Properties of a protein activator of glycosphingolipid hydrolysis isolated from the liver of a patient with GM1 gangliosidosis, type 1.

[1]  H. Christomanou.  Niemann-Pick disease, Type C: evidence for the deficiency of an activating factor stimulating sphingomyelin and glucocerebroside degradation. , 1980, Hoppe-Seyler's Zeitschrift fur physiologische Chemie.

[2]  T. Nakamura,et al.  Evidence for the presence of two separate protein activators for the enzymic hydrolysis of GM1 and GM2 gangliosides. , 1979, The Journal of biological chemistry.

[3]  A. Miller,et al.  Purification of human liver acid beta-D-galactosidases using affinity chromatography. , 1976, Analytical biochemistry.

[4]  D. Wenger,et al.  I-cell disease: activities of lysosomal enzymes toward natural and synthetic substrates. , 1976, Life sciences.

[5]  Y. Li,et al.  An activator stimulating the enzymic hydrolysis of sphingoglycolipids. , 1976, The Journal of biological chemistry.

[6]  D. Wenger,et al.  Lactosyl ceramidosis: normal activity for two lactosyl ceramide beta-galactosidases. , 1975, Science.

[7]  H. Mckelvey,et al.  An improved method for the identification of patients and carriers of Krabbe's disease. , 1974, Clinica chimica acta; international journal of clinical chemistry.

[8]  Y. Li,et al.  Requirement of an activator for the hydrolysis of sphingoglycolipids by glycosidases of human liver. , 1974, Carbohydrate research.

[9]  K. Suzuki,et al.  Specific radioactive labeling of terminal n-acetylgalactosamine of glycosphingolipids by the galactose oxidase-sodium borohydride method. , 1972, Journal of lipid research.

[10]  J V Maizel,et al.  Molecular weight estimation of polypeptide chains by electrophoresis in SDS-polyacrylamide gels. , 1967, Biochemical and biophysical research communications.

[11]  H. Jatzkewitz,et al.  Eine Cerebrosidsulfatase aus Schweineniere , 1964 .