N. Baatallah

发表

Pharmacological chaperone-rescued cystic fibrosis CFTR-F508del mutant overcomes PRAF2-gated access to endoplasmic reticulum exit sites

S. Marullo, H. Enslen, I. Sermet-Gaudelus, 2022, Cellular and Molecular Life Sciences.

Differential CFTR-Interactome Proximity Labeling Procedures Identify Enrichment in Multiple SLC Transporters

S. Marullo, I. Guerrera, I. Sermet-Gaudelus, 2022, International journal of molecular sciences.

Targeting different binding sites in the CFTR structures allows to synergistically potentiate channel activity.

J. Mornon, I. Callebaut, P. Lehn, 2020, European journal of medicinal chemistry.

Pharmacological chaperone-rescued cystic fibrosis CFTR-F508del mutant overcomes PRAF2-gated access to endoplasmic reticulum exit sites

S. Marullo, H. Enslen, I. Sermet-Gaudelus, 2022, Cellular and Molecular Life Sciences.

Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis

L. Touqui, J. Sallenave, X. Nassif, 2019, Scientific Reports.

Keratin 8 is a scaffolding and regulatory protein of ERAD complexes

J. Irving, D. Lomas, G. Lukács, 2022, Cellular and Molecular Life Sciences.

Acting on the CFTR Membrane-Spanning Domains Interface Rescues Some Misfolded Mutants

J. Mornon, I. Sermet-Gaudelus, I. Callebaut, 2022, International journal of molecular sciences.

Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR

J. Mornon, I. Sermet-Gaudelus, I. Callebaut, 2021, Cellular and Molecular Life Sciences.

Cis variants identified in F508del complex alleles modulate CFTR channel rescue by small molecules

J. Mornon, I. Sermet-Gaudelus, I. Callebaut, 2018, Human mutation.

Design of crotoxin-based peptides with potentiator activity targeting the ΔF508NBD1 Cystic Fibrosis Transmembrane Conductance Regulator.

P. Corringer, G. Lukács, P. Zielenkiewicz, 2022, Journal of molecular biology.

The Autophagy Inhibitor Spautin-1 Antagonizes Rescue of Mutant CFTR Through an Autophagy-Independent and USP13-Mediated Mechanism

D. di Bernardo, N. Pedemonte, L. Galietta, 2018, Front. Pharmacol..

Exon identity influences splicing induced by exonic variants and in silico prediction efficacy.

I. Sermet-Gaudelus, E. Girodon, J. Varilh, 2020, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR

J. Mornon, I. Sermet-Gaudelus, I. Callebaut, 2021, Cellular and Molecular Life Sciences.

Predictive factors for lumacaftor/ivacaftor clinical response.

I. Sermet-Gaudelus, E. Girodon, A. Edelman, 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

CFTR corrector efficacy is associated with occupancy of distinct binding sites

J. Mornon, I. Sermet-Gaudelus, I. Callebaut, 2021, bioRxiv.