Primitive neuroectodermal tumour of the adrenal gland

cytoplasm, partially forming distinct Homer Wright Case report rosettes (Fig. 2a). Immunohistochemical stains were positive for MIC2 (CD99) (cytoplasmic surface membrane A 32-year-old woman presented with a 4-month history of abdominal pain. On physical examination, a huge staining, Fig. 2b) and NSE, providing evidence of a primitive neuroectodermal tumour (PNET). The patient firm mass was palpable at the left epigastrium. Laboratory studies revealed high serum LDH and neuronunderwent two courses of adjuvant chemotherapy with etoposide, ifosfamide and cisplatin. However, she died 5 specific enolase (NSE) levels of 4070 U/L and 13 ng/mL (normal range <10), respectively. CT showed a 10 cm months after surgery with progression of local recurrence, and liver, lung and brain metastases. mass in the left retroperitoneal area, with multiple liver metastases. The patient underwent surgery and the large mass of the adrenal gland adherent to the surrounding tissue was removed, together with the left kidney (Fig. 1). The tumour tissue consisted of monomorphic cells with round to oval nuclei and abundant eosinophilic