K. Agematsu

K. Agematsu, Y. Okubo, A. Tsukadaira, 2000, Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology.

Mosaicism of an ELANE Mutation in an Asymptomatic Mother

O. Ohara, Y. Nakazawa, K. Agematsu, 2019, Journal of Clinical Immunology.

Genetic defect in human X-linked agammaglobulinemia impedes a maturational evolution of pro-B cells into a later stage of pre-B cells in the B-cell differentiation pathway.

H. Kanegane, T. Miyawaki, H. Karasuyama, 2000, Blood.

Secretory IgA, salivary peroxidase, and catalase-mediated microbicidal activity during hydrogen peroxide catabolism in viridans streptococci: pathogen coaggregation.

Y. Konishi, T. Sugiura, N. Yoshino, 2006, The Journal of infectious diseases.

Synergistic augmentative effect of interleukin‐10 and CD27/CD70 interactions on B‐cell immunoglobulin synthesis

K. Agematsu, H. Nagumo, 1998, Immunology.

Memory B Cells into Plasma Cells Secretion by Promoting the Differentiation of CD27/CD70 Interaction Augments IgE

T. Nikaido, K. Shinozaki, K. Agematsu, 1998 .

Prominent eosinophilia but less eosinophil activation in a patient with Omenn syndrome

Y. Hayashi, T. Morio, Masahiko Kato, 2010, Pediatrics international : official journal of the Japan Pediatric Society.

Toll-like receptor signaling is impaired in dendritic cells from patients with X-linked agammaglobulinemia.

H. Kanegane, T. Kaisho, T. Miyawaki, 2008, Clinical immunology.

Hypercalcemia associated with all-trans-retinoic acid in the treatment of acute promyelocytic leukemia.

K. Koike, A. Komiyama, T. Nakahata, 1993, Leukemia research.

Cytogenetic clonality analysis in monosomy 7 associated with juvenile myelomonocytic leukemia: clonality in B and NK cells, but not in T cells.

K. Koike, A. Komiyama, K. Agematsu, 1998, Leukemia research.

Dramatic Improvement in the Multifocal Positron Emission Tomography Findings of a Young Adult with Chronic Granulomatous Disease Following Allogeneic Hematopoietic Stem Cell Transplantation

K. Koike, Y. Nakazawa, K. Agematsu, 2014, Journal of Clinical Immunology.

Hematopoietic stem cell transplantation for pulmonary alveolar proteinosis associated with primary immunodeficiency disease

H. Kanegane, T. Morio, M. Takagi, 2018, International Journal of Hematology.

Clonal expansion of Epstein–Barr virus (EBV)-infected γδ T cells in patients with chronic active EBV disease and hydroa vacciniforme-like eruptions

K. Agematsu, M. Hasegawa, K. Takehara, 2012, International Journal of Hematology.

Defect of suppression of inflammasome-independent interleukin-8 secretion from SW982 synovial sarcoma cells by familial Mediterranean fever-derived pyrin mutations

K. Migita, K. Agematsu, J. Masumoto, 2013, Molecular Biology Reports.

MicroRNA-204-3p inhibits lipopolysaccharide-induced cytokines in familial Mediterranean fever via the phosphoinositide 3-kinase &ggr; pathway

K. Yoshiura, K. Migita, K. Eguchi, 2018, Rheumatology.

Detection of Bruton's tyrosine kinase mutations in hypogammaglobulinaemic males registered as common variable immunodeficiency (CVID) in the Japanese Immunodeficiency Registry

H. Kanegane, T. Miyawaki, A. Komiyama, 2000, Clinical and experimental immunology.

Femoral osteomyelitis due to Cladophialophora arxii in a patient with chronic granulomatous disease

K. Koike, K. Nishimura, K. Agematsu, 2009, Infection.

Subcutaneous abscess due to the basidiomycete Phellinus mori in a patient with chronic granulomatous disease

K. Koike, Y. Nakazawa, K. Nishimura, 2015, Infection.

Dramatic Improvement in the Multifocal Positron Emission Tomography Findings of a Young Adult with Chronic Granulomatous Disease Following Allogeneic Hematopoietic Stem Cell Transplantation

K. Koike, Y. Nakazawa, K. Agematsu, 2014, Journal of Clinical Immunology.

Defective IL-10 signaling in hyper-IgE syndrome results in impaired generation of tolerogenic dendritic cells and induced regulatory T cells

H. Takada, T. Hara, M. Nagasawa, 2011, The Journal of experimental medicine.

Molecular explanation for the contradiction between systemic Th17 defect and localized bacterial infection in hyper-IgE syndrome

H. Takada, T. Hara, M. Nagasawa, 2009, The Journal of experimental medicine.

Absence of memory B cells in patients with common variable immunodeficiency.

