An abundant erythroid protein that stabilizes free α-haemoglobin

[1]  G. Miele,et al.  A novel erythroid-specific marker of transmissible spongiform encephalopathies , 2001, Nature Medicine.

[2]  S. Schrier,et al.  The importance of erythroid expansion in determining the extent of apoptosis in erythroid precursors in patients with β-thalassemia major , 2000 .

[3]  S. Schrier,et al.  A correlation of erythrokinetics, ineffective erythropoiesis, and erythroid precursor apoptosis in thai patients with thalassemia. , 2000, Blood.

[4]  S. Orkin,et al.  ABC‐me: a novel mitochondrial transporter induced by GATA‐1 during erythroid differentiation , 2000, The EMBO journal.

[5]  S. Gottesman,et al.  Posttranslational quality control: folding, refolding, and degrading proteins. , 1999, Science.

[6]  S. Orkin,et al.  GATA-1 and erythropoietin cooperate to promote erythroid cell survival by regulating bcl-xL expression. , 1999, Blood.

[7]  F. Cohen,et al.  Prion Protein Biology , 1998, Cell.

[8]  Y Fujiwara,et al.  Arrested development of embryonic red cell precursors in mouse embryos lacking transcription factor GATA-1. , 1996, Proceedings of the National Academy of Sciences of the United States of America.

[9]  P. Detloff,et al.  A mouse model for beta 0-thalassemia. , 1995, Proceedings of the National Academy of Sciences of the United States of America.

[10]  S. Schrier,et al.  The instability of the membrane skeleton in thalassemic red blood cells. , 1995, Blood.

[11]  T. Townes,et al.  Mouse model of human beta zero thalassemia: targeted deletion of the mouse beta maj- and beta min-globin genes in embryonic stem cells. , 1995, Proceedings of the National Academy of Sciences of the United States of America.

[12]  S. Orkin,et al.  GATA transcription factors: key regulators of hematopoiesis. , 1995, Experimental hematology.

[13]  G. Keller,et al.  Novel insights into erythroid development revealed through in vitro differentiation of GATA-1 embryonic stem cells. , 1994, Genes & development.

[14]  S. Schrier,et al.  Accelerated programmed cell death (apoptosis) in erythroid precursors of patients with severe beta-thalassemia (Cooley's anemia) [see comments] , 1993 .

[15]  S. Schrier,et al.  The role of membrane skeletal-associated alpha-globin in the pathophysiology of beta-thalassemia. , 1990, Blood.

[16]  S. Schrier,et al.  Erythrocyte membrane skeleton abnormalities in severe beta-thalassemia. , 1987, Blood.

[17]  J. Shaeffer.  Turnover of excess hemoglobin alpha chains in beta-thalassemic cells is ATP-dependent. , 1983, The Journal of biological chemistry.

[18]  T. Inubushi,et al.  Preparation of hybrid hemoglobins with different prosthetic groups. , 1981, Methods in enzymology.

[19]  S. Wickramasinghe,et al.  Ultrastructural Studies of Erythropoiesis in β‐Thalassaemia Trait , 1980, British journal of haematology.

[20]  Rachmilewitz Ea,et al.  Denaturation of the normal and abnormal hemoglobin molecule. , 1974 .

[21]  J. Peisach,et al.  Studies on the stability of oxyhemoglobin A and its constituent chains and their derivatives. , 1971, The Journal of biological chemistry.

[22]  D. Nathan,et al.  Failure of nitro blue tetrazolium reduction in the phagocytic vacuoles of leukocytes in chronic granulomatous disease. , 1969, The Journal of clinical investigation.

[23]  A. Bank,et al.  Intracellular Loss of Free α Chains in β Thalassaemia , 1969, Nature.

[24]  R. Gunn,et al.  Influence of hemoglobin precipitation on erythrocyte metabolism in alpha and beta thalassemia. , 1969, The Journal of clinical investigation.

[25]  C Baglioni,et al.  Chromosomal and cytoplasmic regulation of haemoglobin synthesis. , 1968, Bibliotheca haematologica.

[26]  J. Shaeffer.  Evidence for soluble alpha-chains as intermediates in hemoglobin synthesis in the rabbit reticulocyte. , 1967, Biochemical and biophysical research communications.

[27]  I. London,et al.  The control of hemoglobin synthesis. , 1967, Transactions of the Association of American Physicians.

[28]  R. Gunn,et al.  Thalassemia: the consequences of unbalanced hemoglobin synthesis. , 1966, The American journal of medicine.