J. Blouin

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Combined Heterozygous Deficiency of the Classical Complement Pathway Proteins C2 and C4

M. Kazatchkine, V. Frémeaux-Bacchi, L. Weiss, 1997, Journal of Clinical Immunology.

Primary glomerulonephritis with isolated C3 deposits: a new entity which shares common genetic risk factors with haemolytic uraemic syndrome

R. Salomon, B. Knebelmann, J. Grünfeld, 2006, Journal of Medical Genetics.

Mutations in complement C3 predispose to development of atypical hemolytic uremic syndrome.

W. Fridman, N. Moghal, J. Atkinson, 2008, Blood.

Development of anti-factor H auto-antibodies genetically predisposed in atypical HUS

W. Fridman, B. Ranchin, M. Davidovits, 2007 .

Protective or aggressive: Paradoxical role of C3 in atypical hemolytic uremic syndrome

W. Fridman, V. Frémeaux-Bacchi, C. Régnier, 2007 .

hemolytic uremic syndrome Mutations in complement C3 predispose to development of atypical

W. Fridman, N. Moghal, J. Atkinson, 2013 .

Molecular Basis of a Selective C1s Deficiency Associated with Early Onset Multiple Autoimmune Diseases1

W. Fridman, A. Prieur, P. Quartier, 2001, The Journal of Immunology.

Autoantibodies to the collagen-like region of C1q are strongly associated with classical pathway-mediated hypocomplementemia in systemic lupus erythematosus

M. Kazatchkine, V. Frémeaux-Bacchi, L. Weiss, 1996, Lupus.

Factor H, membrane cofactor protein, and factor I mutations in patients with hemolysis, elevated liver enzymes, and low platelet count syndrome.

A. Benachi, B. Knebelmann, Y. Pirson, 2008, Blood.

Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome.

W. Fridman, A. Bagga, H. Cheong, 2010, Journal of the American Society of Nephrology : JASN.

Lack of evidence of a specific role for C4A gene deficiency in determining disease susceptibility among C4‐deficient patients with systemic lupus erythematosus (SLE)

M. Kazatchkine, P. Rémy, F. Ariey, 2001, Clinical and experimental immunology.

Prevalence of monoclonal gammopathy in patients presenting with acquired angioedema type 2.

J. Piette, W. Fridman, L. Mouthon, 2002, The American journal of medicine.

Effect of Wine Polysaccharides on the Nucleation of Potassium Hydrogen Tartrate in Model Solutions

V. Gerbaud, C. Laguerie, N. Gabas, 1996 .

Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome.

W. Fridman, H. Nivet, V. Frémeaux-Bacchi, 2005, Journal of the American Society of Nephrology : JASN.

Hereditary complement C7 deficiency in nine families: Subtotal C7 deficiency revisited

C. Sautès-Fridman, W. Fridman, F. Bienaimé, 2007, European journal of immunology.

[Exploration of the complement system in clinical practice].

V. Frémeaux-Bacchi, L. Weiss, J. Blouin, 1994, Archives de pédiatrie.

[Complement protein hereditary deficits during purulent meningitis: study of 61 adult Tunisian patients].

S. Makni, R. Abdelmalek, M. Kallel-Sellami, 2006, Archives de l'Institut Pasteur de Tunis.

[Neisseria meningitidis infection. Clinical criteria orienting towards a deficiency in the proteins of the complement].

W. Fridman, M. Rameix-Welti, V. Frémeaux-Bacchi, 2005, Presse medicale.

Infection par Neisseria meningitidis

M. Rameix-Welti, W. Fridman, J. Alonso, 2005 .

Complete inherited deficiency of the fourth complement component in a child with systemic lupus erythematosus and his disease-free brother in a North African family

M. Kazatchkine, V. Frémeaux-Bacchi, C. Loirat, 1994, Journal of Clinical Immunology.

Mutations in components of complement influence the outcome of Factor I-associated atypical hemolytic uremic syndrome.

