Simplifying the diet for patients with phenylketonuria (PKU): unrestricted consumption of fruit and vegetables

Summary Over a period of three years, the phenylalanine content in fruit and vegetables was not taken into account in the daily phenylalanine balance for patients with phenylketonuria, a congenital metabolic disorder. In spite of a significantly higher intake of phenylalanine, no worsening of metabolic control could be detected.

[1]  U. Ceglarek,et al.  Unrestricted fruits and vegetables in the PKU diet: a 1-year follow-up , 2014, European Journal of Clinical Nutrition.

[2]  John J. Mitchell,et al.  Phenylalanine hydroxylase deficiency: diagnosis and management guideline , 2013, Genetics in Medicine.

[3]  K. Cockell,et al.  Impact of Antinutritional Factors in Food Proteins on the Digestibility of Protein and the Bioavailability of Amino Acids and on Protein Quality , 2012, British Journal of Nutrition.

[4]  M. Baumgartner,et al.  Positive effect of a simplified diet on blood phenylalanine control in different phenylketonuria variants, characterized by newborn BH4 loading test and PAH analysis. , 2012, Molecular genetics and metabolism.

[5]  U. Ceglarek,et al.  Unrestricted consumption of fruits and vegetables in phenylketonuria: no major impact on metabolic control , 2012, European Journal of Clinical Nutrition.

[6]  Gert B. M. Mensink,et al.  Ernährungsstudie als KiGGS-Modul (EsKiMo) , 2007 .

[7]  I. Booth,et al.  Free use of fruits and vegetables in phenylketonuria , 2003, Journal of Inherited Metabolic Disease.

[8]  U. Ceglarek,et al.  Validation of the Phenylalanine/Tyrosine Ratio Determined by Tandem Mass Spectrometry: Sensitive Newborn Screening for Phenylketonuria , 2002, Clinical chemistry and laboratory medicine.

[9]  H. Bremer,et al.  Rationale for the German recommendations for phenylalanine level control in phenylketonuria 1997 , 1999, European Journal of Pediatrics.

[10]  B. Eggum The influence of dietary fibre on protein digestion and utilization in monogastrics. , 1995, Archiv fur Tierernahrung.