Sickle-cell trait: novel clinical significance.

There is a long-standing controversy in the literature as to whether sickle-cell trait (SCT) should be viewed as a benign carrier state or as an intermediate disease phenotype. Because SCT is routinely detected by neonatal screening for sickle-cell disease, it becomes imperative that consensus on this issue be achieved in order to provide the best medical advice to affected individuals. The issue of selective screening in the post-neonatal period was thrust into the limelight recently by the National Collegiate Athletic Association's recommendation that its member colleges and universities test student-athletes to confirm their carrier status if not already known. The stated goal of this recommendation was to prevent exercise-related sudden death in athletes with SCT. We review some of the reported complications of SCT for which new information has emerged, focusing particularly on venous thromboembolism and renal manifestations.

[1]  B. Freedman,et al.  Sickle cell trait and development of microvascular complications in diabetes mellitus. , 2010, Clinical journal of the American Society of Nephrology : CJASN.

[2]  K. Cavanaugh,et al.  Time to recognize an overlooked trait. , 2010, Journal of the American Society of Nephrology : JASN.

[3]  A. Kshirsagar,et al.  High prevalence of sickle cell trait in African Americans with ESRD. , 2010, Journal of the American Society of Nephrology : JASN.

[4]  D. Gozal,et al.  Remodeling of skeletal muscle microvasculature in sickle cell trait and alpha-thalassemia. , 2010, American journal of physiology. Heart and circulatory physiology.

[5]  G. Mutema,et al.  Renal medullary carcinoma: a report of 2 cases and review of the literature. , 2009, Archives of pathology & laboratory medicine.

[6]  H. Austin,et al.  Hormonal contraception, sickle cell trait, and risk for venous thromboembolism among African American women. , 2009, American journal of obstetrics and gynecology.

[7]  Y. Amoateng-Adjepong,et al.  Complications associated with sickle cell trait: a brief narrative review. , 2009, The American journal of medicine.

[8]  J. Biggio,et al.  Impact of Sickle Hemoglobinopathies on Pregnancy-Related Venous Thromboembolism , 2008, American Journal of Perinatology.

[9]  R. Hakim,et al.  The association of race with erythropoietin dose in patients on long-term hemodialysis. , 2008, American journal of kidney diseases : the official journal of the National Kidney Foundation.

[10]  P. Reese,et al.  Screening for sickle trait among potential live kidney donors: policies and practices in US transplant centers , 2008, Transplant international : official journal of the European Society for Organ Transplantation.

[11]  C. J. Wang,et al.  Communication of positive newborn screening results for sickle cell disease and sickle cell trait: Variation across states , 2008, American journal of medical genetics. Part C, Seminars in medical genetics.

[12]  N. Dowling,et al.  Sickle cell trait and the risk of venous thromboembolism among blacks. , 2007, Blood.

[13]  K. Kiryluk,et al.  Sickle cell trait and gross hematuria. , 2007, Kidney international.

[14]  B. Mitchell Sickle cell trait and sudden death--bringing it home. , 2007, Journal of the National Medical Association.

[15]  P. Stein,et al.  Deep venous thrombosis and pulmonary embolism in hospitalized patients with sickle cell disease. , 2006, The American journal of medicine.

[16]  E. Myers,et al.  Venous thromboembolism during pregnancy and the postpartum period: incidence, risk factors, and mortality. , 2006, American journal of obstetrics and gynecology.

[17]  R. Snow,et al.  Sickle cell trait and the risk of Plasmodium falciparum malaria and other childhood diseases. , 2005, The Journal of infectious diseases.

[18]  A. Ajayi,et al.  Sickle cell trait and gender influence type 2 diabetic complications in African patients. , 2004, European journal of internal medicine.

[19]  C. Quinn,et al.  Survival of children with sickle cell disease. , 2004, Blood.

[20]  P. Watkins,et al.  Albuminuria in Afro‐Caribbeans with Type 2 diabetes mellitus: is the sickle cell trait a risk factor? , 2004, Diabetic medicine : a journal of the British Diabetic Association.

[21]  A. Folsom,et al.  Fibrin fragment D-dimer and the risk of future venous thrombosis. , 2003, Blood.

[22]  N. Dowling,et al.  The epidemiology of venous thromboembolism in Caucasians and African‐Americans: the GATE Study 1 , 2003, Journal of thrombosis and haemostasis : JTH.

[23]  P. Williamson,et al.  Coagulation changes in individuals with sickle cell trait , 2002, American journal of hematology.

[24]  R. Sesso,et al.  Renal dysfunction in patients with sickle cell anemia or sickle cell trait. , 1998, Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas.

[25]  F. Mostofi,et al.  Renal Medullary Carcinoma The Seventh Sickle Cell Nephropathy , 1995, The American journal of surgical pathology.

[26]  J. Kark,et al.  Exercise and hemoglobin S. , 1994, Seminars in hematology.

[27]  Ann M. Johnson,et al.  Autosomal dominant polycystic kidney disease in blacks: clinical course and effects of sickle-cell hemoglobin. , 1994, Journal of the American Society of Nephrology : JASN.

[28]  A. Schechter,et al.  Effects of alpha-thalassemia and sickle polymerization tendency on the urine-concentrating defect of individuals with sickle cell trait. , 1991, The Journal of clinical investigation.

[29]  J. Kark,et al.  Sickle-cell trait as a risk factor for sudden death in physical training. , 1987, The New England journal of medicine.

[30]  M. Steinberg,et al.  Influence of HbS levels upon the hematological and clinical characteristics of sickle cell trait , 1986, American journal of hematology.

[31]  L. Johnson Sickle cell trait: an update. , 1982, Journal of the National Medical Association.

[32]  Julian R. E. Davis,et al.  Concurrent Sickle-Cell Anemia and α-Thalassemia: Effect on Severity of Anemia , 1982 .

[33]  W. Best,et al.  Clinical implications of sickle-cell trait and glucose-6-phosphate dehydrogenase deficiency in hospitalized black male patients. , 1979, The New England journal of medicine.

[34]  D. Sears The morbidity of sickle cell trait: a review of the literature. , 1978, The American journal of medicine.

[35]  Richard T. Jones,et al.  Abnormal hemoglobins in a quarter million people , 1976 .

[36]  B. Culliton Sickle cell anemia: national program raises problems as well as hopes. , 1972, Science.

[37]  L. W. Statius van Eps,et al.  Nature of concentrating defect in sickle-cell nephropathy. Microradioangiographic studies. , 1970, Lancet.

[38]  L. Baker,et al.  Gross hematuria in sickle cell trait and sickle cell hemoglobin-C disease. , 1955, The American journal of medicine.

[39]  A. Allison,et al.  Protection Afforded by Sickle-cell Trait Against Subtertian Malarial Infection , 1954, British medical journal.

[40]  Jackson Mh Tubal patency tests. , 1947 .

[41]  M. Luthra,et al.  The seventh sickle cell nephropathy. , 2010, Internal medicine.

[42]  O. Hue,et al.  This material is the copyright of the original publisher. Unauthorised copying and distribution is prohibited. Physiological Responses of Sickle Cell Trait Carriers during Exercise , 2008 .

[43]  K. Ataga,et al.  Hypercoagulability in sickle cell disease: new approaches to an old problem. , 2007, Hematology. American Society of Hematology. Education Program.

[44]  Y. Kan,et al.  Concurrent sickle-cell anemia and alpha-thalassemia: effect on severity of anemia. , 1982, The New England journal of medicine.