SUPPOSED BARRIERS AND MOTIVATORS TO PHYSICAL ACTIVITY IN PATIENTS WITH CHARCOT-MARIE-TOOTH DISEASE

Abstract. Disorders of physical activity in patients with Charcot-Marie-Tooth disease (CMT) can cause disease progression and decreasing time of disability, however, is treatable through regular physical activity. For keeping the physical activity of the patient with CMT it is important to understand how he “sees” the barriers and motivators. Therefore, we tried to systematize the supposed barriers and motivators in the physical activity of patients with CMT. It was conducted tn electronic search in 4 English (Medline, PubMed, ClinicalKey, Springer) and one Russian-speaking (e-LIBRARY) databases. We have included peer-reviewed journal articles in English and Russian languages, published from 1 January 1990 to 30 August 2014, devoted to physical activity in patients with CMT. The searches found 68874 citations, 35 full articles were restored from them. The most common barriers were lack of motivation, environmental factors (eg, transportation), health problems and disorders associated with CMT. The mos t common motivators were social support and daily tasks at work and at home. This review will promote the development of medical and social and habilitation activities aimed at removing of existing barriers, and at the same time, based on the patients most important motivators, will be the basis for increasing and maintaining of physical activity in patients with CMT.

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