Lung Clearance Index in Adults and Children With Cystic Fibrosis.

[1]  S. Stanojevic,et al.  A randomized controlled trial to evaluate the lung clearance index as an outcome measure for early phase studies in patients with cystic fibrosis. , 2016, Respiratory medicine.

[2]  S. Stick,et al.  Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection , 2015, European Respiratory Journal.

[3]  Margaret Rosenfeld,et al.  Multiple-Breath Washout as a Lung Function Test in Cystic Fibrosis. A Cystic Fibrosis Foundation Workshop Report. , 2015, Annals of the American Thoracic Society.

[4]  M. Gappa,et al.  Tracking Lung Clearance Index and chest CT in mild cystic fibrosis lung disease over a period of three years. , 2014, Respiratory medicine.

[5]  P. Reix,et al.  Lung clearance index: evidence for use in clinical trials in cystic fibrosis. , 2014, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[6]  P. Lee,et al.  Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial. , 2013, The Lancet. Respiratory medicine.

[7]  A. Wade,et al.  Evolution of lung function during the first year of life in newborn screened cystic fibrosis infants , 2013, Thorax.

[8]  M. Boon,et al.  Lung clearance index predicts pulmonary exacerbations in young patients with cystic fibrosis , 2013, Thorax.

[9]  G. Sawicki,et al.  Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes. , 2013, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[10]  S. Stanojevic,et al.  Lung clearance index as an outcome measure for clinical trials in young children with cystic fibrosis. A pilot study using inhaled hypertonic saline. , 2013, American journal of respiratory and critical care medicine.

[11]  U. Frey,et al.  Practicability of nitrogen multiple‐breath washout measurements in a pediatric cystic fibrosis outpatient setting , 2013, Pediatric pulmonology.

[12]  A. Numa,et al.  Early cystic fibrosis lung disease detected by bronchoalveolar lavage and lung clearance index. , 2012, American journal of respiratory and critical care medicine.

[13]  M. Paiva,et al.  Lung clearance index in adult cystic fibrosis patients: the role of convection-dependent lung units , 2012, European Respiratory Journal.

[14]  A. Wade,et al.  Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening , 2012, Thorax.

[15]  J. Bradley,et al.  159 Lung Clearance Index (LCI) during and following a pulmonary exacerbation (PEx) in patients with CF , 2012 .

[16]  J. Bradley,et al.  WS7.3 Relationships between lung clearance index (LCI), patient reported symptoms and health related quality of life (HRQoL) in CF , 2012 .

[17]  Florian Singer,et al.  A Realistic Validation Study of a New Nitrogen Multiple-Breath Washout System , 2012, PloS one.

[18]  M. Gappa,et al.  Lung clearance index: clinical and research applications in children. , 2011, Paediatric respiratory reviews.

[19]  J. Bradley,et al.  S44 Lung clearance index (LCI) and FEV1 correlate equally with treatment burden as measured by cystic fibrosis questionnaire-revised (CFQ-R) , 2011, Thorax.

[20]  U. Frey,et al.  Long-term course of lung clearance index between infancy and school-age in cystic fibrosis subjects. , 2011, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[21]  P. Sly,et al.  Air Trapping on Chest CT Is Associated with Worse Ventilation Distribution in Infants with Cystic Fibrosis Diagnosed following Newborn Screening , 2011, PloS one.

[22]  F. Ratjen,et al.  Effects Of Forced Expiratory Maneuvers And Bronchodilator On Lung Clearance Index In Infants , 2011, ATS 2011.

[23]  P. Gustafsson,et al.  The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis , 2011, European Respiratory Journal.

[24]  S. Stanojevic,et al.  Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF , 2011, Thorax.

[25]  S. Stanojevic,et al.  Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis. , 2011, American journal of respiratory and critical care medicine.

[26]  M. Gappa,et al.  Sensitivity of Lung Clearance Index and chest computed tomography in early CF lung disease. , 2010, Respiratory medicine.

[27]  M. Hodson,et al.  Cystic fibrosis and survival to 40 years: a study of cystic fibrosis transmembrane conductance regulator function , 2010, European Respiratory Journal.

[28]  F. Ratjen,et al.  Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function , 2010, Thorax.

[29]  P. Aurora Multiple-breath inert gas washout test and early cystic fibrosis lung disease , 2010, Thorax.

[30]  M. Gappa,et al.  Short‐term effect of physiotherapy on variability of the lung clearance index in children with cystic fibrosis , 2010, Pediatric pulmonology.

[31]  S. Cunningham,et al.  Effects of cystic fibrosis lung disease on gas mixing indices derived from alveolar slope analysis , 2008, Respiratory Physiology & Neurobiology.

[32]  S. Stanojevic,et al.  Reference ranges for spirometry across all ages: a new approach. , 2008, American journal of respiratory and critical care medicine.

[33]  D. Porteous,et al.  Lung clearance index is a sensitive, repeatable and practical measure of airways disease in adults with cystic fibrosis , 2007, Thorax.

[34]  H. Tiddens,et al.  Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis , 2007, Thorax.

[35]  M. Rosenfeld An overview of endpoints for cystic fibrosis clinical trials: one size does not fit all. , 2007, Proceedings of the American Thoracic Society.

[36]  A. Quittner,et al.  Development and validation of The Cystic Fibrosis Questionnaire in the United States: a health-related quality-of-life measure for cystic fibrosis. , 2005, Chest.

[37]  J. Hankinson,et al.  Standardisation of spirometry , 2005, European Respiratory Journal.

[38]  Janet Stocks,et al.  Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis. , 2005, American journal of respiratory and critical care medicine.

[39]  J. Stocks,et al.  Multiple breath inert gas washout as a measure of ventilation distribution in children with cystic fibrosis , 2004, Thorax.

[40]  P. Gustafsson,et al.  Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis , 2003, European Respiratory Journal.

[41]  M. Denton,et al.  Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients. , 2003, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[42]  E. Venkatraman,et al.  A Permutation Test to Compare Receiver Operating Characteristic Curves , 2000, Biometrics.

[43]  G. Cutting,et al.  The diagnosis of cystic fibrosis: a consensus statement. Cystic Fibrosis Foundation Consensus Panel. , 1998, The Journal of pediatrics.

[44]  D. Altman,et al.  STATISTICAL METHODS FOR ASSESSING AGREEMENT BETWEEN TWO METHODS OF CLINICAL MEASUREMENT , 1986, The Lancet.

[45]  A. Beckett,et al.  AKUFO AND IBARAPA. , 1965, Lancet.

[46]  L. Lands,et al.  Paediatric Respiratory Reviews , 2016 .

[47]  R. Klocke,et al.  THE AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE , 1994 .