Z. Bebok

发表

LPS decreases CFTR open probability and mucociliary transport through generation of reactive oxygen species

S. Matalon, Z. Bebők, S. Rowe, 2021, Redox biology.

The CFTR and ENaC debate: how important is ENaC in CF lung disease?

S. Matalon, Z. Bebők, A. Lazrak, 2012, American journal of physiology. Lung cellular and molecular physiology.

Endoplasmic reticulum stress and the unfolded protein response regulate genomic cystic fibrosis transmembrane conductance regulator expression.

J. Wakefield, Rafał Bartoszewski, Z. Bebők, 2007, American journal of physiology. Cell physiology.

conductance regulator expression response regulate genomic cystic fibrosis transmembrane Endoplasmic reticulum stress and the unfolded protein

J. Wakefield, Rafał Bartoszewski, Z. Bebők, 2013 .

Excellent In vivo Bystander Activity of Fludarabine Phosphate against Human Glioma Xenografts that Express the Escherichia coli Purine Nucleoside Phosphorylase Gene

Z. Bebők, D. Levasseur, Jeong S. Hong, 2004, Cancer Research.

Bystander killing of melanoma cells using the human tyrosinase promoter to express the Escherichia coli purine nucleoside phosphorylase gene.

Z. Bebők, V. Gadi, W. Parker, 1995, Cancer research.

The Unfolded Protein Response (UPR)-activated Transcription Factor X-box-binding Protein 1 (XBP1) Induces MicroRNA-346 Expression That Targets the Human Antigen Peptide Transporter 1 (TAP1) mRNA and Governs Immune Regulatory Genes*

Niren Kapoor, Rafał Bartoszewski, Z. Bebők, 2011, The Journal of Biological Chemistry.

Failure of cAMP agonists to activate rescued ΔF508 CFTR in CFBE41o– airway epithelial monolayers

J. Wakefield, J. Clancy, Z. Bebők, 2005, The Journal of physiology.

CFTR expression regulation by the unfolded protein response.

Rafał Bartoszewski, Z. Bebők, J. Collawn, 2011, Methods in enzymology.

Somatic mosaicism for copy number variation in differentiated human tissues

J. Komorowski, E. Partridge, A. Piotrowski, 2008, Human mutation.

Endoplasmic Reticulum Stress Response is Transmissible in vitro from Epithelial Cells to Fibroblasts via the Mediation of Unfolded Protein Response

Z. Bebők, Yiming Zhang, Z. Bebok, 2022 .

Regulation of angiogenesis by hypoxia: the role of microRNA

Niren Kapoor, Rafał Bartoszewski, Z. Bebők, 2012, Cellular & Molecular Biology Letters.

Decoding mechanisms by which silent codon changes influence protein biogenesis and function.

Z. Bebők, V. Bali, Vedrana Bali, 2015, The international journal of biochemistry & cell biology.

Prognostic relevance of transforming growth factor alpha (TGF-α) and tumor necrosis factor alpha (TNF-α) detected in breast cancer tissues by immunohistochemistry

Z. Bebők, P. Németh, B. Márkus, 2004, Breast Cancer Research and Treatment.

Gene delivery systems--gene therapy vectors for cystic fibrosis.

Z. Bebők, D. Schindelhauer, E. Schwiebert, 2004, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

A clinical inflammatory syndrome attributable to aerosolized lipid-DNA administration in cystic fibrosis.

J. Clancy, J. Morris, Z. Bebők, 2001, Human gene therapy.

Development of drug targeting based on recombinant expression of the chicken avidin gene.

Z. Bebők, M. Kulomaa, R. Reynolds, 1996, Journal of drug targeting.

Cigarette smoke and CFTR: implications in the pathogenesis of COPD.

S. Matalon, Z. Bebők, S. Rowe, 2013, American journal of physiology. Lung cellular and molecular physiology.

Cystin is required for maintaining fibrocystin (FPC) levels and safeguarding proteome integrity in mouse renal epithelial cells A mechanistic connection between the kidney defects in cpk mice and human ARPKD

Z. Bebők, Wei Wang, L. Guay-Woodford, 2023, bioRxiv.

A Synonymous Single Nucleotide Polymorphism in ΔF508 CFTR Alters the Secondary Structure of the mRNA and the Expression of the Mutant Protein*

J. Kappes, Rafał Bartoszewski, Z. Bebők, 2010, The Journal of Biological Chemistry.

Severe phenotype in mice with termination mutation in exon 2 of cystic fibrosis gene

A. Beaudet, A. Bradley, Z. Bebők, 1995, Somatic cell and molecular genetics.

Suppression of a CFTR premature stop mutation in a bronchial epithelial cell line

J. Clancy, D. Benos, Z. Bebők, 1997, Nature Medicine.

Suppression of CFTR premature termination codons and rescue of CFTR protein and function by the synthetic aminoglycoside NB54

Z. Bebők, D. Bedwell, E. Schwiebert, 2011, Journal of Molecular Medicine.

Gentamicin-induced correction of CFTR function in patients with cystic fibrosis and CFTR stop mutations.