C. Sautès-Fridman, A. Blom, B. Villoutreix, 2010, Kidney international.

The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome

C. Sautès-Fridman, W. Fridman, W. Fridman, 2009, Journal of Medical Genetics.

Genetic and functional analyses of membrane cofactor protein (CD46) mutations in atypical hemolytic uremic syndrome.

A. Caudy, W. Fridman, J. Atkinson, 2006, Journal of the American Society of Nephrology : JASN.

syndrome endothelial cells and contributes to atypical hemolytic uremic Hyperfunctional C3 convertase leads to complement deposition on

C. Sautès-Fridman, W. Fridman, J. Dimitrov, 2014 .

Functional Complement C1q Abnormality Leads to Impaired Immune Complexes and Apoptotic Cell Clearance

W. Fridman, D. Sène, V. Frémeaux-Bacchi, 2011, The Journal of Immunology.

Cell Clearance to Impaired Immune Complexes and Apoptotic Functional Complement C1q Abnormality Leads

L. Halbwachs‐Mecarelli, M. Radanova, J. Blouin, 2011 .

Apoptotic Cell Clearance Leads to Impaired Immune Complexes and Functional Complement C 1 q Abnormality

W. Fridman, D. Sène, V. Frémeaux-Bacchi, 2011 .

Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome.

C. Sautès-Fridman, W. Fridman, J. Dimitrov, 2009, Blood.

Hyperfunctional C 3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome

C. Sautès-Fridman, W. Fridman, J. Dimitrov, 2009 .

Complement factor I: a susceptibility gene for atypical haemolytic uraemic syndrome

W. Fridman, B. Boudailliez, D. Kuypers, 2004, Journal of Medical Genetics.

Genetic and Functional Analyses of Membrane Cofactor Protein ( CD 46 ) Mutations in Atypical Hemolytic Uremic Syndrome

A. Caudy, W. Fridman, J. Atkinson, 2006 .

Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases.

G. Deschênes, P. Niaudet, P. Coppo, 2004, Journal of the American Society of Nephrology : JASN.

Human complement factor H deficiency associated with hemolytic uremic syndrome.

M. Kazatchkine, G. Deschênes, V. Frémeaux-Bacchi, 1998, Journal of the American Society of Nephrology : JASN.

The Taste of Wine: The Art and Science of Wine Appreciation

Emile Peynaud, Jacques Blouin, J. Blouin, 1987 .

Study of the polyphenolic structure of red wines by physical-chemical and sensory analyses

J. Blouin, E. Stonestreet, N. Papet, 2000 .

Disseminated Tuberculosis in a Patient with Hereditary C1-inhibitor Deficiency

M. Barbouche, S. Makni, V. Frémeaux-Bacchi, 2008, Infection.

Study of wine tartaric acid salt stabilization by addition of carboxymethylcellulose (CMC): comparison with the "protective colloids" effect.

V. Gerbaud, N. Gabas, J. Blouin, 2010 .

Unusual clinical severity of complement membrane cofactor protein-associated hemolytic-uremic syndrome and uniparental isodisomy.

W. Fridman, M. Vekemans, S. Menouer, 2007, American journal of kidney diseases : the official journal of the National Kidney Foundation.

Pediatric Systemic Lupus Erythematosus with C1q Deficiency

S. Makni, V. Frémeaux-Bacchi, M. Abdelmoula, 2007, Annals of the New York Academy of Sciences.

Atypical hemolytic uremic syndrome and mutation analysis of factor H gene in two Tunisian families

Y. Gorgi, K. Ayed, V. Frémeaux-Bacchi, 2010, International journal of nephrology and renovascular disease.

Hereditary Complement Deficiency and Lupus

S. Makni, V. Frémeaux-Bacchi, R. Abdelmalek, 2007, Annals of the New York Academy of Sciences.

The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome

C. Sautès-Fridman, W. Fridman, V. Frémeaux-Bacchi, 2009, Journal of Medical Genetics.

Prognostic Significance of Complement System Activation After Allogeneic Hematopoietic Stem Cell Transplantation.

W. Fridman, P. Milpied, O. Hermine, 2009 .