Cerebral angioendotheliomatosis: a report of two cases and review of the literature.

Cerebral angioendotheliomatosis is a rare form of vascular neoplasia characterized by rapidly progressive dementia and multifocal neurologic deficits. Histologically there is prolifera­ tion of neoplastic cells within the lumina of arteries, arterioles, capillaries, and venules, which results in multiple infarcts within the brain and spinal cord . Although rare, angioendo­ theliomatosis should be considered in the differential diagno­ sis of multifocal vascular disease and rapidly progressive dementia. We report the neuroradiologic findings in two cases of angioendotheliomatosis and review the literature on this disease.