H. Ochs, T. Miyawaki, S. Koyasu, 2002, Clinical immunology.

Regulation of Aged Humoral Immune Defense against Pneumococcal Bacteria by IgM Memory B Cell

K. Agematsu, T. Yamazaki, Y. Uehara, 2005, The Journal of Immunology.

Functional analysis of human memory B-cell subpopulations: IgD+CD27+ B cells are crucial in secondary immune response by producing high affinity IgM.

H. Ochs, K. Agematsu, K. Sugane, 2003, Clinical immunology.

Memory B cells and CD27.

K. Agematsu, 2000, Histology and histopathology.

150820-ms for KURA

T. Akagi, K. Agematsu, M. Muraoka, 2015 .

Neutrophil-specific granule deficiency: homozygous recessive inheritance of a frameshift mutation in the gene encoding transcription factor CCAAT/enhancer binding protein--epsilon.

H P Koeffler, A Komiyama, H. Koeffler, 2001, Blood.

Inhibition of methicillin-resistant Staphylococcus aureus colonization of oral cavities in newborns by viridans group streptococci.

Tomohiko Nakamura, H. Nakama, K. Agematsu, 2001, Clinical infectious diseases : an official publication of the Infectious Diseases Society of America.

Juvenile onset autoinflammatory disease due to a novel mutation in TNFAIP3 (A20)

K. Migita, Y. Kawasaki, M. Yashiro, 2018, Arthritis Research & Therapy.

Recipient origin of bone marrow‐derived fibroblastic stromal cells during all periods following bone marrow transplantation in humans

K. Agematsu, Yutaka Nakahori, 1991, British journal of haematology.

Antibodies to myelin oligodendrocyte glycoprotein are not involved in the severity of chronic non-remitting experimental autoimmune encephalomyelitis.

T. Honjo, M. Muramatsu, K. Agematsu, 2009, Immunology letters.

Protein kinase A-mediated phosphorylation of the T-cell surface antigen CD27.

C. Morimoto, K. Agematsu, Y. Nojima, 1993, Immunology.

Clinical and laboratory features of fatal rapidly progressive interstitial lung disease associated with juvenile dermatomyositis.

S. Takezaki, M. Yamada, I. Kobayashi, 2015, Rheumatology.

Ki-1 positive large cell anaplastic lymphoma: multiple bone lytic lesions and interleukin-6.

A. Komiyama, K. Agematsu, 1992, Leukemia & lymphoma.

Detection of engraftment and chimerism after bone marrow transplantation by in situ hybridization using a Y‐chromosome specific probe

A. Komiyama, Y. Nakahori, K. Agematsu, 1990, American journal of hematology.

Quantification of κ-deleting recombination excision circles in Guthrie cards for the identification of early B-cell maturation defects.

O. Ohara, H. Kanegane, H. Takada, 2011, The Journal of allergy and clinical immunology.

Spontaneous production of interleukin-6 by Ki-1-positive large-cell anaplastic lymphoma with extensive bone destruction.

T. Nakahata, K. Agematsu, T. Katsuyama, 1991, Blood.

A Case Report of Familial Mediterranean Fever Diagnosed Following the Total Knee Arthroplasty

M. Minami, Koji Suzuki, K. Agematsu, 2015, HSS Journal ®.

Next-generation sequencing of the whole MEFV gene in Japanese patients with familial Mediterranean fever: a case-control association study.

K. Yoshiura, K. Migita, K. Eguchi, 2020, Clinical and experimental rheumatology.

Complete arrest from pro‐ to pre‐B cells in a case of B cell‐negative severe combined immunodeficiency (SCID) without recombinase activating gene (RAG) mutations

H. Kanegane, T. Miyawaki, A. Komiyama, 2001, Clinical and experimental immunology.

DNA Cross-Link Repair Protein SNM1A Interacts with PIAS1 in Nuclear Focus Formation

H. Arakawa, J. Buerstedde, M. Takata, 2004, Molecular and Cellular Biology.

Human tyrosine kinase 2 deficiency reveals its requisite roles in multiple cytokine signals involved in innate and acquired immunity.

T. Morio, H. Ochs, H. Takada, 2006, Immunity.

A thiol proteinase inhibitor, E‐64‐d, corrects the abnormalities in concanavalin A cap formation and the lysosomal enzyme activity in leucocytes from patients with Chediak–Higashi syndrome by reversing the down‐regulated protein kinase C activity

T. Hara, T. Onodera, A. Komiyama, 2001, Clinical and experimental immunology.

Mechanism of hypergammaglobulinemia by HIV infection: circulating memory B-cell reduction with plasmacytosis.

A. Komiyama, K. Agematsu, K. Sugane, 2001, Clinical immunology.

Familial Mediterranean fever with P369S/R408Q exon3 variant in pyrin presenting as symptoms of PFAPA

Keiko Kobayashi, K. Agematsu, Tomoyuki Nakamura, 2017, Modern rheumatology.

