The Use of Airway with K-Wire for Pierre Robin Sequence

Pierre Robin Sequence (PRS) is characterized in the triad of glossoptosis, micrognathia, and airway obstruction. The first potential problem for newborn patients is airway obstruction; if we do not manage the respiration appropriately, the baby may die. We were able to manage the respiration of 2 isolated PRS patients without performing surgery by using an airway that increased original improvement (K-wire airway). This method was evaluated by lateral cephalometric radiographs and apnea monitors. The main advantages of this method are as follows: (1)To be able to manage without performing surgery. (2)To be able to breathe through the nostrils without using the K-wire airway. (3)To be 1静岡県立こども病院形成外科(主 任 朴 修三) 2杏林大学形成外科 Department of Plastic and Reconstructive Surgery, Shizuoka Children Hospital (Chief: Prof. Susam PARK) Department of Plastic, Reconstructive and Aesthetic Surgery, School of Medicine, Kyorin University 別刷請求先:堀 切 将 〒420-8660静 岡県静岡市葵区漆山860 静岡県立こ ども病 院形成外科 〔2008年1月9日 受付 〕 able to shape the appropriate form for each child and to change the form with growth. The main disadvantages of this method are as follows: (1)The lumen of the airway easily becomes full of secretions. (2)Hospitalization is longer.(3)Respiration may become worse two months after birth. However, if the family of the patient participates in the treatment positively, these problems will be resolved. We think that this method is worth trying for the respiratory management of PRS children presenting airway obstruction.

[1]  J. McCarthy,et al.  Long-Term Stability and Growth following Unilateral Mandibular Distraction in Growing Children with Craniofacial Microsomia , 2006, Plastic and reconstructive surgery.

[2]  J. Hage,et al.  Pierre Robin syndrome: mandibular growth during the first year of life. , 1999, Annals of plastic surgery.

[3]  J. Gershanik,et al.  Nasoesophageal Intubation in the Pierre Robin Syndrome , 1976 .

[4]  Mikael Andersen,et al.  Pierre Robin Sequence in Denmark: A Retrospective Population-Based Epidemiological Study , 2004, The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association.

[5]  N. Mitsukawa,et al.  Clinical Success of Mandibular Distraction for Obstructive Sleep Apnea Resulting From Micrognathia in 10 Consecutive Japanese Young Children , 2007, The Journal of craniofacial surgery (Print).

[6]  L. Lo,et al.  Robin sequence: review of treatment modalities for airway obstruction in 110 cases. , 2002, International journal of pediatric otorhinolaryngology.

[7]  L. Caouette‐Laberge,et al.  Innovative Surgical Approach for the Pierre Robin Anomalad: Subperiosteal Release of the Floor of the Mouth Musculature , 1989, Plastic and reconstructive surgery.

[8]  R. Routledge The pierre-robin syndrome: A surgical emergency in the neonatal period , 1960 .

[9]  E. Moore,et al.  Mandibular distraction osteogenesis to relieve Pierre Robin airway obstruction. , 2006, American journal of otolaryngology.

[10]  R. Ranta,et al.  Cephalometric measurements in patients with Pierre Robin syndrome and isolated cleft palate. , 1992, Scandinavian journal of plastic and reconstructive surgery and hand surgery.

[11]  A. Figueroa,et al.  Mandible, Tongue, and Airway in Pierre Robin Sequence: A Longitudinal Cephalometric Study , 1991 .

[12]  S. Pruzansky,et al.  Growth of mandible in infants with micrognathia; clinical implications. , 1954, A.M.A. American journal of diseases of children.

[13]  J. Béziat,et al.  Sensitivity of the Inferior Lip and Chin following Mandibular Bilateral Sagittal Split Osteotomy Using Piezosurgery , 2006, Plastic and reconstructive surgery.

[14]  I. Masters,et al.  Modified nasopharyngeal tube for upper airway obstruction , 1999, Archives of disease in childhood.