Giant Fibrosarcoma Arising in Dermatofibrosarcoma Protuberans on the Scalp During Pregnancy

BACKGROUND Dermatofibrosarcoma protuberans (DFSP) is a low-grade malignant soft tissue tumor of subcutaneous tissues that has a propensity for local recurrence; however, it seldom metastasizes. Most lesions occur over the trunk or proximal extremities, and there is slight male preponderance. DFSP is rare on the head and neck. Less than 5% tumors are located on the scalp. OBJECTIVE To describe a case of giant fibrosarcoma arising in DFSP on the scalp during pregnancy. METHOD In our patient, the tumor was on scalp and measured 15×11×7 cm. The recurrent tumor that developed in the same region was measured 33×30×15 cm. Histopathologic examination of this mass revealed fibrosarcoma. The mass was excised from the subperiosteal plane with a 3-cm free margin. Because of the high possibility of recurrence, the defect site was reconstructed with a split-thickness skin graft. Results After 1 year of follow-up, no recurrence or metastasis was detected. CONCLUSION We present a unique case in which the person has a giant fibrosarcoma on her scalp arising from DFSP with fibrosarcomatous change during pregnancy.