A Rare Case of Adult Aortopulmonary Window Combined with Anomalous Origin of the Right Pulmonary Artery from the Aorta Leading to Eisenmenger Syndrome

Aortopulmonary window is a rare congenital heart disease that can increase pulmonary vascular resistance, exacerbate left-to-right shunt and lead to heart failure and respiratory tract infections. Most patients die during childhood. We report a 53-year-old male patient with a large aortopulmonary window combined with anomalous origin of the right pulmonary artery from the aorta, with Eisenmenger syndrome and without surgery.

[1]  I. El-rassi,et al.  Aortopulmonary window in adults: A rare entity leading to Eisenmenger syndrome , 2019, Echocardiography.

[2]  T. Gajjar,et al.  Surgical management of aortopulmonary window: 24 years of experience and lessons learned. , 2017, Interactive cardiovascular and thoracic surgery.

[3]  A. Saxena,et al.  Aortopulmonary window: Morphology, diagnosis, and long‐term results , 2017, Journal of cardiac surgery.

[4]  S. Emet,et al.  A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy , 2015, Case reports in cardiology.

[5]  A. Haverich,et al.  Aortopulmonary window: a rare untreated adult case. , 2014, Heart, lung & circulation.

[6]  David Moher,et al.  The CARE Guidelines: Consensus-based Clinical Case Reporting Guideline Development , 2013, Journal of Medical Case Reports.

[7]  S. Aggarwal,et al.  Aortopulmonary window in adults: diagnosis and treatment of late-presenting patients. , 2008, Congenital heart disease.

[8]  Angela Koh Su-Mei,et al.  Large Unrepaired Aortopulmonary Window—Survival into the Seventh Decade , 2007, Echocardiography.

[9]  L. V. van Mierop,et al.  Anatomy and pathogenesis of aorticopulmonary septal defect. , 1987, The American journal of cardiology.

[10]  M. Ando,et al.  Distal type of aortopulmonary window. Report of 4 cases. , 1978, British heart journal.

[11]  W. Shapiro The Eisenmenger syndrome. , 1967, Progress in cardiovascular diseases.

[12]  B. Schultze,et al.  Review of evidence for bosentan therapy for treatment of Eisenmenger syndrome , 2019, Journal of the American Association of Nurse Practitioners.

[13]  I. Pascual Calleja,et al.  [Aortopulmonary window]. , 2008, Anales de pediatria.

[14]  S. Bharati,et al.  Distal aortopulmonary septal defect, aortic origin of the right pulmonary artery, intact ventricular septum, patent ductus arteriosus and hypoplasia of the aortic isthmus: a newly recognized syndrome. , 1982, The American journal of cardiology.