H. Meng

发表

Treatment with ActRIIB-mFc Produces Myofiber Growth and Improves Lifespan in the Acta1 H40Y Murine Model of Nemaline Myopathy.

R. Fitts, E. Hardeman, R. Hoffmann, 2016, The American journal of pathology.

Myostatin inhibition using mRK35 produces skeletal muscle growth and tubular aggregate formation in wild type and TgACTA1D286G nemaline myopathy mice

Zizhao Zhang, N. Laing, M. Lawlor, 2018, Human molecular genetics.

Tissue Triage and Freezing for Models of Skeletal Muscle Disease

R. Grange, L. Swanson, A. Beggs, 2014, Journal of visualized experiments : JoVE.

Quantitative immuno-electron microscopic analysis of depolarization-induced expression of PGC-1α in cultured rat visual cortical neurons

M. Wong-Riley, Huanling Liang, H. Meng, 2007, Brain Research.

Tetraspanin CD82 is necessary for muscle stem cell activation and supports dystrophic muscle function

J. Widrick, F. Villa, E. Gussoni, 2020, Skeletal muscle.

Myotubularin-deficient myoblasts display increased apoptosis, delayed proliferation, and poor cell engraftment.

Ping Huang, A. Beggs, L. Kunkel, 2012, The American journal of pathology.

Muscle‐directed gene therapy corrects Pompe disease and uncovers species‐specific GAA immunogenicity

F. Mavilio, M. Lawlor, Jianyong Huang, 2021, EMBO molecular medicine.

Skeletal Muscle Pathology in X-Linked Myotubular Myopathy: Review With Cross-Species Comparisons

J. Dowling, A. Beggs, B. Schoser, 2016, Journal of neuropathology and experimental neurology.

Intrahepatic Cholestasis Is a Clinically Significant Feature Associated with Natural History of X-Linked Myotubular Myopathy (XLMTM): A Case Series and Biopsy Report

B. Kamath, M. Lawlor, R. Graham, 2021, Journal of neuromuscular diseases.

Potentially diagnostic electron paramagnetic resonance spectra elucidate the underlying mechanism of mitochondrial dysfunction in the deoxyguanosine kinase deficient rat model of a genetic mitochondrial DNA depletion syndrome.

D. Dimmock, J. V. Van Hove, M. Lawlor, 2016, Free radical biology & medicine.

The nucleotide prodrug CERC‐913 improves mtDNA content in primary hepatocytes from DGUOK‐deficient rats

D. Dimmock, M. Lawlor, D. Helbling, 2020, Journal of inherited metabolic disease.

Long‐term effects of systemic gene therapy in a canine model of myotubular myopathy

R. Grange, A. Beggs, D. Mack, 2017, Muscle & nerve.

Myostatin Inhibition Using ActRIIB-mFc Does Not Produce Weight Gain or Strength in the Nebulin Conditional KO Mouse

H. Granzier, P. Simpson, M. Lawlor, 2018, Journal of neuropathology and experimental neurology.

Nebulin deficiency in adult muscle causes sarcomere defects and muscle-type-dependent changes in trophicity: novel insights in nemaline myopathy.

C. Ottenheijm, H. Granzier, Camille L. Birch, 2015, Human molecular genetics.

CD82 Is a Marker for Prospective Isolation of Human Muscle Satellite Cells and Is Linked to Muscular Dystrophies.

J. Spinazzola, A. Rozkalne, L. Kunkel, 2016, Cell stem cell.

Photobiomodulation partially rescues visual cortical neurons from cyanide-induced apoptosis

M. Wong-Riley, H. Whelan, J. Eells, 2006, Neuroscience.

Enzyme replacement therapy rescues weakness and improves muscle pathology in mice with X-linked myotubular myopathy.

R. Grange, A. Beggs, J. Widrick, 2013, Human molecular genetics.

Systemic AAV8-Mediated Gene Therapy Drives Whole-Body Correction of Myotubular Myopathy in Dogs.

R. Grange, A. Beggs, D. Mack, 2017, Molecular therapy : the journal of the American Society of Gene Therapy.

Assessment of systemic AAV-microdystrophin gene therapy in the GRMD model of Duchenne muscular dystrophy

T. Conlon, B. Byrne, M. Styner, 2023, Science Translational Medicine.

Differential muscle hypertrophy is associated with satellite cell numbers and Akt pathway activation following activin type IIB receptor inhibition in Mtm1 p.R69C mice.

Fujun Liu, Lin Yang, Alan H Beggs, 2014, The American journal of pathology.

Sdha+/- Rats Display Minimal Muscle Pathology Without Significant Behavioral or Biochemical Abnormalities

M. Dwinell, D. Dimmock, M. Lawlor, 2018, Journal of neuropathology and experimental neurology.

Aberrations in energetic metabolism and stress-related pathways contribute to pathophysiology in the Neb cKO mouse model of nemaline myopathy.

M. Lawlor, A. Geurts, H. Granzier, 2023, The American journal of pathology.

Use Of Ankle Immobilization In Evaluating Treatments To Promote Longitudinal Muscle Growth In Mice

D. Riley, James L. W. Bain, R. Pearsall, 2018, Muscle and Nerve.

P.9.10 Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy

C. Ottenheijm, A. Beggs, C. Poggesi, 2013, Neuromuscular Disorders.

Different mouse models of nemaline myopathy harboring Acta1 mutations display differing abnormalities related to mitochondrial biology.

E. Hardeman, M. Lawlor, A. Geurts, 2023, The American journal of pathology.

Aberrations in Energetic Metabolism and Stress-Related Pathways Contribute to Pathophysiology in the Neb Conditional Knockout Mouse Model of Nemaline Myopathy

M. Lawlor, D. Stowe, J. Heisner, 2023 .

CD82 Is a Marker for Prospective Isolation of Human Muscle Satellite Cells and Is Linked to Muscular Dystrophies.

J. Spinazzola, L. Kunkel, E. Gussoni, 2016, Cell stem cell.

Treatment with ActRIIB-mFc Produces Myofiber Growth and Improves Lifespan in the Acta1 H40Y Murine Model of Nemaline Myopathy.

R. Fitts, E. Hardeman, A. Beggs, 2016, American Journal of Pathology.