A RARE FAMILIAL SYSTEMIC AFFECTION OF THE SKELETON: FAIRBANK'S DISEASE.

The case to be presented in this paper belongs to a large group of sclerotic affections involving the skeletal system. Many articles clearly defining these various entities have been written since the early days of radiology, though little has actually been added to their descriptions in that time. Some of these abnormalities are seen not uncommonly in the general practice of radiology, while others are represented by only single case reports. The present report includes information covering four generations. The patient's father suffered the same disease process and a chest film demonstrated the same findings; he died of severe aortic valvular stenosis. The disease process is also well documented in the patient's grandfather, though films were unavailable for demonstration purposes. A child six years of age has been studied, but without evidence of skeletal abnormality. The case presented falls into a group of skeletal affections described in 1943 by Uehlinger (3), whose name they now bear. They are know...