Psoriasiform Febrile Ulceronecrotic Mucha Habermann Disease: A New Clinical Presentation of a Case Report from Upper Egypt

FUMHD is a rare life-threatening variant of pityriasis lichenoides et varioliformis acuta (PLEVA) that is characterized clinically by rapidly progressive necrotic and ulcerating skin lesions together with high fever and various systemic affections. Histological characteristics are typical of PLEVA. The exact pathogenesis of FUMHD remains unclear, with no universally effective treatment [1]. As far as we know, only one case was reported in our country (Lower Egypt) in children by Nofel et al in 2016 [2]. However, no cases were reported from Upper Egypt.

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