S. Carr

发表

The evolution of airway function in early childhood following clinical diagnosis of cystic fibrosis.

A. Wade, J. Stocks, A. Hoo, 2004, American journal of respiratory and critical care medicine.

Scoliosis convexity and organ anatomy are related

S. Padley, R. Castelein, C. Hogg, 2017, European Spine Journal.

Asthma unresponsive to simple treatment in a child

S. Carr, J. Fitzsimons, Niamh O’Carroll, 2008, BMJ : British Medical Journal.

Clinical utility of NGS diagnosis and disease stratification in a multiethnic primary ciliary dyskinesia cohort

T. Cullup, L. Jenkins, H. Mitchison, 2019, Journal of Medical Genetics.

Projecting the impact of triple CFTR modulator therapy on intravenous antibiotic requirements in cystic fibrosis using patient registry data combined with treatment effects from randomised trials

N. Jewell, A. Lewin, E. Andrinopoulou, 2021, Thorax.

Seasonal fluctuation of lung function in cystic fibrosis: A national register-based study in two northern European populations

P. Diggle, D. Taylor-Robinson, S. Carr, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Registries and collaborative studies for primary ciliary dyskinesia in Europe

H. Omran, P. Yiallouros, P. Pennekamp, 2020, ERJ Open Research.

Time trends in diagnostic testing for primary ciliary dyskinesia in Europe

P. Yiallouros, M. Boon, A. Barbato, 2019, European Respiratory Journal.

Are inhaled corticosteroids prescribed rationally in primary ciliary dyskinesia?

A. Bush, C. Hogg, S. Carr, 2018, European Respiratory Journal.

Clinical phenotype and current diagnostic criteria for primary ciliary dyskinesia

A. Bush, C. Hogg, S. Carr, 2016, Expert review of respiratory medicine.

Data Resource Profile: The UK Cystic Fibrosis Registry

S. Stanojevic, R. Keogh, D. Taylor-Robinson, 2017, International journal of epidemiology.

Mutations in Outer Dynein Arm Heavy Chain DNAH9 Cause Motile Cilia Defects and Situs Inversus.

A. Nicholson, A. Tassin, S. Amselem, 2018, American journal of human genetics.

Incidence of SARS-CoV-2 in people with cystic fibrosis in Europe between February and June 2020

M. Mei-Zahav, P. Yiallouros, P. Burgel, 2021, Journal of Cystic Fibrosis.

Identifying exceptional cystic fibrosis care services: combining statistical process control with focus groups

P. Cullinan, J. Boote, D. Bilton, 2019, Health Services and Delivery Research.

Impact of cystic fibrosis on birthweight: a population based study of children in Denmark and Wales

P. Diggle, D. Taylor-Robinson, A. Nybo Andersen, 2018, Thorax.

Health economic modelling in Cystic Fibrosis: A systematic review.

J. Whitty, Arjun Bhadhuri, D. Bilton, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Incidence and risk factors of cancer in individuals with cystic fibrosis in the UK; a case-control study.

P. Cullinan, D. Bilton, E. Mentzakis, 2021, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

A comparison of the prevalence of urinary incontinence in girls with cystic fibrosis, asthma, and healthy controls

S. Carr, I. Balfour-Lynn, S. Prasad, 2006, Pediatric pulmonology.

Changing epidemiology of the respiratory bacteriology of patients with cystic fibrosis-data from the European cystic fibrosis society patient registry.

M. Mei-Zahav, M. Macek, P. Dřevínek, 2020, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Why do children have chronic abdominal pain, and what happens to them when they grow up? Population based cohort study

M. Hotopf, S. Wessely, M. Wadsworth, 1998, BMJ.

The disease-specific clinical trial network for primary ciliary dyskinesia: PCD-CTN

M. Armengot, H. Omran, P. Yiallouros, 2022, ERJ Open Research.

Learning to breathe with Tai Chi online - qualitative data from a randomized controlled feasibility study of patients with cystic fibrosis

N. Robinson, A. Lorenc, P. Ronan, 2020, European Journal of Integrative Medicine.

Exploring the nature of perceived treatment burden: a study to compare treatment burden measures in adults with cystic fibrosis

J. Whitty, J. Abbott, N. Simmonds, 2022, NIHR open research.

Bronchoconstriction following nebulised colistin in cystic fibrosis

S. Cunningham, S. Carr, C. Wallis, 2001, Archives of disease in childhood.

Proceedings of the 4th BEAT-PCD Conference and 5th PCD Training School

C. Kuehni, H. Mitchison, A. Shoemark, 2020, BMC Proceedings.

Relative ability of full and partial forced expiratory maneuvers to identify diminished airway function in infants with cystic fibrosis.

A. Wade, J. Stocks, A. Hoo, 2002, American journal of respiratory and critical care medicine.

Trajectories of early growth and subsequent lung function in cystic fibrosis: An observational study using UK and Canadian registry data.

S. Stanojevic, R. Keogh, D. Bilton, 2022, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Pregnancy rates and outcomes in women with cystic fibrosis in the UK: comparisons with the general population before and after the introduction of disease‐modifying treatment, 2003–17

D. Taylor-Robinson, Denitza Williams, J. Duckers, 2021, BJOG : an international journal of obstetrics and gynaecology.

Lung function in children with cystic fibrosis in the USA and UK: a comparative longitudinal analysis of national registry data

C. Goss, R. Szczesniak, R. Keogh, 2021, Thorax.

An observational study of the lung clearance index throughout childhood in cystic fibrosis: early years matter

S. Stanojevic, A. Wade, J. Stocks, 2020, European Respiratory Journal.

Primary Ciliary Dyskinesia Due to Microtubular Defects is Associated with Worse Lung Clearance Index

A. Bush, H. Mitchison, A. Shoemark, 2018, Lung.

Early detection of cystic fibrosis lung disease: multiple-breath washout versus raised volume tests

A. Wade, J. Stocks, G. Hülskamp, 2007, Thorax.

Heliox Therapy in Bronchiolitis: Phase III Multicenter Double-Blind Randomized Controlled Trial

J. Eliahoo, S. Carr, P. Habibi, 2013, Pediatrics.

Clinical characteristics of SARS-CoV-2 infection in children with cystic fibrosis: An international observational study

C. Goss, P. Burgel, M. Salvatore, 2020, Journal of Cystic Fibrosis.

Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

H. Mussaffi, P. Yiallouros, M. Boon, 2019, ERJ Open Research.

Childhood bronchiectasis, so little is known

S. Carr, Stefan A Unger, S. A. Unger, 2022, Archives of Disease in Childhood.

Factors associated with clinical progression to severe COVID-19 in people with cystic fibrosis: A global observational study

C. Goss, H. Rodgers, P. Burgel, 2022, Journal of Cystic Fibrosis.

Use of a rare disease patient registry in long-term post-authorisation drug studies: a model for collaboration with industry.

N. Caine, D. Bilton, S. Cunningham, 2018, The Lancet. Respiratory medicine.

Cystic fibrosis—Children and adults Tai Chi study (CF CATS2): Can Tai Chi improve symptoms and quality of life for people with cystic fibrosis? Second phase study protocol

N. Robinson, A. Lorenc, P. Ronan, 2015, Chinese journal of integrative medicine.

Quantifying fluctuation in glucose levels to identify early changes in glucose homeostasis in cystic fibrosis.

R. Brugha, S. Carr, M. Wright, 2018, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Pulmonary function deficits in newborn screened infants with cystic fibrosis managed with standard UK care are mild and transient

A. Wade, J. Stocks, A. Hoo, 2017, European Respiratory Journal.

Clinical characteristics of Pseudomonas and Aspergillus co-infected cystic fibrosis patients: A UK registry study.

J. Davies, D. Armstrong-James, S. Carr, 2021, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Lung Clearance Index (LCI) is Stable in Most Primary Ciliary Dyskinesia (PCD) Patients Managed in a Specialist Centre: a Pilot Study

A. Bush, A. Shoemark, C. Hogg, 2017, Lung.

An Update on CFTR Modulators as New Therapies for Cystic Fibrosis

J. Davies, S. Carr, A. Nichols, 2022, Pediatric Drugs.

Impact of cystic fibrosis on birthweight

P. Diggle, D. Taylor-Robinson, S. Paranjothy, 2018 .

The Impact on Parents of Diagnosing PCD in Young Children

M. Leigh, S. Dell, S. Carr, 2022, Journal of clinical medicine.

The global impact of SARS-CoV-2 in 181 people with cystic fibrosis

C. Goss, H. Rodgers, P. Burgel, 2020, Journal of Cystic Fibrosis.

An evaluation of two aerosol delivery systems for rhDNase.