Absence of IgD-CD 27 ( + ) memory B cell population in X-linked hyper-IgM syndrome

H. Ochs, A. Komiyama, S. Nonoyama, 2018 .

Direct B/B–cell interactions in immunoglobulin synthesis

K. Shinozaki, K. Agematsu, K. Yasui, 2001, Clinical and experimental immunology.

Oligoclonal expansion of T lymphocytes with multiple second-site mutations leads to Omenn syndrome in a patient with RAG1-deficient severe combined immunodeficiency.

Y. Hayashi, Masahiko Kato, K. Agematsu, 2005, Blood.

Novel Artemis gene mutations of radiosensitive severe combined immunodeficiency in Japanese families

Y. Fukushima, H. Ochs, A. Komiyama, 2003, Human Genetics.

Effects of increased telomerase activity on radiosensitive human SCID cells

H. Shirasawa, T. Hiwasa, N. Suzuki, 2002 .

Chondrodysplasia punctata with X;Y translocation

K. Koike, Y. Nakahori, K. Agematsu, 1988, Human Genetics.

Familial Mediterranean Fever

A. Nakamura, K. Migita, K. Eguchi, 2014, Medicine.

Identification of Disease-Promoting HLA Class I and Protective Class II Modifiers in Japanese Patients with Familial Mediterranean Fever

A. Nakamura, K. Migita, K. Eguchi, 2015, PloS one.

Thalidomide as an immunotherapeutic agent: the effects on neutrophil-mediated inflammation.

K. Agematsu, T. Yamazaki, N. Kobayashi, 2005, Current pharmaceutical design.

Early-onset inflammatory bowel disease caused by mutations in the X-linked gene IL2RG.

Y. Nakazawa, K. Agematsu, T. Uehara, 2020, Journal of investigational allergology & clinical immunology.

B cell subpopulations separated by CD27 and crucial collaboration of CD27+ B cells and helper T cells in immunoglobulin production

C. Morimoto, A. Komiyama, K. Agematsu, 1997, European journal of immunology.

CD27: a memory B-cell marker.

A. Komiyama, K. Agematsu, H. Nagumo, 2000, Immunology today.

The different process of class switching and somatic hypermutation; a novel analysis by CD27(-) naive B cells.

A. Komiyama, K. Shinozaki, K. Agematsu, 2002, Blood.

Serial monitoring of Mucorales DNA load in serum samples of a patient with disseminated mucormycosis after allogeneic bone marrow transplantation

K. Koike, Y. Nakazawa, K. Matsuda, 2014, International Journal of Hematology.

Rapid Detection of Intracellular p47phox and p67phox by Flow Cytometry; Useful Screening Tests for Chronic Granulomatous Disease

O. Ohara, T. Morio, K. Agematsu, 2013, Journal of Clinical Immunology.

Remarkable effectiveness of tocilizumab in familial Mediterranean fever exon 3 variant with severe abdominal pain and PFAPA-like symptoms: a child case report and review of the literature

K. Agematsu, A. Kawakami, K. Fujimaki, 2019, Modern Rheumatology Case Reports.

[Familial Mediterranean fever as representative autoinflammatory disease].

M. Yazaki, K. Agematsu, J. Masumoto, 2009, Rinsho byori. The Japanese journal of clinical pathology.

The possession of exon 2 or exon 3 variants in the MEFV gene promotes inflammasome activation in Japanese patients with familial Mediterranean fever with a heterozygous exon 10 mutation.

K. Migita, K. Furukawa, K. Agematsu, 2020, Clinical and experimental rheumatology.

[AN ADULT CASE OF PERIODIC FEVER, APHTHOUS STOMATITIS, PHARYNGITIS, AND ADENITIS (PFAPA) SYNDROME DEVELOPED IN CHILDHOOD AND DIAGNOSED AFTER PROGRESS MORE THAN 30 YEARS].

K. Agematsu, Y. Takeuchi, Y. Okubo, 2020, Arerugi = [Allergy].

Early diagnosis of early-onset sarcoidosis: a case report with functional analysis and review of the literature

Keiko Kobayashi, K. Agematsu, J. Masumoto, 2017, Clinical Rheumatology.

Selective IgM deficiency accompanied with IgG4 deficiency, dermal complications and a bronchial polyp.

K. Kubo, K. Agematsu, M. Yasuo, 2008, Allergology international : official journal of the Japanese Society of Allergology.

Theophylline induces neutrophil apoptosis through adenosine A2A receptor antagonism

K. Shinozaki, K. Agematsu, H. Nagumo, 2000, Journal of leukocyte biology.

Markedly elevated CD64 expression on neutrophils and monocytes as a biomarker for diagnosis and therapy assessment in Kawasaki disease

Keiko Kobayashi, K. Agematsu, H. Nagumo, 2016, Inflammation Research.

