B. Brown

发表

Studies of lysosomal alpha-glucosidase. II. Kinetics of action of the rat liver enzyme.

D. H. Brown, P. Jeffrey, B. Brown, 1970, Biochemistry.

Juvenile polysaccharidosis with cardioskeletal myopathy.

B. McManus, V. Ferrans, C. Gumbiner, 1987, Archives of pathology & laboratory medicine.

The experimental production of glycogen storage in cultured human fibroblasts.

D. H. Brown, B. Brown, 1972, Biochemical and biophysical research communications.

Hepatic fructose-1,6-diphosphatase deficiency. A cause of lactic acidosis and hypoglycemia in infancy.

D. Kipnis, I. Karl, A. Pagliara, 1972, Journal of Clinical Investigation.

Portal Diversion for the Treatment of Glycogen Storage Disease in Humans

T. Starzl, B. Brown, K. Porter, 1973, Annals of surgery.

Peripheral nerve in type III glycogenosis: Selective involvement of unmyelinated fiber schwann cells

W. Nyhan, H. Powell, B. Brown, 1985, Muscle & nerve.

STUDIES ON THE STRUCTURE AND MECHANISM OF ACTION OF THE GLYCOGEN DEBRANCHING ENZYMES OF MUSCLE AND LIVER *

R. Gordon, B. Brown, David H. Brown, 1973 .

Glycogen-Storage Diseases: Types I, III, IV, V, VII and Unclassified Glycogenoses

B. Brown, David H. Brown, 1968 .

The molecular heterogeneity of purified human liver lysosomal α-Glucosidase (acid α-Glucosidase)

B. Brown, David H. Brown, A. Murray, 1978 .

Preparation and properties of the glycogen-debranching enzyme from rabbit liver.

D. H. Brown, R. Gordon, B. Brown, 1972, Biochimica et biophysica acta.

Liver transplantation for type IV glycogen storage disease.

T. Starzl, A. Tzakis, B. Brown, 1991, The New England journal of medicine.

The apparent activity in vivo of the lysosomal pathway of glycogen catabolism in cultured human skin fibroblasts from patients with type III glycogen storage disease.

D. H. Brown, B. Brown, L. M. Waindle, 1978, The Journal of biological chemistry.

Administration of a mixture of fungal glucosidases to a patient with type II glycogenosis (Pompe's disease).

R. Lauer, B. Brown, A. Diehl, 1968, Pediatrics.

Clinical and laboratory observations in a child with hepatic phosphorylase kinase deficiency.

M. Tuchman, B. Burke, R. Ulstrom, 1986, Metabolism: Clinical and Experimental.

Studies of the residual glycogen branching enzyme activity present in human skin fibroblasts from patients with type IV glycogen storage disease.

D. H. Brown, B. Brown, 1983, Biochemical and biophysical research communications.

Liver transplantation for type I and type IV glycogen storage disease

T. Starzl, S. Todo, T. Starzl, 2005, European Journal of Pediatrics.

Glycogen storage disease type IB.

B. Brown, J. J. Buchino, D. M. Volk, 1983, Archives of pathology & laboratory medicine.

Hepatorenal glycogenosis (type I glycogenosis) and carcinoma of the liver.

B. Brown, F. Zangeneh, V. Kelley, 1969, The Journal of pediatrics.

The effect of partial portacaval transposition on the canine liver.

T. Starzl, B. Brown, J. Otte, 1967, Surgery.

Studies of lysosomal alpha-glucosidase. I. Purification and properties of the rat liver enzyme.

D. H. Brown, P. Jeffrey, B. Brown, 1970, Biochemistry.

Hypoglycemia, Hepatic Dysfunction, Muscle Weakness, Cardiomyopathy, Free Carnitine Deficiency and Long-Chain Acylcarnitine Excess Responsive to Medium Chain Triglyceride Diet

L. W. Perry, Andrew G Engel, A. Engel, 1983, Pediatric Research.

Glycogen-Storage Diseases**This review is dedicated to Carl F. Cori on the occasion of his seventieth birthday.: Types I, III, IV, V, VII and Unclassified Glycogenoses

B. Brown, David H. Brown, 1968 .

Action of a muscle branching enzyme on polysaccharides enlarged from UDP[14C]glucose

B. Brown, David H. Brown, 1966 .

[67] α-1,4-glucan: α-1,4-glucan 6-glycosyltransferase from mammalian muscle

B. Brown, David H. Brown, 1966 .

Effect of changes in the outer structure of glycogen on the debranching activity of the transferase-glucosidase system.

