Inherited deficiencies of the terminal complement components.
暂无分享,去创建一个
[1] B. H. Petersen,et al. Two types of dysfunctional eighth component of complement (C8) molecules in C8 deficiency in man. Reconstitution of normal C8 from the mixture of two abnormal C8 molecules. , 1983, The Journal of clinical investigation.
[2] L. T. Rosenberg,et al. Mice deficient in C5. , 1986, Chemical Immunology.
[3] L. Reller,et al. Prevalence of congenital or acquired complement deficiency in patients with sporadic meningococcal disease. , 1983, The New England journal of medicine.
[4] P. Densen,et al. Beta chain deficiency in three patients with dysfunctional C8 molecules. , 1983, Molecular immunology.
[5] B. H. Petersen,et al. Genetic polymorphism in C8 beta-chains. Evidence for two unlinked genetic loci for the eighth component of human complement (C8). , 1983, The Journal of clinical investigation.
[6] W. Hsueh,et al. The role of the complement system in shock and tissue injury induced by tumour necrosis factor and endotoxin. , 1990, Immunology.
[7] K. Yoshimura,et al. Inherited deficiencies of the late-acting complement components other than C9 found among healthy blood donors. , 1989, International archives of allergy and applied immunology.
[8] S. Meri,et al. Human protectin (CD59), an 18,000-20,000 MW complement lysis restricting factor, inhibits C5b-8 catalysed insertion of C9 into lipid bilayers. , 1990, Immunology.
[9] T. Mollnes,et al. Regulation of Complement , 1988, Scandinavian journal of immunology.
[10] P. Densen,et al. Infectious diseases associated with complement deficiencies , 1991, Clinical Microbiology Reviews.
[11] I. Brandslund,et al. Screening for complement deficiencies in unselected patients with meningitis. , 1987, Clinical and experimental immunology.
[12] A. Dalmasso,et al. The pathobiology of the terminal complement complexes. , 1989, Complement and inflammation.
[13] P. Potter,et al. Deficiency of the sixth component of complement and susceptibility to Neisseria meningitidis infections: studies in 10 families and five isolated cases. , 1987, Immunology.
[14] S Povey,et al. The gene for human complement component C9 mapped to chromosome 5 by polymerase chain reaction. , 1989, Genomics.
[15] R. Snyderman,et al. Deficiency of the fifth component of complement in human subjects: Clinical, genetic and immunologic studies in a large kindred , 1979 .
[16] J. Leddy,et al. Hereditary deficiency of the fifth component of complement in man. I. Clinical, immunochemical, and family studies. , 1976, The Journal of clinical investigation.
[17] T. Lea,et al. The Terminal Complement Complex in Sera Deficient in the Eighth Component of Complement (C8) , 1986, Scandinavian journal of immunology.
[18] A. Gianella-Borradori,et al. Combined complete C5 and partial C4 deficiency in humans: clinical consequences and complement-mediated functions in vitro. , 1990, Clinical immunology and immunopathology.
[19] Francesco Saverio Tedesco. Component deficiencies. 8. The eighth component. , 1986, Progress in allergy.
[20] P. Lachmann,et al. Combined genetic deficiency of C6 and C7 in man. , 1978, Clinical and experimental immunology.
[21] V. Wahn,et al. Identification of the Heterozygotes for Deficiency of the β-Subunit of the Eighth Component of Complement by Reduced Levels of C8β and Increased Amounts of Free C8α-γ , 1990, Pediatric Research.
[22] M. L. Le Beau,et al. Molecular analysis of human complement component C5: localization of the structural gene to chromosome 9. , 1988, Biochemistry.
[23] G. Hänsch,et al. Complement in inflammation: induction of nephritides and progress to chronicity. , 1991, International archives of allergy and applied immunology.
[24] E. Prochazka,et al. Simultaneous occurrence of hereditary C6 and C2 deficiency in a French-Canadian family. , 1979, Immunology.
[25] V. Wahn,et al. Deficiency of the Eighth Component of Complement. Evidence for Linkage of C8α‐γ Pattern with C8β Deficiency in Sera of Twelve Patients , 1989 .
[26] T. Kawashima,et al. Genetic deficiency of the alpha-gamma-subunit of the eighth complement component in the rabbit. , 1985, Journal of Immunology.
[27] P. Lachmann,et al. INHERITED STRUCTURAL VARIATION AND LINKAGE RELATIONSHIPS OF C7 , 1978, Journal of immunogenetics.
[28] R. Perricone,et al. Complement Deficiency and Antibody Profile in Survivors of Meningococcal Meningitis due to common Serogroups in Italy , 1992, Scandinavian journal of immunology.
[29] S. Tanaka,et al. High-incidence of C9 deficiency throughout Japan: there are no significant differences in incidence among eight areas of Japan. , 1989, International archives of allergy and applied immunology.
[30] C. Parker,et al. PAROXYSMAL NOCTURNAL HEMOGLOBINURIA AND GLYCOSYL PHOSPHATIDYLINOSITOL ANCHORED PROTEINS THAT REGULATE COMPLEMENT , 1991, Clinical and experimental immunology.
