Persistent papules and plaques in systemic juvenile idiopathic arthritis

A 6‐year‐old girl presented with nightly fever, persistent joint pain of the knees, ankles, lower back, and hip. Her skin lesions were evanescent salmon‐colored patches along with persistent pruritic light to dark pink papules and plaques on her face, post‐auricular scalp, trunk, thigh, and bilateral upper extremities. Skin biopsy supported the diagnosis of fixed papules and plaques of systemic juvenile idiopathic arthritis (sJIA). We report this case to highlight diagnostic features of this exceedingly rare cutaneous presentation of sJIA presenting with typical cutaneous salmon‐colored evanescent eruptions.

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