Silvia Smaldone

发表

Fibrillin‐1 Regulates Skeletal Stem Cell Differentiation by Modulating TGFβ Activity Within the Marrow Niche

G. Pascual, B. Wentworth, Seng H. Cheng, 2016, Journal of bone and mineral research : the official journal of the American Society for Bone and Mineral Research.

Differential effects of alendronate and losartan therapy on osteopenia and aortic aneurysm in mice with severe Marfan syndrome.

H. Dietz, D. Rifkin, L. Carta, 2010, Human molecular genetics.

Fibrillin-1 and -2 differentially modulate endogenous TGF-β and BMP bioavailability during bone formation

G. Karsenty, L. Sakai, P. Ducy, 2010, Journal of Cell Biology.

Fibrillin-Rich Microfibrils—Structural and Instructive Determinants of Mammalian Development and Physiology

L. Carta, F. Ramirez, Silvia Smaldone, 2008, Connective tissue research.

Fibrillin assemblies: extracellular determinants of tissue formation and fibrosis

F. Ramirez, J. Olivieri, Silvia Smaldone, 2010, Fibrogenesis & tissue repair.

Fibrillin microfibrils in bone physiology.

F. Ramirez, Silvia Smaldone, 2016, Matrix biology : journal of the International Society for Matrix Biology.

Dimorphic Effects of Transforming Growth Factor-&bgr; Signaling During Aortic Aneurysm Progression in Mice Suggest a Combinatorial Therapy for Marfan Syndrome

B. Wentworth, Seng H. Cheng, L. Carta, 2015, Arteriosclerosis, thrombosis, and vascular biology.

Abnormal Activation of BMP Signaling Causes Myopathy in Fbn2 Null Mice

D. Keene, N. Charbonneau, L. Sakai, 2015, PLoS genetics.

Generation of Fbn1 conditional null mice implicates the extracellular microfibrils in osteoprogenitor recruitment

F. Ramirez, J. Cook, Silvia Smaldone, 2012, Genesis.

Extracellular Microfibrils Control Osteoblast-supported Osteoclastogenesis by Restricting TGFβ Stimulation of RANKL Production*

F. Ramirez, Silvia Smaldone, H. Nistala, 2010, The Journal of Biological Chemistry.

Extracellular regulation of transforming growth factor β and bone morphogenetic protein signaling in bone

F. Ramirez, Silvia Smaldone, H. Nistala, 2010, Annals of the New York Academy of Sciences.

p38 MAPK Is an Early Determinant of Promiscuous Smad2/3 Signaling in the Aortas of Fibrillin-1 (Fbn1)-null Mice*

H. Dietz, D. Rifkin, L. Carta, 2009, Journal of Biological Chemistry.

Role of uL3 in Multidrug Resistance in p53-Mutated Lung Cancer Cells

A. Russo, G. Russo, R. Faraonio, 2017, International journal of molecular sciences.

The human homologue of the mouse Surf5 gene encodes multiple alternatively spliced transcripts.

A. Porcellini, G. Russo, C. Pietropaolo, 2002, Gene.

EHD2 shuttles to the nucleus and represses transcription.

M. Horowitz, Sigi Benjamin, F. Ramirez, 2012, The Biochemical journal.

Establishment of fibrillin-deficient osteoprogenitor cell lines identifies molecular abnormalities associated with extracellular matrix perturbation of osteogenic differentiation

L. Carta, F. Ramirez, Silvia Smaldone, 2011, Cell and Tissue Research.

Fibrillin-1 and -2 differentially modulate endogenous TGF-β and BMP bioavailability during bone formation

G. Karsenty, L. Sakai, P. Ducy, 2010, The Journal of cell biology.

Functional biology of the Steel syndrome founder allele and evidence for clan genomics derivation of COL27A1 pathogenic alleles worldwide

Johnathon R. Walls, Marc S. Williams, J. Lupski, 2020, European Journal of Human Genetics.

Fibrillin-1 microfibrils influence adult bone marrow hematopoiesis.

S. Ghaffari, F. Ramirez, C. Bigarella, 2016, Matrix biology : journal of the International Society for Matrix Biology.

Transcription Factor KLF7 Is Important for Neuronal Morphogenesis in Selected Regions of the Nervous System

C. Mason, L. Parada, A. Puche, 2005, Molecular and Cellular Biology.

Identification of MoKA, a Novel F-Box Protein That Modulates Krüppel-Like Transcription Factor 7 Activity

F. Ramirez, C. Dragomir, Silvia Smaldone, 2004, Molecular and Cellular Biology.

Identification of the Drosophila progenitor of mammalian Krüppel-like factors 6 and 7 and a determinant of fly development.

M. Bhat, M. Mlodzik, F. Ramirez, 2003, Gene.

An Unfortunate Change of Heart

Silvia Smaldone, Justin D. Chronister Do, Simon C. Mathews Ba, 2011 .

Ha-Ras stabilization mediates pro-fibrotic signals in dermal fibroblasts

A. Gabrielli, G. Gusella, G. Moroncini, 2011, Fibrogenesis & tissue repair.

Multiple pathways regulate intracellular shuttling of MoKA, a co-activator of transcription factor KLF7

F. Ramirez, Silvia Smaldone, 2006, Nucleic acids research.

Fibrillin-1 deficiency in the outer perichondrium causes longitudinal bone overgrowth in mice with Marfan syndrome.

D. Rifkin, J. Hansen, F. Ramirez, 2022, Human Molecular Genetics.

Differential effects of alendronate and losartan therapy on osteopenia and aortic aneurysm in mice with severe Marfan syndrome [Human Molecular Genetics (2010) 19,24, 4790-4798] DOI: 10.1093/hmg/ddq409

H. Dietz, D. Rifkin, L. Carta, 2014 .

TENDON-DEPENDENT CONTROL OF LONGITUDINAL BONE GROWTH

F. Ramirez, Silvia Smaldone, N. Andarawis-Puri, 2015 .