Spectral Domain Optical Coherence Tomography Findings in Two Cases of X-Linked Juvenil Retinoschisis

X-linked juvenile retinoschisis (XLRS) is a progressive bilateral disease that is probably present at birth and has been manifested by loss of vision in the early childhood. Due to Xlinked transition the disease is seen predominantly in young boys. In this study we report spectral domain optical coherence tomography (SD-OCT) findings of XLRS in two cases of ten years old boy. One patient demonstrates typical spoke-wheel patern and the second patient demonstrates cystic macular appearance on fundus examinations in both eyes. Although there is different ophthalmoscopic feature between two cases, SD-OCT shows the retinoschisis cavities directly and makes the diagnose of the disase easy with high resolution imaging.