True Aneurysm of the Common Coronary Button in a Marfan Patient with an Anomalous Right Coronary Artery after a Bentall Procedure: A Case Report

True aneurysms of the coronary artery after aortic root replacement in Marfan syndrome patients are very rare. An anomalous origin of the right coronary artery (RCA) from the left sinus of Valsalva adds complexity during aortic root surgery. We present a case of a 37-year-old male patient with Marfan syndrome who had an RCA anomaly and a 4.5-cm true aneurysm of the common coronary button 14 years after a previous Bentall procedure. A redo Bentall operation and hemi-arch replacement were successfully performed. The anomalous origin of the RCA from the left sinus of Valsalva was safely divided and anastomosed as separate coronary buttons to the prosthetic composite valve graft. To prevent coronary button aneurysms after aortic root surgery in Marfan patients, the coronary buttons and the corresponding side holes on the prosthetic graft must be reduced to the maximum possible extent.

[1]  W. Roberts,et al.  Giant Right Coronary Artery Aneurysms. , 2020, The American journal of cardiology.

[2]  L. Chu,et al.  Prevalence and Natural History of Coronary Ostial Aneurysms in Marfan Patients , 2019, Journal of computer assisted tomography.

[3]  L. Martinelli,et al.  Giant true aneurysm of the right coronary artery button long after aortic root replacement. , 2013, European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery.

[4]  F. Casselman,et al.  Giant left coronary ostial aneurysm after modified Bentall procedure in a Marfan patient. , 2008, Interactive cardiovascular and thoracic surgery.

[5]  T. Kazui,et al.  Late reoperation for proximal aortic and arch complications after previous composite graft replacement in Marfan patients. , 2003, The Annals of thoracic surgery.

[6]  J. Tijssen,et al.  Frequency of coronary ostial aneurysms after aortic root surgery in patients with the Marfan syndrome. , 2002, The American journal of cardiology.

[7]  I. Yada,et al.  Coronary artery aneurysm in a patient with Marfan syndrome. , 2001, The Annals of thoracic surgery.

[8]  J. Niinikoski,et al.  Composite graft in annulo-aortic ectasia. Nineteen years' experience without graft inclusion. , 1996, European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery.