De Clerambault’s Syndrome (Erotomania) As a Presenting Feature of Fronto-Temporal Dementia and Motor Neurone Disease (FTD-MND)

Motor neurone disease (MND) is characterized by the progressive degeneration of lower and upper motor neurones in the spinal cord, brainstem and motor cortex of the brain, leading to a variable pattern of motor dysfunction. Typical symptoms include muscle atrophy, limb weakness, bulbar palsy and respiratory failure. Fronto-Temporal Dementia (FTD) is a common neurodegenerative disorder associated with progressive atrophy of the frontal and temporal lobes of the brain, resulting in changes in personality and behaviour and/or speech and language dysfunction. Fifty per cent of patients with MND exhibit frontal executive deficits during the course of their illness, representing in most instances the co-occurrence of FTD. Previous

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