Analysis of nasal potential in murine cystic fibrosis models.
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J. Jais | I. Sermet-Gaudelus | A. Edelman | C. Cottart | A. Hinzpeter | R. Freund | M. F. da Cunha | Juliette Simonin | A. Sassi | A. Hatton | Nadia Elganfoud | Rachid Zoubairi | C. Dragu | Juliette L Simonin
[1] V. Baekelandt,et al. rAAV-CFTRΔR Rescues the Cystic Fibrosis Phenotype in Human Intestinal Organoids and Cystic Fibrosis Mice. , 2016, American journal of respiratory and critical care medicine.
[2] S. Matalon,et al. Inter-α-inhibitor blocks epithelial sodium channel activation and decreases nasal potential differences in ΔF508 mice. , 2014, American journal of respiratory cell and molecular biology.
[3] M. Drumm,et al. Ventilatory pattern and energy expenditure are altered in cystic fibrosis mice. , 2013, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.
[4] I. Sermet-Gaudelus,et al. Characterization of Nasal Potential Difference in cftr Knockout and F508del-CFTR Mice , 2013, PloS one.
[5] O. Kovbasnjuk,et al. Dual activation of CFTR and CLCN2 by lubiprostone in murine nasal epithelia. , 2013, American journal of physiology. Lung cellular and molecular physiology.
[6] S. Noel,et al. PDE5 Inhibitors as Potential Tools in the Treatment of Cystic Fibrosis , 2012, Front. Pharmacol..
[7] P. Lebecque,et al. Comparative Variability of Nasal Potential Difference Measurements in Human and Mice , 2012 .
[8] G. Lukács,et al. Disruption of cytokeratin-8 interaction with F508del-CFTR corrects its functional defect. , 2012, Human molecular genetics.
[9] L. Touqui,et al. Mouse models of cystic fibrosis: phenotypic analysis and research applications. , 2011, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.
[10] M. Rogan,et al. Cystic fibrosis transmembrane conductance regulator intracellular processing, trafficking, and opportunities for mutation-specific treatment. , 2011, Chest.
[11] E. Sorscher,et al. Resveratrol has salutary effects on mucociliary transport and inflammation in sinonasal epithelium , 2011, The Laryngoscope.
[12] E. Sorscher,et al. Hesperidin stimulates cystic fibrosis transmembrane conductance regulator-mediated chloride secretion and ciliary beat frequency in sinonasal epithelium , 2010, Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery.
[13] D. Porteous,et al. Limitations of the murine nose in the development of nonviral airway gene transfer. , 2010, American journal of respiratory cell and molecular biology.
[14] D. Parsons,et al. Lysophosphatidylcholine as an adjuvant for lentiviral vector mediated gene transfer to airway epithelium: effect of acyl chain length , 2010, Respiratory research.
[15] P. Lebecque,et al. Inhaled phosphodiesterase type 5 inhibitors restore chloride transport in cystic fibrosis mice , 2010, European Respiratory Journal.
[16] D. Schuster,et al. The bioflavonoid compound, sinupret, stimulates transepithelial chloride transport in vitro and in vivo , 2010, The Laryngoscope.
[17] Thomas J. Jentsch,et al. Disruption of the K+ Channel β-Subunit KCNE3 Reveals an Important Role in Intestinal and Tracheal Cl− Transport* , 2010, The Journal of Biological Chemistry.
[18] J. Escher,et al. Activation of intestinal Cl- secretion by lubiprostone requires the cystic fibrosis transmembrane conductance regulator. , 2009, Gastroenterology.
[19] L. Ostrowski,et al. Ion transport across CF and normal murine olfactory and ciliated epithelium. , 2009, American journal of physiology. Cell physiology.
[20] P. Lebecque,et al. Airway delivery of low-dose miglustat normalizes nasal potential difference in F508del cystic fibrosis mice. , 2009, American journal of respiratory and critical care medicine.
[21] B. Harfe,et al. Transmembrane Protein 16A (TMEM16A) Is a Ca2+-regulated Cl– Secretory Channel in Mouse Airways* , 2009, Journal of Biological Chemistry.
[22] N. Vij,et al. Lubiprostone activates non-CFTR-dependent respiratory epithelial chloride secretion in cystic fibrosis mice. , 2008, American journal of physiology. Lung cellular and molecular physiology.
[23] Charanjit Singh,et al. Validation of nasal potential difference measurements in gut-corrected CF knockout mice. , 2008, American journal of respiratory cell and molecular biology.
[24] P. Lebecque,et al. Preclinical evidence that sildenafil and vardenafil activate chloride transport in cystic fibrosis. , 2008, American journal of respiratory and critical care medicine.
