Pathogenesis of aortic dilatation in mucopolysaccharidosis VII mice may involve complement activation.
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R. Knutsen | R. Mecham | J. Atkinson | K. Ponder | G. Baldo | Jiali Fang | Susan Wu | Yuli Liu | Xiaobo Wu | Ruth Howe | Meera Ramamoothy
[1] D. Judge,et al. Angiotensin II Type 2 Receptor Signaling Attenuates Aortic Aneurysm in Mice Through ERK Antagonism , 2011, Science.
[2] T. Fujita,et al. Essential Role of Complement Mannose-Binding Lectin-Associated Serine Proteases-1/3 in the Murine Collagen Antibody-Induced Model of Inflammatory Arthritis , 2010, The Journal of Immunology.
[3] M. Haskins,et al. Upregulation of elastase activity in aorta in mucopolysaccharidosis I and VII dogs may be due to increased cytokine expression. , 2010, Molecular genetics and metabolism.
[4] J. Lambris,et al. Crosstalk pathways between Toll-like receptors and the complement system. , 2010, Trends in immunology.
[5] A. Schambach,et al. A Self-inactivating γ-Retroviral Vector Reduces Manifestations of Mucopolysaccharidosis I in Mice. , 2010, Molecular therapy : the journal of the American Society of Gene Therapy.
[6] T. Fujita,et al. Essential role of Mannose-binding lectin-associated serine protease-1 in activation of the complement factor D , 2010, The Journal of experimental medicine.
[7] K. Jepsen,et al. Involvement of the Toll-like receptor 4 pathway and use of TNF-α antagonists for treatment of the mucopolysaccharidoses , 2009, Proceedings of the National Academy of Sciences.
[8] D. Turk,et al. Monitoring compartment-specific substrate cleavage by cathepsins B, K, L, and S at physiological pH and redox conditions , 2009 .
[9] M. Sands,et al. Metabolic Adaptations to Interrupted Glycosaminoglycan Recycling* , 2009, The Journal of Biological Chemistry.
[10] John D Lambris,et al. Complement-Dependent Neutrophil Recruitment Is Critical for the Development of Elastase-Induced Abdominal Aortic Aneurysm , 2009, Circulation.
[11] Lionel B Ivashkiv,et al. Cross-regulation of signaling by ITAM-associated receptors , 2009, Nature Immunology.
[12] John G. Oakeshott,et al. Bridging the Synaptic Gap: Neuroligins and Neurexin I in Apis mellifera , 2008, PloS one.
[13] R. Knutsen,et al. Upregulation of elastase proteins results in aortic dilatation in mucopolysaccharidosis I mice. , 2008, Molecular genetics and metabolism.
[14] D. Cheillan,et al. Early Neurodegeneration Progresses Independently of Microglial Activation by Heparan Sulfate in the Brain of Mucopolysaccharidosis IIIB Mice , 2008, PloS one.
[15] J. Wilson,et al. The mild form of mucopolysaccharidosis type I (Scheie syndrome) is associated with increased ascending aortic stiffness , 2008, Heart and Vessels.
[16] B. Fingleton. MMPs as therapeutic targets--still a viable option? , 2008, Seminars in cell & developmental biology.
[17] M. Haskins,et al. Gene therapy for mucopolysaccharidosis , 2007, Expert opinion on biological therapy.
[18] C. Vite,et al. Correction of clinical manifestations of canine mucopolysaccharidosis I with neonatal retroviral vector gene therapy. , 2007, Molecular therapy : the journal of the American Society of Gene Therapy.
[19] C. Vite,et al. Bone marrow transplantation for feline mucopolysaccharidosis I. , 2007, Molecular genetics and metabolism.
[20] R. Hoft,et al. A follow-up study of MPS I patients treated with laronidase enzyme replacement therapy for 6 years. , 2007, Molecular genetics and metabolism.
[21] J. Berry,et al. Cardiac findings after enzyme replacement therapy for mucopolysaccharidosis type I. , 2006, The American journal of cardiology.
[22] B. Baxter,et al. MMP-12 has a role in abdominal aortic aneurysms in mice. , 2005, Surgery.
[23] S. Ryazantsev,et al. Cardiac manifestations in the mouse model of mucopolysaccharidosis I. , 2005, Molecular genetics and metabolism.
[24] Dean Y. Li,et al. Effects of elastin haploinsufficiency on the mechanical behavior of mouse arteries. , 2005, American journal of physiology. Heart and circulatory physiology.
[25] O. Vasiljeva,et al. Recombinant human procathepsin S is capable of autocatalytic processing at neutral pH in the presence of glycosaminoglycans , 2005, FEBS letters.
[26] T. O'Malley,et al. Gene Therapy Ameliorates Cardiovascular Disease in Dogs With Mucopolysaccharidosis VII , 2004, Circulation.
[27] M. Bogyo,et al. Regulation of Collagenase Activities of Human Cathepsins by Glycosaminoglycans* , 2004, Journal of Biological Chemistry.
[28] J. Berry,et al. Usefulness of bone marrow transplantation in the Hurler syndrome. , 2003, The American journal of cardiology.