B. Kerem, H. Blau, Z. Bebők, 2003, The New England journal of medicine.

Transient transfection of polarized epithelial monolayers with CFTR and reporter genes using efficacious lipids.

Z. Bebők, E. Schwiebert, N. McCarty, 2003, American journal of physiology. Cell physiology.

Targets for cystic fibrosis therapy: proteomic analysis and correction of mutant cystic fibrosis transmembrane conductance regulator

Z. Bebők, J. Collawn, Lianwu Fu, 2010, Expert review of proteomics.

Establishment and Characterization of a Novel Polarized MDCK Epithelial Cellular Model for CFTR Studies

J. Wakefield, Z. Bebők, M. Amaral, 2005, Cellular Physiology and Biochemistry.

Macula densa Na(+)/H(+) exchange activities mediated by apical NHE2 and basolateral NHE4 isoforms.

P. D. Bell, Z. Bebők, D. Warnock, 2000, American journal of physiology. Renal physiology.

miR-200b downregulates CFTR during hypoxia in human lung epithelial cells

M. Sanak, Rafał Bartoszewski, Z. Bebők, 2017, Cellular & Molecular Biology Letters.

ΔF508 CFTR Surface Stability Is Regulated by DAB2 and CHIP-Mediated Ubiquitination in Post-Endocytic Compartments

Rafał Bartoszewski, Z. Bebők, S. Rowe, 2015, PloS one.

Activation of the unfolded protein response by deltaF508 CFTR.

J. Wakefield, Rafał Bartoszewski, Z. Bebők, 2008, American journal of respiratory cell and molecular biology.

Assessment of CFTR localisation in native airway epithelial cells obtained by nasal brushing.

J. Clancy, Z. Bebők, M. Amaral, 2004, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

Mutations in the Amino Terminus of the Cystic Fibrosis Transmembrane Conductance Regulator Enhance Endocytosis*

J. Clancy, Z. Bebők, K. Kirk, 2006, Journal of Biological Chemistry.

No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.

R. Gibson, J. Clancy, Z. Bebők, 2007, American journal of respiratory cell and molecular biology.

Stressors and Stress Responses in Cystic Fibrosis

Z. Bebők, Lianwu Fu, Z. Bebok, 2018, Endoplasmic Reticulum Stress in Diseases.

The silent codon change I507‐ATC→ATT contributes to the severity of the ΔF508 CFTR channel dysfunction

Sadis Matalon, Rafal Bartoszewski, Andras Rab, 2013, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.

Gene therapy for cystic fibrosis using cationic liposome mediated gene transfer: a phase I trial of safety and efficacy in the nasal airway.

S. Matalon, Z. Bebők, R. Frizzell, 1994, Human gene therapy.

Limited ATF4 Expression in Degenerating Retinas with Ongoing ER Stress Promotes Photoreceptor Survival in a Mouse Model of Autosomal Dominant Retinitis Pigmentosa

Z. Bebők, M. Athar, S. Zolotukhin, 2016, PloS one.

Regulation of angiogenesis by hypoxia: the role of microRNA

Niren Kapoor, Rafał Bartoszewski, Z. Bebők, 2012, Cellular & Molecular Biology Letters.

Pkhd1cyli/cyli mice have altered renal Pkhd1 mRNA processing and hormonally sensitive liver disease

Surajit Bhattacharya, L. Guay-Woodford, L. Caldovic, 2023, Journal of Molecular Medicine.

with CFTR and reporter genes using efficacious lipids Transient transfection of polarized epithelial monolayers

E. Schwiebert, N. McCarty, L. Schwiebert, 2013 .

Tumor cell bystander killing in colonic carcinoma utilizing the Escherichia coli DeoD gene to generate toxic purines.

Z. Bebők, W. Parker, E. Sorscher, 1994, Gene therapy.

Interaction of ASIC1 and ENaC subunits in human glioma cells and rat astrocytes.

William M. Lee, D. Benos, Niren Kapoor, 2011, American journal of physiology. Cell physiology.

glioma cells and rat astrocytes Interaction of ASIC1 and ENaC subunits in human

William M. Lee, D. Benos, Rafał Bartoszewski, 2016 .

Restoration of W1282X CFTR activity by enhanced expression.

J. Clancy, Z. Bebők, S. Rowe, 2007, American journal of respiratory cell and molecular biology.

Extracellular Zinc and ATP Restore Chloride Secretion across Cystic Fibrosis Airway Epithelia by Triggering Calcium Entry*

J. Clancy, Z. Bebők, E. Schwiebert, 2004, Journal of Biological Chemistry.

Chapter 1 Structure and Functions of Biomembranes

Z. Bebők, J. Collawn, Z. Bebok, 2008 .

CFTR involvement in chloride, bicarbonate, and liquid secretion by airway submucosal glands.

