with airway and lung vascular impairments

L. Trinquart, C. Delclaux, A. Clément, 2009, European Respiratory Journal.

Hereditary Hypophosphatemic Rickets with Hypercalciuria: Report of a New Kindred

I. Sermet-Gaudelus, G. Lenoir, M. Déchaux, 2001, Nephron.

[Novel therapies for cystic fibrosis in 2009].

I. Sermet-Gaudelus, G. Lenoir, A. Edelman, 2009, Archives de pediatrie : organe officiel de la Societe francaise de pediatrie.

[Endoscopic endonasal ethmoidectomy in severe sinusitis of cystic fibrosis. Mid-term results in 12 patients].

P. Reinert, G. Lenoir, A. Coste, 1997, Annales d'oto-laryngologie et de chirurgie cervico faciale : bulletin de la Societe d'oto-laryngologie des hopitaux de Paris.

Maternally inherited duplication of the mitochondrial genome in a syndrome of proximal tubulopathy, diabetes mellitus, and cerebellar ataxia.

A. Munnich, P. Rustin, A. Rötig, 1992, American journal of human genetics.