[29] P. Libby,et al. Deficiency of the Cysteine Protease Cathepsin S Impairs Microvessel Growth , 2003, Circulation research.
[30] Makoto Naito,et al. Deficiency of cathepsin S reduces atherosclerosis in LDL receptor-deficient mice. , 2003, The Journal of clinical investigation.
[31] J. Lemontt,et al. Replacement therapy in Mucopolysaccharidosis type VI: advantages of early onset of therapy. , 2003, Molecular genetics and metabolism.
[32] S. Ryazantsev,et al. Activated microglia in cortex of mouse models of mucopolysaccharidoses I and IIIB , 2003, Proceedings of the National Academy of Sciences of the United States of America.
[33] M. Haskins,et al. Evaluation of pathological manifestations of disease in mucopolysaccharidosis VII mice after neonatal hepatic gene therapy. , 2002, Molecular therapy : the journal of the American Society of Gene Therapy.
[34] G. Aguirre,et al. Therapeutic neonatal hepatic gene therapy in mucopolysaccharidosis VII dogs , 2002, Proceedings of the National Academy of Sciences of the United States of America.
[35] Cuihua Gao,et al. Transduction of hepatocytes after neonatal delivery of a Moloney murine leukemia virus based retroviral vector results in long-term expression of beta-glucuronidase in mucopolysaccharidosis VII dogs. , 2002, Molecular therapy : the journal of the American Society of Gene Therapy.
[36] T. O'Malley,et al. Effects of bone marrow transplantation on the cardiovascular abnormalities in canine mucopolysaccharidosis VII , 2000, Bone Marrow Transplantation.
[37] S. Wilson,et al. Impaired elastogenesis in Hurler disease: dermatan sulfate accumulation linked to deficiency in elastin-binding protein and elastic fiber assembly. , 2000, The American journal of pathology.
[38] S. Evans,et al. Bone marrow transplantation in newborn rats with mucopolysaccharidosis type VI: biochemical, pathological, and clinical findings. , 1997, Transplantation.
[39] R. Maciewicz,et al. Activation of cathepsin B, secreted by a colorectal cancer cell line requires low pH and is mediated by cathepsin D , 1996, International journal of cancer.
[40] T. Ley,et al. Metalloelastase is required for macrophage-mediated proteolysis and matrix invasion in mice. , 1996, Proceedings of the National Academy of Sciences of the United States of America.
[41] John C. Anderson,et al. Age-related changes in amounts and concentrations of collagen and elastin in normotensive human thoracic aorta. , 1996, Clinica chimica acta; international journal of clinical chemistry.
[42] J. Schofield. Metabolic and molecular basis of inherited disease: paper versus electronic media , 1995 .
[43] M. Zuker,et al. The endogenous vascular elastase that governs development and progression of monocrotaline-induced pulmonary hypertension in rats is a novel enzyme related to the serine proteinase adipsin. , 1994, The Journal of clinical investigation.
[44] W. Sly,et al. Increased life span and correction of metabolic defects in murine mucopolysaccharidosis type VII after syngeneic bone marrow transplantation. , 1991, Blood.
[45] G. Constantopoulos,et al. Cardiovascular changes after bone marrow transplantation in dogs with mucopolysaccharidosis I. , 1990, American journal of veterinary research.
[46] A. Barrett,et al. Elastinolytic activity of human cathepsin L. , 1986, The Biochemical journal.
[47] W. Roberts,et al. The heart in the Hurler syndrome: gross, histologic and ultrastructural observations in five necropsy cases. , 1976, The American journal of cardiology.
[48] A. Beaudet,et al. Variation in the phenotypic expression of β-glucuronidase deficiency , 1975 .
[49] D. Brömme,et al. Role of Cysteine Cathepsins in Extracellular Proteolysis , 2011 .
[50] A. Schambach,et al. A self-inactivating gamma-retroviral vector reduces manifestations of mucopolysaccharidosis I in mice. , 2010, Molecular therapy : the journal of the American Society of Gene Therapy.
[51] M. Haskins,et al. Mechanism of glycosaminoglycan-mediated bone and joint disease: implications for the mucopolysaccharidoses and other connective tissue diseases. , 2008, The American journal of pathology.
[52] J. Tolar,et al. Cardiac Functional and Histopathologic Findings in Humans and Mice with Mucopolysaccharidosis Type I: Implications for Assessment of Therapeutic Interventions in Hurler Syndrome , 2006, Pediatric Research.
[53] S. Cai,et al. Liver-directed neonatal gene therapy prevents cardiac, bone, ear, and eye disease in mucopolysaccharidosis I mice. , 2005, Molecular therapy : the journal of the American Society of Gene Therapy.
[54] A. Beaudet,et al. Variation in the phenotypic expression of beta-glucuronidase deficiency. , 1975, The Journal of pediatrics.
[55] F. Shofer,et al. Clinical Characterization of Cardiovascular Abnormalities Associated with Feline Mucopolysaccharidosis I and Vi , 2022 .
[56] O. Soliman,et al. Cardiac Abnormalities in Adults with the Attenuated Form of Mucopolysaccharidosis Type I , 2022 .