Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs
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D. Meyerholz | M. Welsh | C. Murphy | R. Prather | C. Wohlford-Lenane | M. Rogan | D. Stoltz | J. Zabner | P. McCray | K. Brogden | A. Uc | L. Ostedgaard | A. Rieke | M. Samuel | C. Rogers | O. Itani | T. Starner | A. Pezzulo | Philip H. Karp | Peter J. Taft | Robert A. Hanfland | T. Rokhlina | K. Whitworth | J. Shilyansky | Amanda Kabel | G. J. Davis | T. L. Smith | David Wax
[1] J. T. Fisher,et al. The porcine lung as a potential model for cystic fibrosis. , 2008, American journal of physiology. Lung cellular and molecular physiology.
[2] M. Welsh,et al. Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer. , 2008, The Journal of clinical investigation.
[3] D. Cooper,et al. Selected physiologic compatibilities and incompatibilities between human and porcine organ systems , 2006, Xenotransplantation.
[4] A. Chakravarti,et al. Relative contribution of genetic and nongenetic modifiers to intestinal obstruction in cystic fibrosis. , 2006, Gastroenterology.
[5] J. Carlin,et al. Lower Airway Inflammation in Infants with Cystic Fibrosis Detected by Newborn Screening , 2005, Pediatric pulmonology.
[6] A. Taddei,et al. Discovery of Glycine Hydrazide Pore-occluding CFTR Inhibitors , 2004, The Journal of general physiology.
[7] J. Emerson,et al. Standardized procedure for measurement of nasal potential difference: An outcome measure in multicenter cystic fibrosis clinical trials , 2004, Pediatric pulmonology.
[8] F. Ratjen,et al. Cystic fibrosis , 2003, The Lancet.
[9] D. Look,et al. Inflammatory response in airway epithelial cells isolated from patients with cystic fibrosis. , 2002, American journal of respiratory and critical care medicine.
[10] C. Wise. Epithelial cell culture protocols , 2002 .
[11] J. Christman,et al. Dysregulated Cytokine Production in Human Cystic Fibrosis Bronchial Epithelial Cells , 2001, Inflammation.
[12] S. de Bentzmann,et al. Inflammation and infection in naive human cystic fibrosis airway grafts. , 2000, American journal of respiratory cell and molecular biology.
[13] M. Wilschanski,et al. Pathology of pancreatic and intestinal disorders in cystic fibrosis , 1998, Journal of the Royal Society of Medicine.
[14] G. Roberts,et al. Oral Self-Mutilation Masquerading as Malignancy , 1998, Journal of the Royal Society of Medicine.
[15] L. Gawenis,et al. Increased survival of CFTR knockout mice with an oral osmotic laxative. , 1996, Laboratory animal science.
[16] D. Riches,et al. Early pulmonary inflammation in infants with cystic fibrosis. , 1995, American journal of respiratory and critical care medicine.
[17] C. Higgins,et al. Immunocytochemical localization of the cystic fibrosis gene product CFTR. , 1991, Proceedings of the National Academy of Sciences of the United States of America.
[18] R. Boucher,et al. Regulation of transepithelial ion transport and intracellular calcium by extracellular ATP in human normal and cystic fibrosis airway epithelium , 1991, British journal of pharmacology.
[19] L. Tsui,et al. Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. , 1989, Science.
[20] J. Sturgess,et al. Quantitative evaluation of the development of the exocrine pancreas in cystic fibrosis and control infants. , 1979, The American journal of pathology.
[21] J. Esterly,et al. Hepatic changes in young infants with cystic fibrosis: possible relation to focal biliary cirrhosis. , 1975 .
[22] D. Andersen. CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE: A CLINICAL AND PATHOLOGIC STUDY , 1938 .
[23] G. Downey,et al. Cystic fibrosis mouse models. , 2007, American journal of respiratory cell and molecular biology.
[24] M. Welsh,et al. An in vitro model of differentiated human airway epithelia. Methods for establishing primary cultures. , 2002, Methods in molecular biology.
[25] P. Quinton. Physiological basis of cystic fibrosis: a historical perspective. , 1999, Physiological reviews.
[26] R. Boucher,et al. Pathophysiology of gene-targeted mouse models for cystic fibrosis. , 1999, Physiological reviews.
[27] M. Welsh,et al. Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia. , 1992, The Journal of clinical investigation.
[28] Esterly,et al. Pathology of cystic fibrosis review of the literature and comparison with 146 autopsied cases. , 1975, Perspectives in pediatric pathology.