[31] C. Schwartz,et al. Chromosomal assignment of genes encoding the α, β, and γ subunits of human complement protein C8: Identification of a close physical linkage between the α and the β loci , 1989 .
[32] Y. Mizuno,et al. Inherited deficiency of ninth component of complement: an increased risk of meningococcal meningitis. , 1989, The Journal of pediatrics.
[33] A. Sjöholm,et al. COMPLEMENT DEFICIENCIES IN PATIENTS OVER TEN YEARS OLD WITH MENINGOCOCCAL DISEASE DUE TO UNCOMMON SEROGROUPS , 1989, The Lancet.
[34] P. Späth,et al. Clinical manifestations in humans of combined C7 and C4 deficiency associated with low levels of C2, C8, and C9. , 1991, Complement and inflammation.
[35] K. Tokunaga,et al. Family study on the polymorphisms of the sixth and seventh components (C6 and C7) of human complement: linkage and haplotype analyses. , 1986, American journal of human genetics.
[36] V. Rodríguez-Valverde,et al. Prevalence of deficits of complement components in patients with recurrent meningococcal infections. , 1983, The Journal of infectious diseases.
[37] B. Olaisen,et al. The C8A and C8B loci are closely linked on chromosome 1 , 1986, Annals of human genetics.
[38] R. Thompson,et al. Combined familial C7 and C4B deficiency in an adult with meningococcal disease. , 1987, Clinical and Experimental Immunology.
[39] P. Brandtzaeg,et al. Complement activation and endotoxin levels in systemic meningococcal disease. , 1989, The Journal of infectious diseases.
[40] P. Lachmann,et al. The behaviour of complement and platelets in lethal endotoxin shock in rabbits. , 1973, International archives of allergy and applied immunology.
[41] A. Giovanetti,et al. A lupus-like syndrome in a patient with deficiency of the sixth component of complement. , 1981, Arthritis and rheumatism.
[42] O. Götze,et al. Functionally active complement proteins C6 and C7 detected in C6‐ and C7‐deficient individuals , 1991, Clinical and experimental immunology.
[43] B. Morgan. Complement membrane attack on nucleated cells: resistance, recovery and non-lethal effects. , 1989, The Biochemical journal.
[44] C. Alper,et al. Inherited structural polymorphism of the fourth component of human complement. , 1980, Proceedings of the National Academy of Sciences of the United States of America.
[45] M. Lishner,et al. Hereditary complement deficiency in survivors of meningococcal disease: high prevalence of C7/C8 deficiency in Sephardic (Moroccan) Jews. , 1987, The Quarterly journal of medicine.
[46] B. H. Petersen,et al. Neisseria meningitidis and Neisseria gonorrhoeae bacteremia associated with C6, C7, or C8 deficiency. , 1979, Annals of internal medicine.
[47] C. Ryder,et al. Complement abnormalities during an epidemic of group B meningococcal infection in children. , 1986, Clinical and experimental immunology.
[48] Z. Fishelson,et al. Prevalence of hereditary properdin, C7 and C8 deficiencies in patients with meningococcal infections , 1990, Clinical and experimental immunology.
[49] P. Späth,et al. Dysfunctional C8β Chain in Patients with C8 Deficiency , 1986 .
[50] H. Kitamura,et al. Deficiency of the ninth component of complement in man. , 1979, Journal of clinical & laboratory immunology.
[51] M. Basaglia,et al. Bactericidal-activities of human polymorphonuclear leukocyte proteins against Escherichia coli O111:B4 coated with C5 or C8 , 1986, Infection and immunity.
[52] P. Schur,et al. Inherited deficiency of the sixth component of complement: a silent or null gene. , 1978, Journal of immunology.
[53] R. Ulevitch,et al. The effect of complement depletion on bacterial lipopolysaccharide (LPS)-induced hemodynamic and hematologic changes in the Rhesus monkey. , 1978, The American journal of pathology.
[54] Francesco Saverio Tedesco,et al. Two distinct abnormalities in patients with C8 alpha-gamma deficiency. Low level of C8 beta chain and presence of dysfunctional C8 alpha-gamma subunit. , 1990, The Journal of clinical investigation.
[55] P. Densen,et al. Complement Deficiency States and Infection: Epidemiology, Pathogenesis and Consequences of Neisserial and Other Infections in an Immune Deficiency , 1984, Medicine.
[56] S. Povey,et al. The assignment of the genes coding for human complement components C6 and C7 to chromosome 5 , 1990, Annals of human genetics.
[57] B. H. Petersen,et al. Genetic control of the eighth component of complement. , 1979, The Journal of clinical investigation.
[58] P. Magnussen,et al. Complement deficiencies in selected groups of patients with meningococcal disease. , 1989, Scandinavian journal of infectious diseases.
[59] P. Rosenthal,et al. Killing of Neisseria meningitidis by human neutrophils: implications for normal and complement-deficient individuals. , 1987, The Journal of infectious diseases.
[60] M. Kazatchkine,et al. Relative inefficiency of terminal complement activation. , 1988, Journal of immunology.