Postoperative Respiratory Complications of Patients with Myotonic Dystrophy

筋緊張性ジストロフィー（myotonic dystrophy：MD）合併患者の麻酔管理を8例経験した．2例で術後呼吸器合併症（肺炎）を認め，ともに長期の人工呼吸管理が必要であった．この2例では，(1)筋障害の程度が強く，(2)術前に高二酸化炭素血症，高度の嚥下障害を認め，(3)胸腺腫瘍に対する胸部手術を受けていた．このような重症MD症例に胸腺摘出術を行うと術後呼吸器合併症が高頻度に合併する危険性があり，周術期管理に留意する必要がある．

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