Erdheim-Chester Disease Presenting with Secondary Hypertension as a Result of Bilateral, Proximal Renal Artery Stenosis: A Case Report

Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis presenting most commonly with bone and central nervous system symptoms, including but not limited to bone pain and diabetes insipidus. We present a known case of ECD, which was referred for secondary hypertension workup and diagnosed with severe, proximal, bilateral renal artery stenosis.

[1]  M. Debray,et al.  Erdheim-Chester disease as assessed by modern multimodality imaging. , 2016, International journal of cardiology.

[2]  Jian Sun,et al.  Evaluation of clinicopathologic characteristics and the BRAF V600E mutation in Erdheim-Chester disease among Chinese adults , 2015, Annals of Hematology.

[3]  A. Carnicelli,et al.  Cardiovascular Involvement in Erdheim–Chester Disease , 2015, Medicine.

[4]  G. Ingravallo,et al.  Erdheim-Chester disease: a systematic review. , 2015, Critical reviews in oncology/hematology.

[5]  J. Bosco,et al.  Does the BRAFV600E mutation herald a new treatment era for Erdheim–Chester disease? A case‐based review of a rare and difficult to diagnose disorder , 2015, Internal medicine journal.

[6]  F. Weaver,et al.  Bilateral renal artery involvement of erdheim-chester disease. , 2014, Annals of vascular surgery.

[7]  C. Ponticelli,et al.  Improvement of Erdheim-Chester disease-related renal failure after treatment with anakinra , 2014, Kidney research and clinical practice.

[8]  O. Abdel-Wahab,et al.  Consensus guidelines for the diagnosis and clinical management of Erdheim-Chester disease. , 2014, Blood.

[9]  A. Abdelfattah,et al.  Erdheim-Chester disease: a comprehensive review. , 2014, Anticancer research.

[10]  Y. Shoenfeld,et al.  Erdheim-Chester Disease: a comprehensive review of the literature , 2013, Orphanet Journal of Rare Diseases.

[11]  C. Campochiaro,et al.  The multifaceted clinical presentations and manifestations of Erdheim–Chester disease: comprehensive review of the literature and of 10 new cases , 2013, Annals of the rheumatic diseases.