Desmoplastic fibroma : A rare entity

Desmoplastic fibroma (DF) is an extremely rare beni gn intraosseus, locally aggressive bone tumor with an incidence of 0.11% of all primary bone tumors. The most common sites of involvement are the mandib le and the metaphysis of long bones. Histologically and biolog ically, desmoplastic fibroma mimics extra-abdominal desmoid tumor of soft tissue. A 25-year male presented to outpatient department w ith increasing pain in left hip region since 2 months. Imaging investigations revea led multiloculated cystic lesion in left femoral region. Curettage material was sent to our department. On h istopathology, sections examined showed spindle-sha ped cells without cytological atypia and abundant colla gen production confirming the diagnosis of desmopla stic fibroma.

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