D. H. Brown, C. Cori, B. Brown, 1966, Archives of biochemistry and biophysics.

STUDIES ON THE LYSOSOMAL DEGRADATION OF GLYCOGEN IN CULTURED HUMAN SKIN FIBROBLASTS1

B. Brown, David H. Brown, L. M. Waindle, 1980 .

The subcellular distribution of enzymes in type II glycogenosis and the occurrence of an oligo-alpha-1,4-glucan glucohydrolase in human tissues.

D. H. Brown, B. Brown, 1965, Biochimica et biophysica acta.

Glycogen Storage Disease in Adults

C. Alter, J. Wolfsdorf, J. Keating, 1994, Annals of Internal Medicine.

Neutropenia in a patient with type IB glycogen storage disease: in vitro response to lithium chloride.

E. McCabe, R. Montgomery, D. O'brien, 1980, The Journal of pediatrics.

Portal diversion in glycogen storage disease.

T. Starzl, B. Brown, L. Brettschneider, 1969, Surgery.

A mild form of muscular glycogenosis in two brothers with alpha-1, 4-glucosidase deficiency.

B. Brown, W. Mccormick, H. Zellweger, 1965, Annales paediatrici. International review of pediatrics.

Simultaneous absence of alpha-1,4-glucosidase and alpha-1,6-glucosidase activities (pH 4) in tissues of children with type II glycogen storage disease.

D. H. Brown, P. Jeffrey, B. Brown, 1970, Biochemistry.

Pompe's Disease: Detection of Heterozygotes by Lymphocyte Stimulation

K. Hirschhorn, B. Brown, R. Hirschhorn, 1969, Science.

Lack of an alpha-1,4-glucan: alpha-1,4-glucan 6-glycosyl transferase in a case of type IV glycogenosis.

D. H. Brown, B. Brown, 1966, Proceedings of the National Academy of Sciences of the United States of America.

Hypoglycemia in type IV glycogenosis: hepatic improvement in two patients with nutritional management.

H. Greene, F. Ghishan, D. Freese, 1988, The Journal of pediatrics.

Clinical and laboratory findings in four patients with the non-progressive hepatic form of type IV glycogen storage disease

D. Piccoli, P. Kishnani, B. Brown, 1996, Journal of Inherited Metabolic Disease.

A new variant of type IV glycogenosis: Deficiency of branching enzyme activity without apparent progressive liver disease

B. Brown, Suzanne R. Taylor, R. M. Agostini, 1988, Hepatology.

Glycogen debranching enzyme: purification, antibody characterization, and immunoblot analyses of type III glycogen storage disease.

B. Brown, Y. T. Chen, J. Ding, 1987, American journal of human genetics.

Lipid storage myopathy in infantile Pompe's disease.

B. Brown, H. Sarnat, J. Carroll, 1982, Archives of neurology.

Metabolic and biochemical studies in fructose 1,6-diphosphatase deficiency.

B. Brown, A. Khachadurian, S. Melançon, 1973, The Journal of pediatrics.

Immunoblot analyses of glycogen debranching enzyme in different subtypes of glycogen storage disease type III.

R. Coleman, Yuan-Tsong Chen, T. de Barsy, 1990, The Journal of pediatrics.

Structure of the polysaccharide formed by incubating glycogen with D-[14C]glucose in the presence of the glycogen debranching enzyme [amylo-(1 linked to 6)-glucosidase-4-alpha-glucanotransferase].

D. H. Brown, B. Brown, D. J. Sprinkle, 1978, Carbohydrate research.

[88] Enzymes of glycogen debranching: Amylo-1,6-glucosidase (I) and oligo-1,4→1,4-glucantransferase (II)

B. Brown, David H. Brown, 1966 .

Alpha-1,4-glucosidase activity in leucocytes from the family of two brothers who lack this enzyme in muscle.

B. Brown, H. Zellweger, 1966, The Biochemical journal.

The Lysosomal α-Glucosidases of Mammalian Tissues

B. Brown, David H. Brown, A. Murray, 1975 .

X-linked glycogen storage disease. A cause of hypotonia, hyperuricemia, and growth retardation.

S. Dimauro, J. Keating, B. Brown, 1985, American journal of diseases of children.

Structure of the polysaccharide formed incubating glycogen with d-[14C]glucose in the presence of the glycogen debranching enzyme [amylo-(1 → 6)-glucosidase-4-α-glucanotransferase]

B. Brown, David H. Brown, D. J. Sprinkle, 1978 .

Type IV glycogen storage disease: branching enzyme deficiency in skin fibroblasts and possible heterozygote detection.

R. Howell, B. Brown, M. Kaback, 1971, The Journal of pediatrics.

LACK OF AN a-1 ,4-GLUCAN: a-i ,4-GLUCAN 6-GLYCOSYL TRANSFERASE IN A CASE OF TYPE IV GLYCOGENOSIS*

B. Brown, David H. Brown, 2022 .