Prune belly syndrome.

SUMMARY The Prune Belly Syndrome is a congenitally occurring group of anomalies found almost exclusively in new-born males. The three principle features are absent or hypoplastic musculature of the abdominal wall, bilateral cryptorchism, and dilation of the urinary tract. Early drainage of the kidneys by bilateral cutaneous loop ureterostomies may be necessary to preserve borderline renal function until the child matures enough to have surgery to provide adequate drainage and freedom from infection. The cause of the syndrome is probably some undetermined insult to the embryo between its fifth and eight gestational week. One hundred and seventy five cases have been previously reported; 16 cases seen in Pittsburg since 1953 are reviewed with the principles of management.

[1]  V. F. Marshall,et al.  The prune belly syndrome: a diagnostic therapeutic plan. , 1970, The Journal of urology.

[2]  P. Kelalis,et al.  Prune-Belly Syndrome Clinical Findings and Survival , 1969 .

[3]  D. Williams,et al.  The prune belly syndrome. , 1967, The Journal of urology.

[4]  J. Cerny,et al.  Congenital absence of abdominal muscles: report of 6 cases. , 1967, The Journal of urology.

[5]  J. Lagergren,et al.  Congenital Aplasia of the Abdominal Muscles with Urogenital Malformations , 1964, Acta radiologica: diagnosis.

[6]  T. Allen,et al.  CONGENITAL ABSENCE OF ABDOMINAL MUSCULATURE. UROLOGIC ASPECTS. , 1964, JAMA.

[7]  J. Brierre.  Congenital abnormalities of the genitourinary tract: abdominal muscle dysplasia and choanal atresia. , 1963, Pediatrics.

[8]  F. D. Stephens,et al.  The triad syndrome: a composite anomaly of the abdominal wall, urinary system and testes. , 1961, The Journal of urology.

[9]  J. Lattimer.  Congenital deficiency of the abdominal musculature and associated genitourinary anomalies: a report of 22 cases. , 1958, The Journal of urology.

[10]  S. Metrick,et al.  Congenital absence of the abdominal musculature and associated anomalies; review of recent literature and four new cases. , 1957, Pediatrics.

[11]  B. Mathieu,et al.  Congenital deficiency of the abdominal muscles, with associated multiple anomalies. , 1953, Jornal de Pediatria.

[12]  J. Eagle,et al.  Congenital deficiency of abdominal musculature with associated genitourinary abnormalities: A syndrome. Report of 9 cases. , 1950, Pediatrics.

[13]  F. N. Silverman,et al.  Congenital absence of the abdominal muscles associated with malformation of the genitourinary and alimentary tracts; report of cases and review of literature. , 1950, American journal of diseases of children.

[14]  P. Howard.  CONGENITAL ABSENCE OF THE ABDOMINAL MUSCLES AND GENITOURINARY MALFORMATION: REPORT OF TWO CASES , 1940 .

[15]  W. Gardner.  Sexual dimorphism of the pelvis of the mouse, the effect of estrogenic hormones upon the pelvis and upon the development of scrotal hernias , 1936 .

[16]  W. Gardner.  Pelvic Changes Occurring in Male Mice Receiving Large Amounts of Folliculin Benzoate , 1935 .