Impaired ketogenesis in patients with adult-type citrullinemia.
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Y. Matsuzawa | S. Kawata | S. Tarui | N. Kono | M. Kuwajima | Y. Inui | K. Fukuda | T. Igura | Y. Maeda
[1] W. C. McMurray,et al. Citrullinuria. A new aminoaciduria associated with mental retardation. , 1962 .
[2] Y. Matsuzawa,et al. Increased level of apolipoprotein B mRNA in the liver of ventromedial hypothalamus lesioned obese rats. , 1989, Biochemical and biophysical research communications.
[3] T. Saheki,et al. Treatment of adult-type citrullinemia with oral administration of citrate , 1980 .
[4] G. Labbe,et al. Inhibition of mitochondrial beta-oxidation of fatty acids by pirprofen. Role in microvesicular steatosis due to this nonsteroidal anti-inflammatory drug. , 1987, The Journal of pharmacology and experimental therapeutics.
[5] G. Labbe,et al. Inhibition of the mitochondrial oxidation of fatty acids by tetracycline in mice and in man: Possible role in microvesicular steatosis induced by this antibiotic , 1988, Hepatology.
[6] Y. Matsuzawa,et al. Inhibitory effect of a new α-glucosidase inhibitor on fatty liver in Zucker fatty rats , 1990 .
[7] L. Barness,et al. Citrullinemia with defective urea production. , 1967, Pediatrics.
[8] T. Saheki,et al. Immunohistochemical localization of argininosuccinate synthetase in the liver of control and citrullinemic patients , 1983 .
[9] T. Saheki,et al. Arginine Metabolism in Citrullinemic Patients , 1985 .
[10] C. Rebouche,et al. Carnitine metabolism and function in humans. , 1986, Annual review of nutrition.
[11] S. K. Wadman,et al. Urinary purines and pyrimidines in patients with hyperammonemia of various origins. , 1980, Clinica chimica acta; international journal of clinical chemistry.
[12] S. Chaithiraphan,et al. Letter: Propranolol and digitalis. , 1974, Lancet.
[13] T. Saheki,et al. Serum Amino Acid Pattern of Type II Citrullinemic Patients and Effect of Oral Administration of Citrulline , 1986 .
[14] S. Ratner. [48] Enzymatic synthesis of arginine (condensing and splitting enzymes) , 1955 .
[15] P. Handler,et al. Fatty Liver Induced by Orotic Acid Feeding , 1955, Proceedings of the Society for Experimental Biology and Medicine. Society for Experimental Biology and Medicine.
[16] Y. Matsuzawa,et al. Morphological study of lipoprotein particles in the livers of ventromedial hypothalamus lesioned rats. , 1987, International journal of obesity.
[17] T. Tsujii,et al. A case of Nutritional Form of Hepatocerebral disease , 1975 .
[18] R. Schimke. Adaptive characteristics of urea cycle enzymes in the rat. , 1962, The Journal of biological chemistry.
[19] K. Hasumi,et al. GC/MS Analysis of Urine in 3‐Hydroxy‐3‐Methylglutaryl‐CoA Lyase Deficiency , 1992, Acta paediatrica Japonica : Overseas edition.
[20] M. Ogasawara,et al. [A case of adult-type citrullinemia]. , 1988, Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine.
[21] T. Saheki,et al. Animal model of systemic carnitine deficiency: Analysis in C3H-H-2° strain of mouse associated with juvenile visceral steatosis , 1991 .
[22] T. Saheki,et al. Enzymatic analysis of citrullinemia (12 cases) in Japan. , 1982, Advances in experimental medicine and biology.
[23] W. S. Thayer. Inhibition of mitochondrial fatty acid oxidation in pentenoic acid-induced fatty liver. A possible model for Reye's syndrome. , 1984, Biochemical pharmacology.
[24] J. McGarry,et al. Regulation of hepatic fatty acid oxidation and ketone body production. , 1980, Annual review of biochemistry.
[25] T. Saheki,et al. Qualitative and quantitative abnormalities of argininosuccinate synthetase in citrullinemia. , 1981, Clinica chimica acta; international journal of clinical chemistry.