Development of muscle pathology in canine X-linked muscular dystrophy. I. Delayed postnatal maturation of affected and normal muscle as revealed by myosin isoform analysis and utrophin expression

[1]  K. Davies,et al.  Skeletal muscle-specific expression of a utrophin transgene rescues utrophin-dystrophin deficient mice , 1998, Nature Genetics.

[2]  Hanns Lochmüller,et al.  High-level dystrophin expression after adenovirus-mediated dystrophin minigene transfer to skeletal muscle of dystrophic dogs: prolongation of expression with immunosuppression. , 1998, Human gene therapy.

[3]  Susan C. Brown,et al.  Utrophin-Dystrophin-Deficient Mice as a Model for Duchenne Muscular Dystrophy , 1997, Cell.

[4]  J. Sanes,et al.  Skeletal and Cardiac Myopathies in Mice Lacking Utrophin and Dystrophin: A Model for Duchenne Muscular Dystrophy , 1997, Cell.

[5]  G. Karpati.  Utrophin muscles in on the action , 1997, Nature Medicine.

[6]  K. Davies,et al.  Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene , 1996, Nature.

[7]  B. Brambati,et al.  Developmental expression of dystrophin, dystrophin-associated glycoproteins and other membrane cytoskeletal proteins in human skeletal and heart muscle. , 1996, Brain research. Developmental brain research.

[8]  Hanns Lochmüller,et al.  Dystrophin expression in muscles of mdx mice after adenovirus-mediated in vivo gene transfer. , 1996, Human gene therapy.

[9]  V. Dubowitz,et al.  Expression of utrophin (dystrophin–related protein) during regeneration and maturation of skeletal muscle in canine X–linked muscular dystrophy , 1994, Neuropathology and applied neurobiology.

[10]  G. Acsadi,et al.  A differential efficiency of adenovirus-mediated in vivo gene transfer into skeletal muscle cells of different maturity. , 1994, Human molecular genetics.

[11]  K. Davies,et al.  Localization and Quantitation of the Chromosome 6-Encoded Dystrophin-Related Protein in Normal and Pathological Human Muscle , 1993, Journal of neuropathology and experimental neurology.

[12]  K. Davies,et al.  The dystrophin-related protein, utrophin, is expressed on the sarcolemma of regenerating human skeletal muscle fibres in dystrophies and inflammatory myopathies , 1992, Neuromuscular Disorders.

[13]  Eric P. Hoffman,et al.  Dystrophin deficiency causes lethal muscle hypertrophy in cats , 1992, Journal of the Neurological Sciences.

[14]  B. Cooper,et al.  Canine X-linked muscular dystrophy: Selective involvement of muscles in neonatal dogs , 1991, Neuromuscular Disorders.

[15]  Simon C Watkins,et al.  Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle , 1991, Neuromuscular Disorders.

[16]  K. Davies,et al.  Localization of the DMDL gene-encoded dystrophin-related protein using a panel of nineteen monoclonal antibodies: presence at neuromuscular junctions, in the sarcolemma of dystrophic skeletal muscle, in vascular and other smooth muscles, and in proliferating brain cell lines , 1991, The Journal of cell biology.

[17]  L. Kunkel,et al.  Identification of a chromosome 6-encoded dystrophin-related protein. , 1990, The Journal of biological chemistry.

[18]  B. Cooper,et al.  Canine X-linked muscular dystrophy: Morphologic lesions , 1990, Journal of the Neurological Sciences.

[19]  B. Cooper,et al.  Mosaic expression of dystrophin in carriers of canine X-linked muscular dystrophy. , 1990, Laboratory investigation; a journal of technical methods and pathology.

[20]  Simon C Watkins,et al.  Dystrophin distribution in heterozygote mdx mice , 1989, Muscle & nerve.

[21]  D. Hill,et al.  An autosomal transcript in skeletal muscle with homology to dystrophin , 1989, Nature.

[22]  B. Cooper,et al.  Canine X-linked muscular dystrophy An animal model of Duchenne muscular dystrophy: Clinical studies , 1988, Journal of the Neurological Sciences.

[23]  Eric P. Hoffman,et al.  The homologue of the Duchenne locus is defective in X-linked muscular dystrophy of dogs , 1988, Nature.

[24]  H. Blau,et al.  Fast muscle fibers are preferentially affected in Duchenne muscular dystrophy , 1988, Cell.

[25]  K. Moore,et al.  X chromosome-linked muscular dystrophy (mdx) in the mouse. , 1984, Proceedings of the National Academy of Sciences of the United States of America.

[26]  Braund Kg,et al.  Histochemical differentiation of fiber types in neonatal canine skeletal muscle. , 1981 .

[27]  K. Braund,et al.  Histochemical differentiation of fiber types in neonatal canine skeletal muscle. , 1981, American journal of veterinary research.

[28]  V. Dubowitz.  Enzyme histochemistry of skeletal muscle. , 1965, Journal of neurology, neurosurgery, and psychiatry.