E. Sorscher, L. Trout, A. Crews, 1999, American journal of physiology. Lung cellular and molecular physiology.

Cationic lipids for reporter gene and CFTR transfer to rat pulmonary epithelium.

Z. Bebők, G. Siegal, R. Frizzell, 1995, Gene therapy.

Influenza virus infection alters ion channel function of airway and alveolar cells: mechanisms and physiological sequelae.

S. Matalon, Z. Bebők, A. Lazrak, 2017, American journal of physiology. Lung cellular and molecular physiology.

Cigarette smoke and CFTR: implications in the pathogenesis of COPD.

S. Matalon, S. Rowe, J. Collawn, 2013, American journal of physiology. Lung cellular and molecular physiology.

VCP/p97 AAA-ATPase does not interact with the endogenous wild-type cystic fibrosis transmembrane conductance regulator.

Z. Bebők, J. Collawn, L. Wilson, 2007, American journal of respiratory cell and molecular biology.

Evidence that systemic gentamicin suppresses premature stop mutations in patients with cystic fibrosis.

J. Clancy, D. Bedwell, M. Macaluso, 2001, American journal of respiratory and critical care medicine.

Glioma-specific Cation Conductance Regulates Migration and Cell Cycle Progression*

D. Benos, Rafał Bartoszewski, A. Rooj, 2011, The Journal of Biological Chemistry.

Reactive Oxygen Nitrogen Species Decrease Cystic Fibrosis Transmembrane Conductance Regulator Expression and cAMP-mediated Cl− Secretion in Airway Epithelia*

S. Matalon, Z. Bebők, K. Hardiman, 2002, The Journal of Biological Chemistry.

Search and rescue: finding ways to correct deltaF508 CFTR.

Sadis Matalon, S. Matalon, Z. Bebők, 2009, American journal of respiratory cell and molecular biology.

Knockdown of ASIC1 and Epithelial Sodium Channel Subunits Inhibits Glioblastoma Whole Cell Current and Cell Migration*

D. Benos, Niren Kapoor, Y. Qadri, 2009, The Journal of Biological Chemistry.

Functional stability of rescued delta F508 cystic fibrosis transmembrane conductance regulator in airway epithelial cells.

S. Matalon, Rafał Bartoszewski, Z. Bebők, 2010, American journal of respiratory cell and molecular biology.

A synonymous codon change alters the drug sensitivity of ΔF508 cystic fibrosis transmembrane conductance regulator

S. Matalon, Z. Bebők, A. Lazrak, 2016, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.

Suppression of CFTR premature termination codons and rescue of CFTR protein and function by the synthetic aminoglycoside NB54

D. Bedwell, E. Schwiebert, S. Rowe, 2011, Journal of Molecular Medicine.

Niren Kapoor, Rafał Bartoszewski, D. Crossman, 2011 .

Dab2 is a key regulator of endocytosis and post-endocytic trafficking of the cystic fibrosis transmembrane conductance regulator.

Z. Bebők, S. Rowe, J. Collawn, 2012, The Biochemical journal.

Dab 2 is a key regulator of endocytosis and post-endocytic trafficking of the cystic fibrosis transmembrane conductance regulator

Z. Bebők, S. Rowe, J. Collawn, 2011 .

Mechanistic Approaches to Improve Correction of the Most Common Disease-Causing Mutation in Cystic Fibrosis

S. Matalon, Z. Bebők, A. Lazrak, 2016, PloS one.

Enhanced cell-surface stability of rescued DeltaF508 cystic fibrosis transmembrane conductance regulator (CFTR) by pharmacological chaperones.

S. Matalon, Z. Bebők, J. Collawn, 2008, The Biochemical journal.

Influenza virus M2 targets cystic fibrosis transmembrane conductance regulator for lysosomal degradation during viral infection

S. Matalon, Z. Bebők, A. Lazrak, 2015, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.

Cystin is required for maintaining fibrocystin (FPC) levels and safeguarding proteome integrity in mouse renal epithelial cells

Wei Wang, E. Sztul, L. Caldovic, 2023, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.

Ablation of Internalization Signals in the Carboxyl-terminal Tail of the Cystic Fibrosis Transmembrane Conductance Regulator Enhances Cell Surface Expression*

Z. Bebők, E. Schwiebert, J. Collawn, 2002, The Journal of Biological Chemistry.

A method for the rapid detection of recombinant CFTR during gene therapy in cystic fibrosis.

A. Pavirani, E. Sorscher, A. Thomas-Soumarmon, 1996, Gene therapy.