Pauci-immune Crescentic Glomerulonephritis in a Patient With Immunoglobulin A Nephropathy and Serum Antineutrophil Cytoplasmic Autoantibody Positivity.

©2018 Turkish League Against Rheumatism. All rights reserved. Immunoglobulin A nephropathy (IgAN) is the most prevalent form of primary glomerulopathy worldwide.1 Antineutrophil cytoplasmic autoantibodies (ANCAs) are commonly associated with vasculitis [ANCA associated vasculitis (AAV)] and a pauci-immune crescentic glomerulonephritis. The co-existence of IgAN and AAV is rare. In this report, we describe the clinical course and treatment of a patient with such an association.

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