Rapunzel Syndrome: A Rare Cause of Biliary Obstruction

522 e is a rare manifestat ands of hair extendin R apunzel syndrom ion of gastric trichobezoars with str g beyond the pylorus into the small intestine, and occasionally up to the colon. So far, only 29 cases of Rapunzel syndrome have been reported in the literature worldwide, with the first case described in 1968 (1). With the exception of 1 male, all of the other reported cases were females. Nausea, vomiting, abdominal pain, and symptoms of obstruction were the common presenting features. Trichobezoars rarely results in biliary obstruction or pancreatitis. We describe a 3-year-old girl with Rapunzel syndrome presenting with a picture of cholestasis because of biliary obstruction from a trichobezoar.

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