Infantile congenital cutis laxa with multiple hernias and ventricular septal defect

Cutis laxa is a rare disorder characterized by degenerative changes in elastic fibres. Congenital cutis laxa is more common than acquired cutis laxa. The recessively inherited form is severe and more frequent. Cutis laxa affects all races and both the sexes equally. We report the first ever case of cutis laxa associated with multiple hernias and cardiac anomaly in an infant.