The Lung Life of a Cystic Fibrosis Patient: A Patient and Physician Perspective

[1]  L. Lands,et al.  Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele. , 2019, The New England journal of medicine.

[2]  J. Pilewski,et al.  Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines. , 2019, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[3]  M. Gentzsch,et al.  Ion Channel Modulators in Cystic Fibrosis , 2018, Chest.

[4]  M. Gentzsch,et al.  Recent progress in translational cystic fibrosis research using precision medicine strategies. , 2017, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[5]  R. Szczesniak,et al.  Detection of CFTR function and modulation in primary human nasal cell spheroids. , 2018, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[6]  Justin M. Leach,et al.  Nasospheroids permit measurements of CFTR-dependent fluid transport. , 2017, JCI insight.

[7]  H. Clevers,et al.  Characterizing responses to CFTR-modulating drugs using rectal organoids derived from subjects with cystic fibrosis , 2016, Science Translational Medicine.

[8]  Garry R. Cutting,et al.  From CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations , 2016, Molecular biology of the cell.

[9]  L. Saiman,et al.  Infection Prevention and Control Guideline for Cystic Fibrosis: 2013 Update , 2014, Infection Control & Hospital Epidemiology.

[10]  Hans Clevers,et al.  A functional CFTR assay using primary cystic fibrosis intestinal organoids , 2013, Nature Medicine.

[11]  Margaret Rosenfeld,et al.  Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation. , 2010, American journal of respiratory and critical care medicine.

[12]  G. Sawicki,et al.  High treatment burden in adults with cystic fibrosis: challenges to disease self-management. , 2009, Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society.

[13]  David Rodman,et al.  Cystic fibrosis adult care: consensus conference report. , 2004, Chest.