M. D'Aurelio

发表

Respiratory chain supercomplexes set the threshold for respiration defects in human mtDNA mutant cybrids.

G. Lenaz, G. Manfredi, M. D'Aurelio, 2006, Human molecular genetics.

Bioenergetics of mitochondrial diseases associated with mtDNA mutations.

V. Carelli, A. Baracca, G. Sgarbi, 2004, Biochimica et biophysica acta.

Ubiquinol and a Coenzyme Q Reducing System Protect Platelet Mitochondrial Function of Transfusional Buffy Coats from Oxidative Stress

P. Tazzari, R. Conte, A. Biondi, 2002, Free radical research.

Enhanced activity of the plasma membrane oxidoreductase in circulating lymphocytes from insulin-dependent diabetes mellitus patients.

G. Sgarbi, G. Lenaz, U. Paolucci, 2002, Biochemical and biophysical research communications.

BCL-2 Improves Oxidative Phosphorylation and Modulates Adenine Nucleotide Translocation in Mitochondria of Cells Harboring Mutant mtDNA*

J. Oca-Cossio, M. Woischnik, C. Moraes, 2003, The Journal of Biological Chemistry.

Coenzyme Q deficiency in mitochondria: kinetic saturation versus physical saturation.

G. Formiggini, G. Lenaz, H. Rauchová, 1997, Molecular aspects of medicine.

Mitochondrial bioenergetics in aging.

M. L. Genova, G. Formiggini, G. Lenaz, 2000, Biochimica et biophysica acta.

Mutated Human SOD1 Causes Dysfunction of Oxidative Phosphorylation in Mitochondria of Transgenic Mice*

M. Beal, M. Kiaei, M. Mattiazzi, 2002, The Journal of Biological Chemistry.

Barth syndrome: cellular compensation of mitochondrial dysfunction and apoptosis inhibition due to changes in cardiolipin remodeling linked to tafazzin (TAZ) gene mutation.

R. Wanders, P. Petit, E. Gottlieb, 2013, Biochimica et biophysica acta.

Heterologous mitochondrial DNA recombination in human cells.

William M. Mauck, C. Moraes, G. Lenaz, 2004, Human molecular genetics.

Role of Mitochondria in Oxidative Stress and Aging

M. L. Genova, G. Formiggini, G. Lenaz, 2002, Annals of the New York Academy of Sciences.

Rewiring of Glutamine Metabolism Is a Bioenergetic Adaptation of Human Cells with Mitochondrial DNA Mutations.

M. Beal, V. Carelli, Yevgeniya I. Shurubor, 2018, Cell metabolism.

The glutamate/cystine xCT antiporter antagonizes glutamine metabolism and reduces nutrient flexibility

Prashant Mishra, Mohit M. Jain, V. Carelli, 2017, Nature Communications.

Mitochondrial activities of a cell line derived from thyroid Hürthle cell tumors.

G. Romeo, A. Biondi, A. Falasca, 2006, Thyroid : official journal of the American Thyroid Association.

Prohibitin Reduces Mitochondrial Free Radical Production and Protects Brain Cells from Different Injury Modalities

G. Wang, C. Iadecola, V. Pickel, 2012, The Journal of Neuroscience.

Distinct intracellular sAC-cAMP domains regulate ER Ca2+ signaling and OXPHOS function

L. Levin, J. Buck, A. Starkov, 2017, Journal of Cell Science.

An Assembled Complex IV Maintains the Stability and Activity of Complex I in Mammalian Mitochondria*

G. Manfredi, Yidong Bai, M. D'Aurelio, 2007, Journal of Biological Chemistry.

A role of mitochondrial complex II defects in genetic models of Huntington's disease expressing N-terminal fragments of mutant huntingtin

D. Houitte, M. Guillermier, F. Petit, 2013, Human molecular genetics.

Oxidative stress, antioxidant defences and aging

M. L. Genova, G. Formiggini, G. Lenaz, 1998, BioFactors.

Lymphocyte dysmetabolism: an immunocytochemical comparative approach in IDDM and control subjects.

S. Zucchini, G. Sgarbi, G. Lenaz, 2009, European journal of histochemistry : EJH.

Bioenergetic markers in skin fibroblasts of sporadic amyotrophic lateral sclerosis and progressive lateral sclerosis patients

C. Gennings, H. Mitsumoto, J. Hupf, 2014, Annals of neurology.

Mitochondrial DNA background modifies the bioenergetics of NARP/MILS ATP6 mutant cells.

G. Manfredi, C. Vives-Bauza, M. Davidson, 2010, Human molecular genetics.

Decreased Pasteur effect in platelets of aged individuals

H. Baum, G. Formiggini, G. Sgarbi, 2001, Mechanisms of Ageing and Development.

In Vivo Regulation of Oxidative Phosphorylation in Cells Harboring a Stop-codon Mutation in Mitochondrial DNA-encoded Cytochrome c Oxidase Subunit I*

M. Beal, A. Barrientos, G. Manfredi, 2001, The Journal of Biological Chemistry.

A coordinated multiorgan metabolic response contributes to human mitochondrial myopathy

S. Servidei, V. Carelli, M. Valentino, 2023, EMBO molecular medicine.

Determination of Coenzyme A and Acetyl-Coenzyme A in Biological Samples Using HPLC with UV Detection

M. Beal, Arthur J. L. Cooper, Yevgeniya I. Shurubor, 2017, Molecules.

High fat diet ameliorates mitochondrial cardiomyopathy in CHCHD10 mutant mice

Nicole M. Sayles, H. Kawamata, G. Manfredi, 2023, bioRxiv.