Congenital Absence of the Left Pulmonary Artery: Association with Congenital Bronchiectasis and Hemophilia

Bronchiectasis is a condition which every physician may expect to see in a lifetime. In the present case, however, it coexisted with hemophilia and congenital absence of the left pulmonary artery. Tachycardia, productive cough, dyspnea on exertion, and episodes of pleuritic pain had existed for many years. The patient was 47 years of age when he came to be treated for an acute onset of chills, fever, cough, and pain in his chest. At operation the left lung was found to be polycystic and was removed; at the same time the extensive anomalies of the pulmonary circulation were disclosed. The hemorrhagic tendency was dealt with successfully, and the patient re