D. Geddes, P. Shah, M. Hodson, 1997, The European respiratory journal.

University of Dundee Mutations in Outer Dynein Arm Heavy Chain DNAH9 Cause Motile Cilia Defects and Situs Inversus Fassad,

A. Tassin, S. Amselem, T. Cullup, 2018 .

Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis.

S. Stanojevic, A. Wade, J. Stocks, 2008, American journal of respiratory and critical care medicine.

Paranasal sinus pathogens in children with cystic fibrosis: do they relate to lower respiratory tract pathogens and is eradication successful?

S. Carr, C. Pao, C. Lambert, 2013, Journal of Cystic Fibrosis.

Randomised controlled trial of nasal continuous positive airways pressure (CPAP) in bronchiolitis

S. Carr, S. Mckenzie, C. Minasian, 2007, Archives of Disease in Childhood.

A multinational report to characterise SARS-CoV-2 infection in people with cystic fibrosis

C. Goss, H. Rodgers, P. Burgel, 2020, Journal of Cystic Fibrosis.

Treatment Preference Among People With Cystic Fibrosis

J. Whitty, J. Abbott, N. Simmonds, 2022, Chest.

Combination antifungal therapy for Scedosporium species in cystic fibrosis

J. Davies, S. Carr, I. Balfour-Lynn, 2020, Pediatric pulmonology.

Diagnosis of cystic fibrosis in London and South East England before and after the introduction of newborn screening

P. Seddon, J. Price, R. Chavasse, 2013, Archives of Disease in Childhood.

Minimal change in structural, functional and inflammatory markers of lung disease in newborn screened infants with cystic fibrosis at one year.

A. Wade, J. Stocks, A. Hoo, 2020, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

De Novo Mutations in FOXJ1 Result in a Motile Ciliopathy with Hydrocephalus and Randomization of Left/Right Body Asymmetry.

H. Omran, A. Brentrup, S. Dutcher, 2019, American journal of human genetics.

Future therapies for cystic fibrosis

J. Davies, K. Southern, A. Smyth, 2023, Nature Communications.

Communicating cystic fibrosis newborn screening results to parents

S. Carr, I. Balfour-Lynn, L. Seddon, 2020, European Journal of Pediatrics.

Topological data analysis reveals genotype–phenotype relationships in primary ciliary dyskinesia

G. Carlsson, J. Brandsma, N. S. Thomas, 2021, European Respiratory Journal.

Non-cystic fibrosis bronchiectasis: its diagnosis and management

S. Carr, P. Stafler, 2010, Archives of Disease in Childhood: Education & Practice Edition.

Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF

S. Stanojevic, A. Wade, J. Stocks, 2011, Thorax.

Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis.

S. Stanojevic, A. Wade, J. Stocks, 2011, American journal of respiratory and critical care medicine.

Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis.

Janet Stocks, Colin Wallis, Paul Aurora, 2005, American journal of respiratory and critical care medicine.

Factors for severe outcomes following SARS-CoV-2 infection in people with cystic fibrosis in Europe

M. Mei-Zahav, P. Yiallouros, P. Dřevínek, 2021, ERJ Open Research.

Hypersensitivity reactions to intravenous antibiotics in cystic fibrosis.

A. Bush, S. Carr, M. Wright, 2018, Paediatric respiratory reviews.

Clinical features and management of children with primary ciliary dyskinesia in England

Sunayna Best, A. Shoemark, C. Hogg, 2020, Archives of Disease in Childhood.

Children and Adults Tai Chi Study (CF-CATS2): a randomised controlled feasibility study comparing internet-delivered with face-to-face Tai Chi lessons in cystic fibrosis

N. Robinson, A. Lorenc, P. Ronan, 2018, ERJ Open Research.

CF-CATS: An uncontrolled feasibility study of using tai chi for adults with cystic fibrosis

N. Robinson, A. Lorenc, S. Carr, 2013 .

Recovery of baseline lung function after pulmonary exacerbation in children with primary ciliary dyskinesia

A. Bush, C. Hogg, S. Carr, 2016, Pediatric pulmonology.

Health State Utility Data in Cystic Fibrosis: A Systematic Review

J. Whitty, Arjun Bhadhuri, D. Bilton, 2019, PharmacoEconomics - Open.

The prevalence, clinical status and genotype of cystic fibrosis patients living in Cuba using national registry data.