[25] A. Bush,et al. Nasal abnormalities in cystic fibrosis mice independent of infection and inflammation. , 2008, American journal of respiratory cell and molecular biology.
[26] L. Ostrowski,et al. Expression of CFTR from a ciliated cell-specific promoter is ineffective at correcting nasal potential difference in CF mice , 2007, Gene Therapy.
[27] L. Ostrowski,et al. Olfactory epithelia exhibit progressive functional and morphological defects in CF mice. , 2007, American journal of physiology. Cell physiology.
[28] M. D. De Kock,et al. Successful protocol of anaesthesia for measuring transepithelial nasal potential difference in spontaneously breathing mice , 2006, Laboratory animals.
[29] M. Schluchter,et al. Role of Cftr genotype in the response to chronic Pseudomonas aeruginosa lung infection in mice. , 2004, American journal of physiology. Lung cellular and molecular physiology.
[30] J. Bates,et al. The "Goldilocks Effect" in Cystic Fibrosis: identification of a lung phenotype in the cftr knockout and heterozygous mouse , 2004, BMC Genetics.
[31] N. Pedemonte,et al. CFTR involvement in nasal potential differences in mice and pigs studied using a thiazolidinone CFTR inhibitor. , 2004, American journal of physiology. Lung cellular and molecular physiology.
[32] M. Drumm,et al. Examining basal chloride transport using the nasal potential difference response in a murine model. , 2001, American journal of physiology. Lung cellular and molecular physiology.
[33] W. Colledge,et al. Genistein activates CFTR-mediated Cl(-) secretion in the murine trachea and colon. , 2000, American journal of physiology. Cell physiology.
[34] H. Ye,et al. Distribution of ion transport mRNAs throughout murine nose and lung. , 2000, American journal of physiology. Lung cellular and molecular physiology.
[35] H. Durrington,et al. Importance of basolateral K+ conductance in maintaining Cl− secretion in murine nasal and colonic epithelia , 1998, The Journal of physiology.
[36] L. Tsui,et al. Impaired ability of Cftr knockout mice to control lung infection with Pseudomonas aeruginosa. , 1998, American journal of respiratory and critical care medicine.
[37] D. Sheppard,et al. Comparison of the gating behaviour of human and murine cystic fibrosis transmembrane conductance regulator Cl− channels expressed in mammalian cells , 1998, The Journal of physiology.
[38] L. Tsui,et al. Lung disease in mice with cystic fibrosis. , 1997, The Journal of clinical investigation.
[39] P. French,et al. A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. , 1996, The Journal of clinical investigation.
[40] D. Porteous,et al. Cystic fibrosis mice carrying the missense mutation G551D replicate human genotype‐phenotype correlations. , 1996, The EMBO journal.
[41] L. Tsui,et al. Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor , 1996, Nature Genetics.
[42] K. Thomas,et al. A mouse model for the delta F508 allele of cystic fibrosis. , 1995, The Journal of clinical investigation.
[43] H. Morreau,et al. A mouse model for the cystic fibrosis delta F508 mutation. , 1995, The EMBO journal.
[44] J. Whitsett,et al. Correction of lethal intestinal defect in a mouse model of cystic fibrosis by human CFTR. , 1994, Science.
[45] James M. Wilson,et al. Inefficient gene transfer by adenovirus vector to cystic fibrosis airway epithelia of mice and humans , 1994, Nature.
[46] C. Cotton,et al. Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice. , 1994, Proceedings of the National Academy of Sciences of the United States of America.
[47] R. Boucher,et al. CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship , 1993, Nature.
[48] M. Evans,et al. Production of a severe cystic fibrosis mutation in mice by gene targeting , 1993, Nature Genetics.
[49] B. Koller,et al. An Animal Model for Cystic Fibrosis Made by Gene Targeting , 1992, Science.
[50] P. Scambler,et al. Cloning the mouse homolog of the human cystic fibrosis transmembrane conductance regulator gene. , 1991, Genomics.
[51] L. Tsui,et al. Physical localization of two DNA markers closely linked to the cystic fibrosis locus by pulsed-field gel electrophoresis. , 1989, American journal of human genetics.
[52] M. Brennan,et al. Cystic Fibrosis: A Review of Associated Phenotypes, Use of Molecular Diagnostic Approaches, Genetic Characteristics, Progress, and Dilemmas. , 2016, The Journal of molecular diagnostics : JMD.
[53] L. Tsui,et al. Erratum: Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor (Nature Genetics (1996) 12 (280-287)) , 1996 .
[54] D. R. Adams,et al. Olfactory and non-olfactory epithelia in the nasal cavity of the mouse, Peromyscus. , 1972, The American journal of anatomy.