Corrected Transposition of the Great Vessels, Atrioventricular Heart Block, and Ventricular Septal Defect: A Clinical Triad

Three cases with the triad of ventricular septal defect, atrioventricular heart block, and corrected transposition of the great vessels are presented. In each instance the patient successfully underwent open heart surgery on the pump-oxygenator for closure of the ventricular septal defect. A review of the literature suggests a frequent association of these 3 congenital anomalies. In our experience atrioventricular heart block is rarely encountered with simple ventricular septal defect. The finding of atrioventricular heart block in a patient with an interventricular septal defect warrants consideration of an associated corrected transposition of the great vessels.