DNA double strand break repair enzymes function at multiple steps in retroviral infection

Y. Sakurai, M. Matsuoka, K. Komatsu, 2018 .

B cell development and primary immunodeficiencies with hypogammaglobulinemia.

A. Komiyama, K. Agematsu, S. Hokibara, 2000, Archivum immunologiae et therapiae experimentalis.

Successful treatment for West syndrome with severe combined immunodeficiency

K. Koike, Y. Nakazawa, K. Agematsu, 2015, Brain and Development.

Effective combination therapy using interferon-gamma and interleukin-2 for disseminated Mycobacterium avium complex infection in a pediatric patient with AIDS.

K. Koike, K. Agematsu, T. Yamazaki, 2005, Clinical infectious diseases : an official publication of the Infectious Diseases Society of America.

Role of tonsillar IgD+CD27+ memory B cells in humoral immunity against pneumococcal infection.

K. Agematsu, K. Sugane, Masahiro Takizawa, 2006, Human immunology.

Adult onset X-linked chronic granulomatous disease in a woman patient caused by a de novo mutation in paternal-origin CYBB gene and skewed inactivation of normal maternal X chromosome.

S. Ikeda, M. Yazaki, K. Agematsu, 2008, Internal medicine.

Recombinant Human Granulocyte Colony-stimulating Factor Therapy for Sepsis in Infants With Neutropenia

A. Komiyama, K. Agematsu, K. Yasui, 1999, Pediatrics.

[Clinical observation of autoinflammatory diseases].

K. Agematsu, 2007, Nihon Rinsho Men'eki Gakkai kaishi = Japanese journal of clinical immunology.

Novel mutations in a Japanese patient with CD19 deficiency

H. Kanegane, T. Miyawaki, K. Agematsu, 2007, Genes and Immunity.

Direct cellular communications between CD45R0 and CD45RA T cell subsets via CD27/CD70.

C. Morimoto, T. Hirose, K. Agematsu, 1995, Journal of immunology.

Acute Myeloid Leukemia in a Patient With X-linked Severe Combined Immunodeficiency.

Y. Nakazawa, K. Matsuda, K. Agematsu, 2017, Journal of pediatric hematology/oncology.

X-Linked Agammaglobulinemia Diagnosed in Adulthood: A Case Report

H. Kanegane, T. Miyawaki, K. Agematsu, 2006, International journal of hematology.

Immune Complex-Mediated Glomerulonephritis in a Patient with Wiskott–Aldrich Syndrome

Y. Nakazawa, K. Agematsu, T. Shigemura, 2016, Journal of Clinical Immunology.

Mosaicism of an ELANE Mutation in an Asymptomatic Mother

O. Ohara, Y. Nakazawa, K. Agematsu, 2019, Journal of Clinical Immunology.

Later development of Fas ligand‐mediated cytotoxicity as compared with granule‐mediated cytotoxicity during the maturation of natural killer cells

K. Agematsu, A. Yabuhara, T. Nakazawa, 1997, Immunology.

Expansion of clonotype-restricted HLA-identical maternal CD4+ T cells in a patient with severe combined immunodeficiency and a homozygous mutation in the Artemis gene.

A. Komiyama, K. Agematsu, M. Ota, 2003, Clinical immunology.

Interleukin-21 stimulates B-cell immunoglobulin E synthesis in human beings concomitantly with activation-induced cytidine deaminase expression and differentiation into plasma cells.

H. Ochs, K. Agematsu, K. Sugane, 2009, Human immunology.

Nod2-Nodosome in a Cell-Free System: Implications in Pathogenesis and Drug Discovery for Blau Syndrome and Early-Onset Sarcoidosis

K. Migita, T. Heike, T. Sawasaki, 2016, TheScientificWorldJournal.

Interleukin-1beta suppression in Blau syndrome: comment on the article by Martin et al.

K. Agematsu, J. Masumoto, J. Nakayama, 2009, Arthritis and rheumatism.

Cytomegalovirus Encephalitis in a Patient with Severe Combined Immunodeficiency

K. Koike, Y. Nakazawa, K. Agematsu, 2015, Journal of Clinical Immunology.

KN3014, a piperidine-containing small compound, inhibits auto-secretion of IL-1β from PBMCs in a patient with Muckle–Wells syndrome

K. Yoshiura, K. Migita, T. Urano, 2020, Scientific Reports.

Monitoring serum IL-18 levels is useful for treatment of a patient with systemic juvenile idiopathic arthritis complicated by macrophage activation syndrome

H. Ochs, K. Koike, K. Agematsu, 2011, Pediatric rheumatology online journal.