A. Fogarty, A. Smyth, R. Suárez-Medina, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

High prevalence of CCDC103 p.His154Pro mutation causing primary ciliary dyskinesia disrupts protein oligomerisation and is associated with normal diagnostic investigations

M. Schmidts, R. Patel-King, A. Bush, 2017, Thorax.

Survival estimates in European cystic fibrosis patients and the impact of socioeconomic factors: a retrospective registry cohort study

R. Keogh, M. Macek, C. Ariti, 2021, European Respiratory Journal.

Eradication success for non-tuberculous mycobacteria in children with cystic fibrosis

S. Carr, Idan Bokobza, Dominic A. Hughes, 2021, European Respiratory Journal.

The impact of switching to the new global lung function initiative equations on spirometry results in the UK CF registry.

S. Stanojevic, J. Stocks, M. Rosenfeld, 2013, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening

A. Wade, J. Stocks, K. Costeloe, 2012, Thorax.

Non-invasive ventilation and clinical outcomes in cystic fibrosis: Findings from the UK CF registry.

P. Cullinan, W. Banya, D. Bilton, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

COVID-19 vaccine prioritisation for people with cystic fibrosis

C. Goss, P. Burgel, M. Salvatore, 2021, Journal of Cystic Fibrosis.

Investigating the effects of long-term dornase alfa use on lung function using registry data.

R. Keogh, S. Newsome, D. Bilton, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Restoration of exocrine pancreatic function in older children with cystic fibrosis on ivacaftor.

J. Davies, S. Carr, D. Jones, 2020, Paediatric respiratory reviews.

Response.

J. Whitty, S. Jacobson, N. Simmonds, 2018, Chest.

Treatment Preference Among People With Cystic Fibrosis

J. Whitty, J. Abbott, N. Simmonds, 2022, Chest.

Growth and nutritional status, and their association with lung function: a study from the international Primary Ciliary Dyskinesia Cohort

P. Yiallouros, A. Clément, I. Amirav, 2017, European Respiratory Journal.

Growth and lung function in Asian patients with cystic fibrosis

A. Hoo, R. Dinwiddie, S. Carr, 2005, Archives of Disease in Childhood.

cystic fibrosis Growth and lung function in Asian patients with

A. Hoo, R. Dinwiddie, S. Carr, 2009 .

Using Negative Control Outcomes and Difference-in-Differences Analysis to Estimate Treatment Effects in an Entirely Treated Cohort: The Effect of Ivacaftor in Cystic Fibrosis

R. Keogh, S. Newsome, D. Bilton, 2021, American journal of epidemiology.

Optimising equity of access: how should we allocate slots to the most competitive trials in Cystic Fibrosis (CF)?

J. Davies, N. Simmonds, S. Carr, 2021, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis.

S. Stanojevic, A. Wade, J. Stocks, 2008, American journal of respiratory and critical care medicine.

Early detection of cystic fibrosis lung disease: multiple-breath washout versus raised volume tests

A. Wade, J. Stocks, G. Hülskamp, 2007, Thorax.

Airway function in infants newly diagnosed with cystic fibrosis

A. Wade, J. Stocks, A. Bush, 2001, The Lancet.

Exploring the nature of perceived treatment burden: a study to compare treatment burden measures in adults with cystic fibrosis [version 1; peer review: awaiting peer review]

S. Carr, R. Cosgriff, R. Cameron, 2022 .

Non-invasive ventilation and clinical outcomes in cystic fibrosis: Findings from the UK CF registry.

P. Cullinan, W. Banya, D. Bilton, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Investigating the effects of long-term dornase alfa use on lung function using registry data.

S. Carr, Rhian Daniel, Simon Newsome, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Recovery of baseline lung function after pulmonary exacerbation in children with primary ciliary dyskinesia

A. Bush, C. Hogg, S. Carr, 2016, Pediatric pulmonology.

OP45 Pregnancy and perinatal outcomes for women with cystic fibrosis: a UK population-based registry study, 2003–2017

D. Taylor-Robinson, Denitza Williams, J. Duckers, 2021, SSM Annual Scientific Meeting.

A grumbling concern: an international survey of gastrointestinal symptoms in cystic fibrosis in the modulator era

A. Smyth, S. Carr, H. Barr, 2023, NIHR open research.